Mlembi: Roger Morrison
Tsiku La Chilengedwe: 19 Sepitembala 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
Chotupa cha Wilms: ndi chiyani, zizindikiro ndi chithandizo - Thanzi
Chotupa cha Wilms: ndi chiyani, zizindikiro ndi chithandizo - Thanzi

Zamkati

Chotupa cha Wilms, chotchedwanso nephroblastoma, ndi khansa yosawerengeka yomwe imakhudza ana azaka zapakati pa 2 ndi 5, ndipo imachitika pafupipafupi zaka zitatu. Chotupa chamtunduwu chimadziwika ndi kutenga kwa impso imodzi kapena zonse ziwiri ndipo zimatha kuzindikirika kudzera pamawonekedwe olimba pamimba.

Chotupachi nthawi zambiri chimayamba popanda zizindikilo, kuzipeza chikakhala kuti chapita patsogolo kwambiri. Ngakhale atapezeka kuti ndiwokulu kwambiri, pali chithandizo chamankhwala ndipo kuchuluka kwake kumasiyana malinga ndi gawo lomwe chotupacho chidadziwika, ndi mwayi wochiritsidwa.

Zizindikiro zazikulu

Chotupa cha Wilms chimatha kukhala opanda zisonyezo, komabe, zimakhala zachilendo kuwona minyewa yosagundika yomwe siyimapweteka m'mimba mwa mwanayo, ndipo ndikofunikira kuti makolo amutengere mwanayo kwa adotolo kuti akachite.


Zizindikiro zina zomwe zitha kuchitika chifukwa cha izi ndi izi:

  • Kutaya njala;
  • Kutupa m'mimba;
  • Malungo;
  • Nseru kapena kusanza;
  • Pamaso pa magazi mu mkodzo;
  • Kuchuluka kwa magazi;
  • Sinthani momwe mungapumulire.

Chotupa cha Wilms chimakhudza impso imodzi, komabe, pakhoza kukhala kutengapo mbali zonse ziwiri kapena kunyalanyaza ziwalo zina za mwanayo, kukulitsa matenda ake ndikupangitsa zizindikilo zowopsa, monga kutuluka magazi m'maso, kusintha kwa chidziwitso kuvuta kupuma.

Zomwe zingayambitse

Zomwe zimayambitsa chotupa cha Wilms sizinafotokozeredwe bwino, sizikudziwika ngati pali cholowa chobadwa nacho komanso ngati zinthu zachilengedwe monga momwe amayi amapatsira mankhwala ali ndi pakati zimayambitsa chotupachi. Komabe, mitundu ina ya ma syndromes imakhudzana ndikupezeka kwa chotupa cha Wilms, monga matenda a Fraser, matenda a Perlman, Beckwith-Wiedemann syndrome ndi matenda a Li-Fraumeni.


Ena mwa ma syndromes amalumikizidwa ndi kusintha kwa majini ndi kusintha kwa maselo ndipo ali ndi jini inayake, yotchedwa WT1 ndi WT2, ndipo izi zimatha kubweretsa chotupa cha Wilms.

Kuphatikiza apo, ana omwe adabadwa ndi vuto lobadwa nalo amakhala pachiwopsezo chotenga chotupa chotere, monga ana omwe ali ndi cryptorchidism, ndipamene machende samatsikira. Pezani zambiri za momwe mankhwala a cryptorchidism amachitikira.

Momwe matendawa amapangidwira

Kuzindikira koyambirira kumapangidwa ndikuphimba pamimba kuti muwone m'mimba, kuphatikiza pakuwunika zomwe mwana wapereka. Kawirikawiri dokotala wa ana amapempha kuyesa kuyerekezera, monga ultrasound, ultrasound, computed tomography ndi kujambula kwa maginito, kuti aone ngati pali chotupacho.

Ngakhale imatha kukula mwachangu komanso mwakachetechete, chotupacho nthawi zambiri chimadziwika ziwalo zina zisanachitike.

Njira zothandizira

Chotupa cha Wills chitha kuchiritsidwa pogwiritsa ntchito mankhwala oyenera, omwe amaphatikizapo kuchotsa impso zosokonekera, ndikutsatiridwa ndi mankhwala othandizira, omwe amachitidwa ndi chemotherapy ndi radiation radiation. Pochita opaleshoni, adotolo ayenera kusanthula ziwalo zina kuti azindikire zosintha zina ndikuwona metastases, ndipamene chotupacho chimafalikira mbali zina za thupi.


Pakakhala kuwonongeka kwa impso zonse, chemotherapy imachitidwa asanachite opareshoni kotero kuti pamakhala mwayi wambiri kuti impso imodzi izigwira bwino ntchito, popanda kuwonongeka kochuluka. Onani zambiri za chemotherapy komanso momwe zimachitikira.

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