Matenda a Bartter

Matenda a Bartter ndi gulu lazovuta zomwe zimakhudza impso.

Pali zolakwika zisanu za jini zomwe zimadziwika kuti zimalumikizidwa ndi matenda a Bartter. Vutoli limakhalapo pakubadwa (kobadwa nako).

Matendawa amayamba chifukwa cha vuto la impso kuthekanso kubwezeretsanso sodium. Anthu omwe akhudzidwa ndi matenda a Bartter amataya sodium wochuluka kwambiri kudzera mumkodzo. Izi zimapangitsa kukwera kwa mulingo wa hormone aldosterone, ndikupangitsa impso kuchotsa potaziyamu wochuluka mthupi. Izi zimadziwika ngati kuwonongeka kwa potaziyamu.

Vutoli limayambitsanso kuchuluka kwa asidi m'magazi otchedwa hypokalemic alkalosis, omwe amayambitsa calcium yambiri mumkodzo.

Matendawa amapezeka nthawi zambiri ali mwana. Zizindikiro zake ndi izi:

• Kudzimbidwa
• Mlingo wa kunenepa kwambiri ndi wotsika kwambiri kuposa wa ana ena azaka zofananira komanso kugonana (kukula kulephera)
• Kufunika kukodza nthawi zambiri kuposa pafupipafupi (pafupipafupi)
• Kuthamanga kwa magazi
• Miyala ya impso
• Minofu cramping ndi kufooka

Matenda a Bartter nthawi zambiri amakayikiridwa pamene kuyezetsa magazi kumapeza potaziyamu wochepa m'magazi. Mosiyana ndi mitundu ina yamatenda a impso, izi sizimayambitsa kuthamanga kwa magazi. Pali chizoloŵezi chotsika magazi. Mayeso a labotale atha kuwonetsa:

• Mlingo waukulu wa potaziyamu, calcium, ndi mankhwala enaake mumkodzo
• Mahomoni ambiri, renin ndi aldosterone, m'magazi
• Mankhwala otsika a magazi
• Kagayidwe kachakudya alkalosis

Zizindikiro zomwezi zimatha kukhalanso mwa anthu omwe amatenga okodzetsa ambiri (mapiritsi amadzi) kapena mankhwala ofewetsa tuvi tolimba. Kuyezetsa mkodzo kumatha kuchitika pazifukwa zina.

Kupanga kwa impso kumatha kuchitika.

Matenda a Bartter amachizidwa ndi kudya zakudya zokhala ndi potaziyamu kapena kumwa potaziyamu.

Anthu ambiri amafunikiranso zowonjezera mchere.Mankhwala angafunike omwe amalepheretsa impso potaziyamu. Mankhwala osagwiritsidwa ntchito poletsa kutupa (NSAIDs) atha kugwiritsidwanso ntchito.

Makanda omwe amalephera kukula akhoza kukula bwino ndi chithandizo. Popita nthawi, anthu ena omwe ali ndi vutoli amakhala ndi impso zolephera.

Imbani wothandizira zaumoyo wanu ngati mwana wanu ali:

• Kukhala ndi kukokana kwa minofu
• Osakula bwino
• Kukodza pafupipafupi

Kuwonongeka kwa potaziyamu; Nephropathy yowononga mchere

• Mayeso a Aldosterone level

Dixon BP. Zovuta zonyamula ma tubular zolakwika: Matenda a Bartter. Mu: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 549.1

Masewera a Guay-Woodford LM. Cholowa nephropathies ndi chitukuko chitukuko cha kwamikodzo thirakiti. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. 26 wa. Philadelphia, PA: Elsevier; 2020: chap 119.

Phiri la DB. Kusokonezeka kwa potaziyamu bwino. Mu: Yu ASL, Chertow GM, Luyckx VA, Marsden PA, Skorecki K, Taal MW, olemba. Brenner ndi Rector a Impso. 11th ed. Philadelphia, PA: Elsevier; 2020: chap 17.