Mlembi: Laura McKinney
Tsiku La Chilengedwe: 6 Epulo 2021
Sinthani Tsiku: 24 Kuni 2024
Anonim
Sekondale Polycythemia (Sekondale Erythrocytosis) - Thanzi
Sekondale Polycythemia (Sekondale Erythrocytosis) - Thanzi

Zamkati

Chidule

Sekondale polycythemia ndikuchulukitsa kwa maselo ofiira amwazi. Zimayambitsa magazi anu kuti awonjezeke, zomwe zimawonjezera chiopsezo cha sitiroko. Ndi chikhalidwe chosowa.

Ntchito yoyamba ya maselo ofiira a magazi ndikunyamula mpweya kuchokera m'mapapu anu kupita nawo m'maselo onse amthupi lanu.

Maselo ofiira ofiira amapangidwa m'mafupa anu nthawi zonse. Mukasamukira kumtunda wapamwamba komwe mpweya umakhala wochepa, thupi lanu limazindikira izi ndikuyamba kupanga maselo ofiira ochulukirapo patatha milungu ingapo.

Sekondale vs. primary

Sekondale polycythemia amatanthauza kuti vuto lina limapangitsa kuti thupi lanu lipange maselo ofiira ochulukirapo.

Nthawi zambiri mumakhala ndi mahomoni owonjezera a erythropoietin (EPO) omwe amayendetsa kupanga maselo ofiira.

Chifukwa chake chikhoza kukhala:

  • cholepheretsa kupuma monga matenda obanika kutulo
  • matenda am'mapapo kapena amtima
  • kugwiritsa ntchito mankhwala opititsa patsogolo ntchito

Choyambirira polycythemia ndi chibadwa. Zimayambitsidwa ndi kusintha kwa maselo am'mafupa, omwe amatulutsa maselo ofiira amwazi.


Sekondale polycythemia imatha kukhalanso ndi chibadwa. Koma sizomwe zimachokera pakusintha kwama cell am'mafupa.

Mu polycythemia yachiwiri, gawo lanu la EPO lidzakhala lokwera ndipo mudzakhala ndi kuchuluka kwama cell ofiira. Mu pulayimale polycythemia, kuchuluka kwanu kwama cell ofiira ofiira kudzakhala kwakukulu, koma mudzakhala ndi EPO yochepa.

Dzina laumisiri

Sekondale polycythemia tsopano imadziwika kuti sekondale erythrocytosis.

Polycythemia amatanthauza mitundu yonse yamagazi - maselo ofiira, maselo oyera, ndi ma platelet. Mabakiteriya Ndi maselo ofiira okha, omwe amachititsa kuti erythrocytosis ikhale dzina lovomerezeka la vutoli.

Zomwe zimayambitsa polycythemia yachiwiri

Zomwe zimayambitsa polycythemia yachiwiri ndi:

  • kugona tulo
  • kusuta kapena matenda am'mapapo
  • kunenepa kwambiri
  • hypoventilation
  • Matenda a Pickwickian
  • Matenda osokoneza bongo (COPD)
  • okodzetsa
  • mankhwala opititsa patsogolo ntchito, kuphatikiza EPO, testosterone, ndi anabolic steroids

Zina mwazomwe zimayambitsa polycythemia yachiwiri ndi izi:


  • Mpweya wa carbon monoxide
  • kukhala kumtunda
  • matenda a impso kapena zotupa

Pomaliza, matenda ena amatha kupangitsa kuti thupi lanu lichulukire kuchuluka kwa mahomoni a EPO, omwe amachititsa kuti maselo ofiira apangidwe. Zina mwazomwe zingayambitse izi ndi izi:

  • zotupa zina zamaubongo (cerebellar hemangioblastoma, meningioma)
  • chotupa cha parathyroid England
  • khansa ya hepatocellular (chiwindi)
  • khansa ya impso (impso)
  • chotupa cha adrenal gland
  • chosaopsa cha fibroids m'chiberekero

Mu, chifukwa cha polycythemia yachiwiri chimatha kukhala chibadwa. Izi zimachitika makamaka chifukwa cha kusintha komwe kumapangitsa kuti maselo anu ofiira amwe mpweya wabwino.

Zowopsa za polycythemia yachiwiri

Zomwe zimayambitsa chiopsezo cha polycythemia yachiwiri (erythrocytosis) ndi:

  • kunenepa kwambiri
  • kumwa mowa mwauchidakwa
  • kusuta
  • kuthamanga kwa magazi (matenda oopsa)

Zowopsa zomwe zapezedwa posachedwa ndikukhala ndi kufalikira kwama cell ofiira (RDW), zomwe zikutanthauza kuti kukula kwa maselo ofiira amwazi wosiyanasiyana. Izi zimadziwikanso kuti anisocytosis.


