Mlembi: Robert Simon
Tsiku La Chilengedwe: 19 Kuni 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
Pachimake Cerebellar Ataxia (ACA) - Thanzi
Pachimake Cerebellar Ataxia (ACA) - Thanzi

Zamkati

Kodi pachimake cerebellar ataxia ndi chiyani?

Pachimake cerebellar ataxia (ACA) ndi vuto lomwe limachitika cerebellum ikatupa kapena kuwonongeka. Cerebellum ndi gawo laubongo lomwe limayang'anira kuwongolera ndi kulumikizana kwa minofu.

Teremuyo ataxia amatanthauza kusowa koyendetsa bwino kayendedwe kodzifunira. Pachimake amatanthauza kuti ataxia imabwera mwachangu, motsata mphindi mpaka tsiku limodzi kapena awiri. ACA imadziwikanso kuti cerebellitis.

Anthu omwe ali ndi ACA nthawi zambiri amasowa mgwirizano ndipo amatha kukhala ndi zovuta kuchita ntchito za tsiku ndi tsiku. Matendawa amakhudza kwambiri ana, makamaka azaka zapakati pa 2 ndi 7. Komabe, nthawi zina amakhudzanso achikulire.

Nchiyani chimayambitsa pachimake cerebellar ataxia?

Mavairasi ndi matenda ena omwe amakhudza dongosolo lamanjenje amatha kuvulaza cerebellum. Izi zikuphatikiza:

  • nthomba
  • chikuku
  • matumba
  • chiwindi A
  • Matenda omwe amayamba chifukwa cha ma virus a Epstein-Barr ndi Coxsackie
  • Kachilombo ka West Nile

ACA ikhoza kutenga milungu ingapo kuti iwonekere kutsatira matenda a virus.


Zina mwa zifukwa za ACA ndizo:

  • kutuluka magazi mu cerebellum
  • Kuwonetsedwa kwa mercury, lead, ndi poizoni zina
  • matenda a bakiteriya, monga matenda a Lyme
  • kupwetekedwa mutu
  • kusowa kwa mavitamini ena, monga B-12, B-1 (thiamine), ndi E

Kodi zizindikiro za pachimake cerebellar ataxia ndi ziti?

Zizindikiro za ACA ndizo:

  • Kusayenda bwino kwa torso kapena mikono ndi miyendo
  • kupunthwa pafupipafupi
  • mayendedwe osakhazikika
  • kusayenda kapena kusinthasintha kwa maso
  • kuvuta kudya ndi kuchita ntchito zina zabwino zamagalimoto
  • mawu osalankhula
  • kusintha kwa mawu
  • kupweteka mutu
  • chizungulire

Zizindikirozi zimalumikizidwanso ndi zinthu zina zingapo zomwe zimakhudza dongosolo lamanjenje. Ndikofunika kuti muwone dokotala wanu kuti athe kupeza matenda oyenera.

Kodi pachimake cerebellar ataxia imapezeka bwanji?

Dokotala wanu amayesa mayeso angapo kuti adziwe ngati muli ndi ACA ndi kupeza chomwe chimayambitsa vutoli. Mayesowa atha kuphatikizanso kuyezetsa thupi nthawi zonse komanso kuwunika kwamitsempha yosiyanasiyana. Dokotala wanu amathanso kuyesa mayeso anu:


  • kumva
  • kukumbukira
  • kulinganiza ndi kuyenda
  • masomphenya
  • ndende
  • malingaliro
  • mgwirizano

Ngati simunatenge kachilombo posachedwa, dokotala wanu adzawonanso zizindikiro za zovuta zina zomwe zimayambitsa ACA.

