Mlembi: Gregory Harris
Tsiku La Chilengedwe: 8 Epulo 2021
Sinthani Tsiku: 25 Kuni 2024
Anonim
Neurosarcoidosis | Dr Kidd (Part 1)
Kanema: Neurosarcoidosis | Dr Kidd (Part 1)

Neurosarcoidosis ndi vuto la sarcoidosis, momwe kutupa kumachitika muubongo, msana, ndi madera ena amanjenje.

Sarcoidosis ndi matenda osachiritsika omwe amakhudza mbali zambiri za thupi, makamaka mapapu. Mwa anthu ochepa, matendawa amakhudza gawo lina lamanjenje. Izi zimatchedwa neurosarcoidosis.

Neurosarcoidosis ingakhudze gawo lililonse lamanjenje. Mwadzidzidzi, kufooka kwa nkhope (kupunduka kwa nkhope kapena nkhope kugwa) ndichizindikiro chofala chamitsempha chomwe chimakhudza mitsempha ya minofu ya nkhope. Mitsempha ina iliyonse ya chigaza imatha kukhudzidwa, kuphatikiza ya m'diso ndi yomwe imayendetsa kulawa, kununkhiza, kapena kumva.

Msana wam'mimba ndi gawo lina lamanjenje omwe sarcoidosis imatha kukhudza. Anthu atha kukhala ofooka m'manja ndi m'miyendo, ndikulephera kuyenda kapena kuwongolera mkodzo kapena matumbo awo. Nthawi zina, msana umakhudzidwa kwambiri kwakuti miyendo yonse imakhala yopuwala.

Vutoli limatha kukhudzanso ziwalo zamaubongo zomwe zimakhudzidwa ndikuwongolera zochitika zambiri zamthupi, monga kutentha, kugona, komanso mayankho amapanikizika.


Zofooka zam'mimba kapena zotayika zimatha kuchitika ndikutenga mbali kwa mitsempha. Madera ena aubongo, kuphatikiza ubongo wa pituitary womwe uli m'munsi mwa ubongo, kapena msana wam'mimba amathanso kutenga nawo mbali.

Kuphatikizidwa kwa khungu lamatenda kumatha kuyambitsa:

  • Kusintha kwa msambo
  • Kutopa kwambiri kapena kutopa
  • Ludzu lokwanira
  • Kutulutsa kwamkodzo kwambiri

Zizindikiro zimasiyanasiyana. Gawo lililonse lamanjenje limatha kukhudzidwa. Kuphatikizidwa kwa ubongo kapena mitsempha yamagazi kumatha kuyambitsa:

  • Kusokonezeka, kusokonezeka
  • Kuchepetsa kumva
  • Kusokonezeka maganizo
  • Chizungulire, chizungulire, kapena kuyenda kosazolowereka
  • Masomphenya awiri kapena mavuto ena a masomphenya, kuphatikizapo khungu
  • Nthenda ya nkhope (kufooka, kugwa)
  • Mutu
  • Kutaya kununkhiza
  • Kutaya kwakumva kukoma, zokonda zosazolowereka
  • Kusokonezeka kwamaganizidwe
  • Kugwidwa
  • Kuwonongeka kwamalankhulidwe

Kuphatikizidwa kwa mitsempha imodzi kapena zingapo zotumphukira kumatha kubweretsa ku:


  • Zovuta zathupi lililonse
  • Kutayika kwa gawo lililonse la thupi
  • Kutaya chidwi m'thupi lililonse
  • Kufooka kwa gawo lililonse la thupi

Mayeso atha kuwonetsa mavuto ndi imodzi kapena zingapo zamitsempha.

Mbiri ya sarcoidosis yotsatiridwa ndi zizindikilo zokhudzana ndi mitsempha imatsimikizira za neurosarcoidosis. Komabe, zizindikiro za vutoli zimatha kutsanzira zovuta zina zamankhwala, kuphatikizapo matenda a shuga insipidus, hypopituitarism, optic neuritis, meningitis, ndi zotupa zina. Nthawi zina, dongosolo lamanjenje limatha kukhudzidwa munthu asanadziwike kuti ali ndi sarcoidosis, kapena osakhudza mapapo kapena ziwalo zina.

