Mlembi: William Ramirez
Tsiku La Chilengedwe: 20 Sepitembala 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Kanema: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias ndi mitsempha yaying'ono, yotakata pakhungu. Nthawi zambiri zimakhala zopanda vuto, koma zimatha kuphatikizidwa ndi matenda angapo.

Telangiectasias amatha kukula kulikonse m'thupi. Koma amawoneka mosavuta pakhungu, mamina, komanso azungu amaso. Kawirikawiri, sizimayambitsa zizindikiro. Ma telangiectasias ena amatuluka magazi ndipo amabweretsa mavuto akulu. Telangiectasias amathanso kupezeka muubongo kapena m'matumbo ndipo zimayambitsa mavuto akulu kutuluka magazi.

Zoyambitsa zingaphatikizepo:

  • Rosacea (vuto la khungu lomwe limapangitsa kuti nkhope ikhale yofiira)
  • Kukalamba
  • Vuto ndi majini
  • Mimba
  • Kutuluka kwa dzuwa
  • Mitsempha ya Varicose
  • Kugwiritsa ntchito mafuta a steroid mopitirira muyeso
  • Zovuta kuderalo

Matenda okhudzana ndi izi ndi awa:

  • Ataxia-telangiectasia (matenda omwe amakhudza khungu, kulumikizana bwino, komanso kulumikizana, komanso madera ena amthupi)
  • Matenda a Bloom (matenda obadwa nawo omwe amachititsa kuti thupi likhale lalifupi, khungu limamva za dzuwa, komanso kufiira kwa nkhope)
  • Cutis marmorata telangiectatica congenita (matenda akhungu omwe amayambitsa zigamba zofiira)
  • Therangiectasia yotengera magazi (Osler-Weber-Rendu syndrome)
  • Matenda a Klippel-Trenaunay-Weber (matenda omwe amachititsa kuti vinyo azisunthika pa doko, mitsempha ya varicose, komanso mavuto amtundu wofewa)
  • Nevus flammeus monga doko-vinyo banga
  • Rosacea (khungu lomwe limapangitsa kufiira kwa nkhope)
  • Matenda a Sturge-Weber (matenda omwe amaphatikizira kutayika kwa vinyo wa doko ndi mavuto amanjenje)
  • Xeroderma pigmentosa (matenda omwe khungu komanso minofu yophimba diso imakhudzidwa kwambiri ndi kuwala kwa ultraviolet)
  • Lupus (matenda amthupi)
  • Matenda a CREST (mtundu wa scleroderma womwe umakhudza minofu yambiri pakhungu ndi kwina kulikonse m'thupi ndikuwononga maselo omwe amayenda pamakoma amitsempha yaying'ono)

Itanani wanu wothandizira zaumoyo mukawona zotupa zokulitsa pakhungu, mamina, kapena maso.


Wothandizirayo ayesa mayeso ndikufunsa za zomwe ali nazo, kuphatikiza:

  • Mitsempha yamagazi ili kuti?
  • Kodi amatuluka magazi mosavuta komanso popanda chifukwa?
  • Ndi zisonyezo zina ziti zomwe zilipo?

Mayeso angafunike kuti mupeze kapena mupewe matenda. Mayeso atha kuphatikiza:

  • Kuyesa magazi
  • Kujambula kwa CT
  • Maphunziro a chiwindi
  • Kujambula kwa MRI
  • X-ray

Sclerotherapy ndi chithandizo cha telangiectasias pamapazi. Pochita izi, mankhwala amchere amchere (salt) kapena mankhwala ena amabayidwa mumitsempha ya kangaude pamiyendo. Chithandizo cha laser chimagwiritsidwa ntchito pochizira telangiectasias ya nkhope.

Ectasias yamitsempha; Kangaude angioma

  • Angioma serpiginosum
  • Telangiectasia - miyendo
  • Telangiectasias - mkono wapamwamba

Kelly R, Baker C. Matenda ena amitsempha. Mu: Bolognia JL, Schaffer JV, Cerroni L, olemba. Matenda Opatsirana. Wolemba 4. Philadelphia, PA: Elsevier; 2018: mutu 106.


Patterson JW. Zotupa zamitsempha. Mu: Patterson JW, mkonzi. Matenda a Khungu la Weedon. Wolemba 4. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: chap 38.

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