Hugles-Stovin Syndrome Zizindikiro ndi Chithandizo

Zamkati

• Zizindikiro
• Chithandizo
• Zovuta

Matenda a Hugles-stovin ndi osowa kwambiri komanso oopsa omwe amachititsa kuti mitsempha yambiri ikhale ndi mitsempha yambiri m'mapapo mwanga komanso nthawi zambiri za mitsempha yambiri ya m'thupi. Chiyambire kufotokoza kwa matendawa padziko lonse lapansi, anthu ochepera 40 adapezeka ndi chaka cha 2013.

Matendawa amatha kudziwonetsa m'magulu atatu, pomwe woyamba amakhala ndi thrombophlebitis, gawo lachiwiri lokhala ndi zotupa zam'mapapo, ndipo gawo lachitatu ndi lomaliza limadziwika ndikutuluka kwa matenda am'mimba omwe angayambitse chifuwa chamagazi ndi imfa.

Dokotala woyenera kwambiri kuti azindikire ndikuthandizira matendawa ndi rheumatologist ndipo ngakhale chifukwa chake sichikudziwika bwino, amakhulupirira kuti atha kukhala okhudzana ndi systemic vasculitis.

Zizindikiro

Zizindikiro za Hugles-stovin ndi izi:

• Kutsokomola magazi;
• Kupuma kovuta;
• Kumva kupuma movutikira;
• Mutu;
• Kutentha kwakukulu, kosalekeza;
• Kutaya pafupifupi 10% ya kulemera popanda chifukwa chomveka;
• Papilledema, yomwe imachulukitsa papilla yamagetsi yomwe imayimira kuwonjezeka kwa kuthamanga mkati mwa ubongo;
• Kutupa ndi kupweteka kwambiri kwa ng'ombe;
• Masomphenya awiri ndi
• Kugwedezeka.

Nthawi zambiri munthu yemwe ali ndi matenda a Hugles-stovin amakhala ndi zizindikilo kwazaka zambiri ndipo matendawa amatha kusokonezedwa ndi matenda a Behçet ndipo ofufuza ena amakhulupirira kuti matendawa kwenikweni ndi mtundu wa Behçet.

Matendawa samapezeka nthawi zambiri ali mwana ndipo amatha kupezeka ali mwana kapena wachikulire atapereka zizindikiro zomwe zatchulidwazi ndikuyesedwa monga magazi, chifuwa cha X-rays, MRIs kapena computed tomography ya mutu ndi chifuwa, kuphatikiza pa doppler ultrasound kuti muwone magazi ndi mtima. Palibe njira yodziwira matendawa ndipo adotolo ayenera kukayikira matendawa chifukwa chofanana ndi matenda a Behçet, koma osakhala ndi mawonekedwe ake onse.

Zaka za anthu omwe amapezeka ndi matendawa zimasiyanasiyana pakati pa zaka 12 ndi 48.

Chithandizo

Chithandizo cha matenda a Hugles-Stovin sichiri chachindunji, koma adotolo angavomereze kugwiritsa ntchito corticosteroids monga hydrocortisone kapena prednisone, anticoagulants monga enoxaparin, pulse therapy ndi ma immunosuppressants monga Infliximab kapena Adalimumab omwe amachepetsa chiopsezo komanso zotsatirapo zake a aneurysms ndi thrombosis, potero kukonza moyo ndikukhala ochepera kufa.

Zovuta

Matenda a Hugles-Stovin atha kukhala ovuta kuchiza ndipo amatha kufa kwambiri chifukwa chomwe chimayambitsa matendawa sichikudziwika ndipo chifukwa chake chithandizo chamankhwala sichingakhale chokwanira kusunga thanzi la munthu amene wakhudzidwa. Popeza pali anthu ochepa omwe amapezeka padziko lonse lapansi, madokotala nthawi zambiri samadziwa matendawa, omwe angapangitse kuti matenda ndi chithandizo chovuta kwambiri.

Kuphatikiza apo, maanticoagulants amayenera kugwiritsidwa ntchito mosamala kwambiri chifukwa nthawi zina amatha kuonjezera ngozi yotuluka magazi pambuyo poti matenda a aneurysm komanso kutayikira magazi kungakhale kwakukulu kotero kuti kumalepheretsa kusunga moyo.