Mlembi: Joan Hall
Tsiku La Chilengedwe: 6 Febuluwale 2021
Sinthani Tsiku: 24 Kuni 2024
Anonim
Leukocytoclastic vasculitis   Jill Magee
Kanema: Leukocytoclastic vasculitis Jill Magee

Hypersensitivity vasculitis imakhudza kwambiri mankhwala, matenda, kapena zinthu zakunja. Zimayambitsa kutupa ndi kuwonongeka kwa mitsempha yamagazi, makamaka pakhungu. Mawuwa sanagwiritsidwe ntchito pakadali pano chifukwa mayina ena amawerengedwa kuti ndi olondola.

Hypersensitivity vasculitis, kapena chotengera chochepa chotengera vasculitis, chimayambitsidwa ndi:

  • Zomwe zimachitika chifukwa cha mankhwala kapena chinthu china chakunja
  • Zomwe zimachitika kudwala

Nthawi zambiri zimakhudza anthu achikulire kuposa zaka 16.

Nthawi zambiri, chomwe chimayambitsa vutoli sichimapezeka ngakhale mutasanthula bwino mbiri yazachipatala.

Hypersensitivity vasculitis imawoneka ngati ya systemic, necrotizing vasculitis, yomwe imatha kukhudza mitsempha yamagazi mthupi lonse osati pakhungu lokha. Kwa ana, imatha kuwoneka ngati Henoch-Schonlein purpura.

Zizindikiro zimaphatikizapo:

  • Ziphuphu zatsopano ndimadontho ofiira, ofiira kapena ofiira ofiira m'malo akulu
  • Zilonda za khungu makamaka zimapezeka pa miyendo, matako, kapena thunthu
  • Matuza pakhungu
  • Ming'oma (urticaria), imatha kupitilira maola 24
  • Tsegulani zilonda ndi minofu yakufa (zilonda zam'mimba)

Wothandizira zaumoyo adzatengera matendawa pazizindikiro. Woperekayo awunika mankhwala aliwonse kapena mankhwala omwe mwamwa ndi matenda aposachedwa. Mudzafunsidwa za chifuwa, malungo, kapena kupweteka pachifuwa.


Kuyezetsa kwathunthu kumachitika.

Mayeso amwazi ndi mkodzo atha kuchitidwa kuti afufuze zovuta zama systemic monga systemic lupus erythematosus, dermatomyositis, kapena hepatitis C. Mayeso amwazi atha kuphatikizira:

  • Kuwerengera kwathunthu kwa magazi ndikusiyanitsa
  • Mlingo wa sedimentation wa erythrocyte
  • Chemistry yokhala ndi michere ya chiwindi ndi creatinine
  • Antinuclear antibody (ANA)
  • Chifuwa cha nyamakazi
  • Antineutrophil cytoplasmic antibodies (ANCA)
  • Malizitsani milingo
  • Cryoglobulins
  • Mayeso a hepatitis B ndi C
  • Kuyezetsa HIV
  • Kupenda kwamadzi

Khungu la khungu limasonyeza kutupa kwa mitsempha yaying'ono yamagazi.

Cholinga cha chithandizo ndikuchepetsa kutupa.

Wothandizira anu akhoza kukupatsani mankhwala a aspirin, nonsteroidal anti-inflammatory drugs (NSAIDs), kapena corticosteroids kuti achepetse kutupa kwa mitsempha yamagazi. (MUSAMAPATSE ana aspirin kupatula ngati walangizidwa ndi omwe amakupatsani).

Wothandizira anu adzakuuzani kuti musiye kumwa mankhwala omwe angayambitse vutoli.


Hypersensitivity vasculitis nthawi zambiri imapita pakapita nthawi. Vutoli limatha kubwerera kwa anthu ena.

Anthu omwe ali ndi vasculitis mosalekeza amayenera kuwunika ngati ali ndi vasculitis.

Zovuta zingaphatikizepo:

  • Kuwonongeka kwakanthawi pamitsempha yamagazi kapena khungu lokhala ndi zipsera
  • Mitsempha yotupa yam'mimba yomwe imakhudza ziwalo zamkati

Itanani omwe akukuthandizani ngati muli ndi zizindikiro za hypersensitivity vasculitis.

Musamamwe mankhwala omwe amachititsa kuti thupi lanu lisamayende bwino m'mbuyomu.

Chotengera chochepa chotengera chotchedwa vasculitis; Matupi awo sagwirizana vasculitis; Leukocytoclastic vasculitis

  • Vasculitis pachikhatho
  • Vasculitis
  • Vasculitis - urticarial padzanja

Khalani TP. Hypersensitivity syndromes ndi vasculitis. Mu: Habif TP, mkonzi. Matenda Opatsirana Matenda. Lachisanu ndi chimodzi. Philadelphia, PA: Elsevier; 2016: mutu 18.


Jennette JC, Falk RJ, Bacon PA, ndi al. 2012 yasinthidwanso pamsonkhano wapadziko lonse wa Chapel Hill pamasankho a vasculitides. Nyamakazi Rheum. 2013; 65 (1): 1-11. PMID: 23045170 www.ncbi.nlm.nih.gov/pubmed/23045170.

Patterson JW. Njira ya vasculopathic reaction. Mu: Patterson JW, mkonzi. Matenda a Khungu la Weedon. Wolemba 4. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: mutu 8.

Mwala JH. Mawonekedwe a vasculitides. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. Wolemba 25. Philadelphia, PA: Elsevier Saunders; 2016: chap 270.

Sunderkötter CH, Zelger B, Chen KR, ndi al. Nomenclature ya cutaneous vasculitis: dermatologic addendum ku 2012 Revised International Chapel Hill Consensus Conference Nomenclature ya Vasculitides. Nyamakazi Rheumatol. 2018; 70 (2): 171-184. (Adasankhidwa) PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340. (Adasankhidwa)

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