Pali mayesero angapo omwe dokotala angagwiritse ntchito poyesa zizindikiro zanu, kuphatikizapo:

  • Kuphunzira kwamitsempha. Kafukufuku wopanga mitsempha amadziwika ngati minyewa yanu ikugwira ntchito moyenera.
  • Zojambulajambula (EMG). Electromyogram imalemba ndikuwunika momwe magetsi amagwirira ntchito m'minyewa yanu.
  • Mphepete wamtsempha. Mpopi wamtsempha umalola dokotala wanu kuti ayese cerebrospinal fluid (CSF) yanu, yomwe imazungulira msana ndi ubongo.
  • Kuwerengera kwathunthu kwa magazi (CBC). Kuwerengera kwathunthu kwa magazi kumatsimikizira ngati pali kuchepa kulikonse kapena kuwonjezeka kwama cell anu amwazi. Izi zitha kuthandiza dokotala kuti awone thanzi lanu lonse.
  • CT kapena MRI jambulani. Dokotala wanu amathanso kuyang'ana kuwonongeka kwaubongo pogwiritsa ntchito mayeso ojambulawa. Amapereka zithunzi zambiri zaubongo wanu, zomwe zimamupatsa dokotala kuti ayang'ane ndikuwunika zovuta zilizonse muubongo.
  • Kupenda kwamadzi ndipo akupanga. Izi ndi mayeso ena omwe dokotala wanu angachite.

Kodi pachimake cerebellar ataxia amathandizidwa bwanji?

Kuchiza kwa ACA sikofunikira nthawi zonse. Pamene kachilombo kamayambitsa ACA, nthawi zambiri kuyembekezera kwathunthu popanda chithandizo. Viral ACA nthawi zambiri imatha milungu ingapo osalandira chithandizo.


Komabe, chithandizo chimafunikira ngati kachilombo sikuchititsa ACA yanu. Mankhwalawa amasiyana malinga ndi oyambitsa, ndipo amatha masabata, zaka, kapena moyo wonse. Nawa mankhwala ena omwe angakhalepo:

  • Mungafunike kuchitidwa opaleshoni ngati matenda anu atuluka chifukwa cha magazi.
  • Mungafunike maantibayotiki ngati muli ndi matenda.
  • Ochepetsa magazi amatha kuthandizira ngati stroke idayambitsa ACA yanu.
  • Mutha kumwa mankhwala kuti muchepetse kutupa kwa cerebellum, monga steroids.
  • Ngati poizoni ndiye gwero la ACA, muchepetse kapena muchepetse kukhudzana kwanu ndi poizoni.
  • Ngati ACA idabwera ndi vuto la mavitamini, mutha kuwonjezera mavitamini E, jakisoni wa vitamini B-12, kapena thiamine.
  • Nthawi zina, ACA imatha kubweretsedwanso kudzera mukumvetsetsa kwa gluten. Poterepa, muyenera kudya zakudya zopanda thanzi.

Ngati muli ndi ACA, mungafunike kuthandizidwa ndi ntchito za tsiku ndi tsiku. Ziwiya zapadera zodyera komanso zida zosinthira monga ndodo ndi zothandizira polankhula zitha kuthandiza. Thandizo lakuthupi, mankhwala olankhula, komanso chithandizo chantchito zitha kuthandizanso kukulitsa zizindikilo zanu.

Anthu ena amapezanso kuti kusintha zina ndi zina m'moyo kumatha kuchepetsa zizolowezi. Izi zingaphatikizepo kusintha zakudya zanu kapena kumwa zakudya zowonjezera.

Kodi pachimake cerebellar ataxia imakhudza bwanji akulu?

Zizindikiro za ACA mwa akulu ndizofanana ndi za ana. Mofanana ndi ana, kuchiza ACA wamkulu kumaphatikizapo kuthana ndi vuto lomwe lidayambitsa.

Ngakhale zambiri zomwe ACA zimayambitsa ana zingayambitsenso ACA kwa akuluakulu, pali zifukwa zina zomwe zingayambitse ACA kwa akuluakulu.

Poizoni, makamaka kumwa mowa mopitirira muyeso, ndi chimodzi mwazomwe zimayambitsa ACA mwa akulu. Kuphatikiza apo, mankhwala monga antiepileptic mankhwala ndi chemotherapy nthawi zambiri amagwirizanitsidwa ndi ACA mwa akulu.

Mavuto monga HIV, multiple sclerosis (MS), ndi zovuta zama autoimmune zitha kukhalanso pachiwopsezo cha ACA mukadzakula. Komabe, nthawi zambiri, chifukwa cha ACA mwa akulu sichimadziwika.

