Matenda a Birt-Hogg-Dubé

Zamkati

• Zithunzi za Birt-Hogg-Dubé Syndrome
• Zizindikiro za Birt-Hogg-Dubé Syndrome
• Chithandizo cha Birt-Hogg-Dubé Syndrome
• Maulalo othandiza:

Birt-Hogg-Dubé Syndrome ndimatenda achilendo omwe amayambitsa zotupa pakhungu, zotupa za impso ndi zotupa m'mapapu.

Pa zimayambitsa Birt-Hogg-Dubé Syndrome amasintha mu jini ya chromosome 17, yotchedwa FLCN, yomwe imasiya kugwira ntchito ngati chotupa chotupa ndipo imayambitsa kuwonekera kwa zotupa mwa anthu.

THE Matenda a Birt-Hogg-Dubé alibe mankhwala ndipo chithandizo chake chimakhala kuchotsa zotupazo komanso kupewa mawonekedwe.

Zithunzi za Birt-Hogg-Dubé Syndrome

M'zithunzizi mutha kuzindikira zotupa pakhungu zomwe zimapezeka mu Birt-Hogg-Dubé Syndrome, zomwe zimayambitsa zotupa zazing'ono zomwe zimazungulira tsitsi.

Zizindikiro za Birt-Hogg-Dubé Syndrome

Zizindikiro za Birt-Hogg-Dubé Syndrome zitha kukhala:

• Zotupa za Benign pakhungu, makamaka nkhope, khosi ndi chifuwa;
• Aimpso zotupa;
• Zotupa za impso za Benign kapena khansa ya impso;
• Zotupa m'mapapo mwanga;
• Kudzikundikira kwa mpweya pakati pa mapapo ndi pleura, komwe kumabweretsa mawonekedwe a pneumothorax;
• Mitundu ya chithokomiro.

Anthu omwe ali ndi Birt-Hogg-Dubé Syndrome amatha kukhala ndi khansa m'malo ena amthupi monga bere, amygdala, mapapo kapena matumbo.

Zilonda zomwe zimapezeka pakhungu zimatchedwa fibrofolliculomas ndipo zimakhala ndi ziphuphu zazing'ono zomwe zimabwera chifukwa chokhala ndi collagen ndi ulusi kuzungulira tsitsi. Nthawi zambiri, chikwangwani ichi pakhungu la Birt-Hogg-Dubé Syndrome chimapezeka pakati pa 30 ndi 40 wazaka zakubadwa.

O matenda a Birt-Hogg-Dubé Syndrome zimatheka pozindikira zizindikilo za matendawa ndi kuyesa kwa majini kuti azindikire kusintha kwa jini la FLNC.

Chithandizo cha Birt-Hogg-Dubé Syndrome

Chithandizo cha Birt-Hogg-Dubé Syndrome sichichiza matendawa, koma chimathandiza kuchepetsa zizindikilo zake ndi zotsatirapo zake m'miyoyo ya anthu.

Zotupa za Benign zomwe zimawoneka pakhungu zitha kuchotsedwa opaleshoni, dermo-abrasion, laser kapena kuvala khungu.

Zotupa zam'mapapo kapena zotupa za impso ziyenera kupewedwa pogwiritsa ntchito makina owerengera, maginito omveka kapena mayeso a ultrasound. Ngati kupezeka kwa zotupa kapena zotupa zikupezeka mu mayeso, ayenera kuchotsedwa opaleshoni.

Nthawi yomwe khansa ya impso imayamba, chithandizo chimayenera kukhala ndi opareshoni, chemotherapy kapena radiation radiation.

Maulalo othandiza:

• Chotupa cha impso
• Pneumothorax