Retroperitoneal fibrosis

Retroperitoneal fibrosis ndi matenda osowa omwe amalepheretsa timachubu (ureters) tomwe timanyamula mkodzo kuchokera ku impso kupita ku chikhodzodzo.

Retroperitoneal fibrosis imachitika ndikamatuluka minofu yolimba kwambiri kumbuyo kwa mimba ndi matumbo. Minofu imapanga misa (kapena misa) kapena minofu yolimba ya fibrotic. Itha kutsekereza machubu omwe amanyamula mkodzo kuchokera ku impso kupita ku chikhodzodzo.

Zomwe zimayambitsa vutoli sizikudziwika. Amakonda kwambiri anthu azaka zapakati pa 40 mpaka 60. Amuna amakhala ndi mwayi wowirikiza kawiri kuposa akazi.

Zizindikiro zoyambirira:

• Kupweteka kosautsa m'mimba komwe kumawonjezeka ndi nthawi
• Ululu ndikusintha kwamtundu wa miyendo (chifukwa chotsika magazi)
• Kutupa kwa mwendo umodzi

Zizindikiro zamtsogolo:

• Kuchepetsa mkodzo
• Palibe mkodzo (anuria)
• Nseru, kusanza, kusintha kwa malingaliro chifukwa cha kulephera kwa impso komanso kuchuluka kwa mankhwala owopsa m'magazi
• Kupweteka kwambiri m'mimba ndi magazi m'mipando (chifukwa cha kufa kwa minofu yamatumbo)

Mimba yam'mimba ya CT ndiyo njira yabwino kwambiri yopezera misa ya retroperitoneal.

Mayesero ena omwe angathandize kuzindikira vutoli ndi awa:

• BUN ndi mayeso a magazi a creatinine
• Intravenous pyelogram (IVP), osagwiritsidwa ntchito kwambiri
• Impso ultrasound
• MRI ya pamimba
• Kujambula kwa CAT pamimba ndi retroperitoneum

Chidziwitso cha misa chingathenso kuthetsa khansa.

Corticosteroids amayesedwa kaye. Ena othandizira zaumoyo amaperekanso mankhwala otchedwa tamoxifen.

Ngati mankhwala a corticosteroid sakugwira ntchito, biopsy iyenera kuchitidwa kuti mutsimikizire kuti ali ndi matendawa. Mankhwala ena opondereza chitetezo cha mthupi amatha kuperekedwa.

Ngati mankhwala sakugwira ntchito, amafunika opaleshoni ndi fungo (lokhetsa machubu).

Maganizo adzadalira kukula kwa vutoli komanso kuchuluka kwa kuwonongeka kwa impso.

Kuwonongeka kwa impso kungakhale kwakanthawi kapena kosatha.

Matendawa atha kubweretsa ku:

• Kupitilira kwamachubu komwe kumachokera ku impso mbali imodzi kapena mbali zonse ziwiri
• Kulephera kwa impso

Itanani omwe akukuthandizani ngati muli ndi m'mimba kapena kupweteka m'mbali komanso mumatuluka mkodzo pang'ono.

Yesetsani kupewa kugwiritsa ntchito mankhwala kwa nthawi yayitali omwe ali ndi methysergide. Mankhwalawa awonetsedwa kuti amayambitsa retroperitoneal fibrosis. Methysergide nthawi zina imagwiritsidwa ntchito pochiza mutu waching'alang'ala.

Idiopathic retroperitoneal fibrosis; Matenda a Ormond

• Njira yamikodzo yamwamuna

Comperat E, Bonsib SM, Cheng L. Renal mafupa a chiuno ndi ureter. Mu: Cheng L, MacLennan GT, Bostwick DG, olemba., Eds. Matenda Opangira Urologic. Wolemba 4. Philadelphia, PA: Elsevier; 2020: chaputala 3.

Nakada SY, SL Yabwino Kwambiri. Kuwongolera kutsekemera kwapamwamba kwamikodzo. Mu: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, olemba. Urology wa Campbell-Walsh. 11th ed. Philadelphia, PA: Elsevier; 2016: chap 49.

O'Connor OJ, Maher MM. Thirakiti: kuwunika kwa anatomy, maluso ndi zovuta za radiation. Mu: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, olemba. Grainger & Allison's Diagnostic Radiology: Buku Lophunzirira Kujambula Kwazachipatala. Lachisanu ndi chimodzi. Philadelphia, PA: Elsevier Churchill Livingstone; 2015: chap 35.

Chikhali Mukasa VK. Vasculitis ndi ma arteriopathies ena achilendo. Mu: Sidawy AN, Perler BA, olemba. Rutherford Opaleshoni ya Mitsempha ndi Endovascular Therapy. 9th ed. Philadelphia, PA: Elsevier; 2019: mutu 137.

Turnage RH, Mizell J, Badgwell B. Khoma lam'mimba, umbilicus, peritoneum, mesenteries, omentum, ndi retroperitoneum. Mu: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Buku Lopanga Opaleshoni. Wolemba 20th. Philadelphia, PA: Elsevier Saunders; 2017: mutu 43.