Kallmann Syndrome ndi chiyani

Zamkati
- Zizindikiro zake ndi ziti
- Zomwe zingayambitse
- Momwe matendawa amapangidwira
- Chithandizo chake ndi chiyani
Matenda a Kallman ndimatenda achilendo omwe amadziwika ndikuchedwa kutha msinkhu komanso kuchepa kapena kusanunkhiza, chifukwa chakuchepa pakupanga mahomoni otulutsa gonadotropin.
Chithandizochi chimakhala ndi kasamalidwe ka ma gonadotropin ndi mahomoni ogonana ndipo amayenera kuchitidwa mwachangu kuti mupewe zovuta zakuthupi ndi zamaganizidwe.

Zizindikiro zake ndi ziti
Zizindikiro zimadalira majini omwe amasintha, chofala kwambiri ndikusowa kapena kuchepetsa kununkhira kwakuchedwa kutha msinkhu.
Komabe, zizindikilo zina zimatha kuchitika, monga khungu khungu, kusintha kwamaso, kugontha, kukamwa kwamphongo, kuphwanya kwa mitsempha ndi minyewa komanso kusapezeka kwa machende kumatumbo.
Zomwe zingayambitse
Matenda a Kallmann amayenda chifukwa cha kusintha kwa majini omwe amaphatikiza mapuloteni omwe amachititsa kuti mitsempha ikule bwino, zomwe zimapangitsa kusintha kwa babu wonyeketsa ndikusintha kwamankhwala otulutsa gonadotropin (GnRH).
Kulephera kwa Congenital GnRH kumatanthauza kuti mahomoni a LH ndi FSH sanapangidwe mokwanira kuti ziwalo zogonana zizipanga testosterone ndi estradiol, mwachitsanzo, kuchedwa kutha msinkhu. Onani zomwe zimasintha m'thupi mukamatha msinkhu.
Momwe matendawa amapangidwira
Ana omwe samayamba msinkhu wogonana ali ndi zaka pafupifupi 13 mwa atsikana ndi azaka 14 mwa anyamata, kapena ana omwe samakula bwino nthawi yaunyamata, ayenera kuyesedwa ndi adotolo.
Dokotala ayenera kusanthula mbiri yamankhwala yamunthuyo, kuyesa thupi ndikupempha kuyeza kwamiyeso ya plasma gonadotropin.
Kuzindikira kumayenera kupangidwa munthawi yake kuti ayambe kulandira mankhwala m'malo mwa mahomoni ndikupewa zovuta zakuthupi ndi zamaganizidwe akuchedwa kutha msinkhu
Chithandizo chake ndi chiyani
Chithandizo mwa amuna chiyenera kuchitika nthawi yayitali, ndikuwongolera chorionic gonadotropin kapena testosterone komanso mwa amayi omwe ali ndi cyclic estrogen ndi progesterone.
Chonde chimatha kubwezeretsedwanso mwa kupatsa ma gonadotropin kapena kugwiritsa ntchito mpope wolowetsedwa kuti utulutse GnRH.