Pozindikira kuti ACA ndi akuluakulu, madokotala amayesa kusiyanitsa ACA ndi mitundu ina ya cerebellar ataxias yomwe imabwera pang'onopang'ono. Ngakhale ACA imamenya mphindi zochepa mpaka maola, mitundu ina ya cerebellar ataxia imatha kutenga masiku mpaka zaka kuti ichitike.

Ma ataxias omwe amachepetsa pang'onopang'ono amatha kukhala ndi zifukwa zosiyanasiyana, monga majeremusi, ndipo amafunikira chithandizo chosiyanasiyana.

Monga wamkulu, ndizotheka kuti mudzalandira kulingalira kwaubongo, monga MRI, panthawi yomwe mukudziwa. Kujambula uku kumatha kuwonetsa zodetsa nkhawa zomwe zimatha kuyambitsa ataxias pang'onopang'ono.

Ndi ziti zina zomwe zikufanana ndi pachimake cerebellar ataxia?

ACA imadziwika ndi kuyamba mwachangu - mphindi mpaka maola. Palinso mitundu ina ya ataxia yomwe ili ndi zizindikilo zofananira koma zifukwa zosiyanasiyana:

Subacute ataxias

Subacute ataxias amakula masiku kapena milungu. Nthawi zina subacute ataxias imawoneka ngati ikubwera mwachangu, koma kwenikweni, yakhala ikukula pang'onopang'ono pakapita nthawi.

Zomwe zimayambitsa nthawi zambiri zimakhala zofanana ndi ACA, koma subacute ataxias zimayambitsanso matenda opatsirana monga matenda a prion, matenda a Whipple, ndi leukoencephalopathy (PML) yopita patsogolo.

Matenda osalekeza opita patsogolo

Ma ataxias opita patsogolo amakula ndipo amatha miyezi kapena zaka. Nthawi zambiri zimayambitsidwa ndi cholowa.

Maxixias opita patsogolo amatha kukhalanso chifukwa cha zovuta za mitochondrial kapena neurodegenerative. Matenda ena atha kuyambitsa kapena kutsanzira ma ataxias osachiritsika, monga mutu waching'alang'ala wokhala ndi brainstem aura, matenda osowa pomwe ataxia imatsagana ndi mutu wa migraine.

Ataxias obadwa nawo

Ma ataxias obadwa nawo amapezeka pobadwa ndipo nthawi zambiri amakhala okhazikika, ngakhale ena amatha kuchiritsidwa ndi opaleshoni. Ma ataxias amayamba chifukwa chobadwa ndi zovuta zaubongo.

Ndi zovuta ziti zomwe zimakhudzana ndi pachimake cerebellar ataxia?

Zizindikiro za ACA zitha kukhala zachikhalire ngati matendawa amayamba chifukwa cha sitiroko, matenda, kapena kutuluka magazi mu cerebellum.

Ngati muli ndi ACA, mulinso pachiwopsezo chachikulu chokhala ndi nkhawa komanso kukhumudwa. Izi ndizowona makamaka ngati mukufuna kuthandizidwa ndi ntchito za tsiku ndi tsiku, kapena simungathe kuyendera nokha.

Kuyanjana ndi gulu lothandizira kapena kukumana ndi mlangizi kungakuthandizeni kuthana ndi zizindikilo zanu komanso zovuta zilizonse zomwe mukukumana nazo.

Kodi ndizotheka kupewa pachimake cerebellar ataxia?

Ndizovuta kupewa ACA, koma mutha kuchepetsa chiopsezo cha ana anu kuchipeza powonetsetsa kuti atemera katemera wama virus omwe angayambitse ACA, monga nkhuku.

Monga wamkulu, mutha kuchepetsa chiopsezo chanu cha ACA popewa kumwa kwambiri mowa ndi poizoni wina. Kuchepetsa chiopsezo cha sitiroko pochita masewera olimbitsa thupi, kukhala ndi thanzi labwino, komanso kusungunuka kwa magazi ndi cholesterol kungathandizenso kupewa ACA.

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