Zizindikiro za polycythemia yachiwiri

Zizindikiro za polycythemia yachiwiri ndi izi:

  • kupuma movutikira
  • chifuwa ndi kupweteka m'mimba
  • kutopa
  • kufooka ndi kupweteka kwa minofu
  • mutu
  • kulira m'makutu (tinnitus)
  • kusawona bwino
  • kuwotcha kapena "zikhomo ndi singano" kumverera m'manja, mikono, miyendo, kapena mapazi
  • ulesi wamaganizidwe

Kuzindikira ndikuchiza kwa polycythemia yachiwiri

Dokotala wanu adzafuna kudziwa polycythemia yachiwiri komanso chomwe chimayambitsa. Chithandizo chanu chimadalira pazomwe zimayambitsa.

Adotolo atenga mbiri yakuchipatala, kukufunsani zamatenda anu, ndikukuyesani. Adzayesa kuyesa kwa kujambula ndi kuyesa magazi.

Chimodzi mwazizindikiro za polycythemia yachiwiri ndi kuyesa kwa hematocrit. Ili ndi gawo la gulu lathunthu lamagazi. Hematocrit ndiyeso ya kuchuluka kwa maselo ofiira m'magazi anu.

Ngati hematocrit yanu ndiyokwera ndipo mulinso ndi ma EPO ambiri, itha kukhala chizindikiro cha polycythemia yachiwiri.

Mankhwala akulu a polycythemia yachiwiri ndi awa:

  • aspirin wa mlingo wochepa kuti achepetse magazi anu
  • magazi, amatchedwanso phlebotomy kapena venesection

Ma aspirin ocheperako amagwira ntchito yochepetsetsa magazi ndipo amachepetsa chiopsezo cha sitiroko (thrombosis) kuchokera pakupanga magazi ambiri ofiira.

Kujambula penti yamagazi kumachepetsa kuchuluka kwa maselo ofiira m'magazi anu.

Dokotala wanu adzazindikira kuchuluka kwa magazi omwe ayenera kutengedwa komanso kangati. Njirayi siyopweteka ndipo ili ndi chiopsezo chochepa. Muyenera kupumula mukakoka magazi ndipo onetsetsani kuti mwakhala ndi chotupitsa ndi zakumwa zambiri pambuyo pake.

Dokotala wanu amathanso kukupatsirani mankhwala kuti muchepetse matenda anu.

Nthawi yosachepetsera kuchuluka kwama cell of red

Nthawi zina, dokotala wanu amasankha kuti asachepetse kuchuluka kwanu kwama cell ofiira ofiira. Mwachitsanzo, ngati kuchuluka kwanu kukukula chifukwa chosuta, kutulutsa mpweya wa carbon monoxide, kapena matenda amtima kapena m'mapapo, mungafunike maselo ofiira owonjezera kuti mupeze mpweya wokwanira m'thupi lanu.

Chithandizo chanthawi yayitali chitha kukhala chosankha. Okosijeni wambiri akafika m'mapapu, thupi lanu limamalipira ndikupanga maselo ofiira ochepa. Izi zimachepetsa makulidwe amwazi komanso kupwetekedwa ndi sitiroko. Dokotala wanu akhoza kukutumizirani kwa pulmonologist kuti akuthandizireni oxygen.

Chiwonetsero

Sekondale polycythemia (erythrocytosis) ndichinthu chosowa chomwe chimayambitsa magazi anu kuti achepetse ndikuwonjezera chiopsezo cha sitiroko.

Kawirikawiri zimachitika chifukwa cha vuto linalake, lomwe limatha kukhala lolemera kuyambira pakubanika kwa tulo kupita kudwala lalikulu la mtima. Ngati vutoli silowopsa, anthu ambiri omwe ali ndi polycythemia yachiwiri amatha kuyembekezera kukhala ndi moyo wabwinobwino.

Koma ngati polycythemia imapangitsa magazi kukhala owoneka bwino kwambiri, pamakhala chiopsezo chowonjezeka cha sitiroko.

Polycythemia yachiwiri sikutanthauza chithandizo nthawi zonse. Ngati pakufunika, mankhwala nthawi zambiri amakhala ndi ma aspirin ochepa kapena kujambula magazi (phlebotomy).

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