Mlembi: Christy White
Tsiku La Chilengedwe: 7 Meyi 2021
Sinthani Tsiku: 1 Epulo 2025
Anonim
Kallmann Syndrome ndi chiyani - Thanzi
Kallmann Syndrome ndi chiyani - Thanzi

Zamkati

Matenda a Kallman ndimatenda achilendo omwe amadziwika ndikuchedwa kutha msinkhu komanso kuchepa kapena kusanunkhiza, chifukwa chakuchepa pakupanga mahomoni otulutsa gonadotropin.

Chithandizochi chimakhala ndi kasamalidwe ka ma gonadotropin ndi mahomoni ogonana ndipo amayenera kuchitidwa mwachangu kuti mupewe zovuta zakuthupi ndi zamaganizidwe.

Zizindikiro zake ndi ziti

Zizindikiro zimadalira majini omwe amasintha, chofala kwambiri ndikusowa kapena kuchepetsa kununkhira kwakuchedwa kutha msinkhu.

Komabe, zizindikilo zina zimatha kuchitika, monga khungu khungu, kusintha kwamaso, kugontha, kukamwa kwamphongo, kuphwanya kwa mitsempha ndi minyewa komanso kusapezeka kwa machende kumatumbo.

Zomwe zingayambitse

Matenda a Kallmann amayenda chifukwa cha kusintha kwa majini omwe amaphatikiza mapuloteni omwe amachititsa kuti mitsempha ikule bwino, zomwe zimapangitsa kusintha kwa babu wonyeketsa ndikusintha kwamankhwala otulutsa gonadotropin (GnRH).


Kulephera kwa Congenital GnRH kumatanthauza kuti mahomoni a LH ndi FSH sanapangidwe mokwanira kuti ziwalo zogonana zizipanga testosterone ndi estradiol, mwachitsanzo, kuchedwa kutha msinkhu. Onani zomwe zimasintha m'thupi mukamatha msinkhu.

Momwe matendawa amapangidwira

Ana omwe samayamba msinkhu wogonana ali ndi zaka pafupifupi 13 mwa atsikana ndi azaka 14 mwa anyamata, kapena ana omwe samakula bwino nthawi yaunyamata, ayenera kuyesedwa ndi adotolo.

Dokotala ayenera kusanthula mbiri yamankhwala yamunthuyo, kuyesa thupi ndikupempha kuyeza kwamiyeso ya plasma gonadotropin.

Kuzindikira kumayenera kupangidwa munthawi yake kuti ayambe kulandira mankhwala m'malo mwa mahomoni ndikupewa zovuta zakuthupi ndi zamaganizidwe akuchedwa kutha msinkhu

Chithandizo chake ndi chiyani

Chithandizo mwa amuna chiyenera kuchitika nthawi yayitali, ndikuwongolera chorionic gonadotropin kapena testosterone komanso mwa amayi omwe ali ndi cyclic estrogen ndi progesterone.


Chonde chimatha kubwezeretsedwanso mwa kupatsa ma gonadotropin kapena kugwiritsa ntchito mpope wolowetsedwa kuti utulutse GnRH.

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