Kuyezetsa magazi sikothandiza kwambiri pakuzindikira vutoli. Kuboola lumbar kumatha kuwonetsa zizindikilo zotupa. Kuchulukitsa kwa enzyme yotembenuza angiotensin kumatha kupezeka m'magazi kapena cerebrospinal fluid (CSF). Komabe, iyi siyayeso yodalirika yodziwitsa matenda.

MRI yaubongo itha kukhala yothandiza. X-ray pachifuwa nthawi zambiri imawulula zizindikiro za sarcoidosis yamapapu. Mitsempha ya mitsempha ya mitsempha yokhudzidwa imatsimikizira matendawa.


Palibe mankhwala odziwika a sarcoidosis. Chithandizo chimaperekedwa ngati zizindikiro zakulimba kapena zikukulirakulira. Cholinga cha chithandizo ndikuchepetsa zizindikiritso.

Corticosteroids monga prednisone amalembedwa kuti achepetse kutupa. Nthawi zambiri amapatsidwa mpaka zizindikiro zitayamba bwino kapena kutha. Mungafunike kumwa mankhwalawo kwa miyezi, kapena ngakhale zaka.

Mankhwala ena amatha kuphatikiza m'malo mwa mahomoni ndi mankhwala omwe amaletsa chitetezo cha mthupi.

Ngati muli ndi dzanzi, kufooka, kusawona kapena kumva, kapena mavuto ena chifukwa cha kuwonongeka kwa mitsempha pamutu, mungafunike chithandizo chamankhwala, kulumikizana, ndodo, kuyenda kapena chikuku.

Matenda amisala kapena matenda amisala angafunike mankhwala othandizira kukhumudwa, chitetezo, komanso kuthandizidwa mosamala.

Milandu ina imatha yokha m'miyezi 4 mpaka 6. Zina zimapitilira ndikupitilira kwa moyo wonse wamunthuyo. Neurosarcoidosis imatha kupangitsa kuti munthu akhale wolumala kwanthawi yayitali, ndipo nthawi zina, kumwalira.

Zovuta zimasiyanasiyana kutengera gawo lamanjenje lomwe limakhudzidwa ndi momwe mumayankhira chithandizo. Kukula pang'onopang'ono kapena kutayika kwanthawi yayitali kwa mitsempha ndizotheka. Nthawi zambiri, ma brainstem amatha kutenga nawo mbali. Izi zikuwopseza moyo.

Itanani omwe akukuthandizani ngati muli ndi sarcoidosis ndipo matenda aliwonse amanjenje amapezeka.

Pitani kuchipinda chodzidzimutsa kapena itanani nambala yadzidzidzi yakomweko (monga 911) ngati mwadzidzidzi mwataya chidwi, kuyenda, kapena thupi.

Chithandizo chaukali cha sarcoidosis chimazimitsa mphamvu yolimbana ndi chitetezo chamthupi musanawononge misempha yanu. Izi zitha kuchepetsa mwayi woti zizindikiritso zamitsempha zizichitika.

Sarcoidosis - mantha dongosolo

  • Sarcoid, gawo I - x-ray pachifuwa
  • Sarcoid, gawo II - x-ray pachifuwa
  • Sarcoid, gawo IV - x-ray pachifuwa

Iannuzzi MC. Sarcoidosis. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. Wolemba 25. Philadelphia, PA: Elsevier Saunders; 2016: chap 95.

Ibitoye RT, Wilkins A, Mokomera NJ. Neurosarcoidosis: njira yothandizira pakuwunika ndi kuwongolera. J Neurol. 2017; 264 (5): 1023-1028. (Adasankhidwa) PMID: 27878437 www.ncbi.nlm.nih.gov/pubmed/27878437.

Josephson SA, Aminoff MJ. Mavuto amitsempha yama systemic matenda: akulu. Mu: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, olemba. Neurology ya Bradley mu Kuchita Zachipatala. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2016: chap 58.

Krumholz A, Kumadzulo BJ. Sarcoidosis wamanjenje. Mu: Aminoff MJ, Josephson SW, olemba., Eds. Aminoff's Neurology ndi General Medicine. 5th ed. Waltham, MA: Atolankhani a Elsevier Academic; 2014: mutu 49.

Tavee JO, Stern BJ. Neurosarcoidosis. Clin Chifuwa Med. 2015; 36 (4): 643-656. PMID: 26593139 www.ncbi.nlm.nih.gov/pubmed/26593139.

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