Mlembi: Janice Evans
Tsiku La Chilengedwe: 26 Kulayi 2021
Sinthani Tsiku: 22 Kuni 2024
Anonim
Wokongola dysplasia - Mankhwala
Wokongola dysplasia - Mankhwala

Fibrous dysplasia ndi matenda am'mafupa omwe amawononga ndikusintha mafupa abwinobwino ndi minofu ya mafupa. Fupa limodzi kapena angapo amatha kukhudzidwa.

Fibrous dysplasia nthawi zambiri imachitika ali mwana. Anthu ambiri amakhala ndi zizindikilo akafika zaka 30. Matendawa amapezeka kwambiri mwa akazi.

Fibrous dysplasia imalumikizidwa ndi vuto la majini (kusintha kwa majini) komwe kumayang'anira maselo omwe amapanga mafupa. Kusintha kumachitika mwana akamakula m'mimba. Vutoli silimaperekedwa kuchokera kwa kholo kupita kwa mwana.

Zizindikiro zimatha kuphatikizira izi:

  • Kupweteka kwa mafupa
  • Zilonda za mafupa (zilonda)
  • Matenda a Endocrine (hormone)
  • Kupasuka kapena kupindika kwa mafupa
  • Mtundu wachilendo wachilendo (pigmentation), womwe umachitika ndi matenda a McCune-Albright

Zotupa za mafupa zimatha kutha mwanayo akatha msinkhu.

Wothandizira zaumoyo adzayesa. X-ray ya mafupa amatengedwa. MRI ingalimbikitsidwe.

Palibe mankhwala a fibrous dysplasia. Kuphulika kwa mafupa kapena kupunduka kumathandizidwa pakufunika. Mavuto a mahomoni adzafunika kuthandizidwa.


Maganizo amatengera kukula kwa vutoli komanso zizindikilo zomwe zimachitika.

Kutengera mafupa omwe akhudzidwa, zovuta zaumoyo zomwe zingachitike ndi monga:

  • Ngati fupa la chigaza lakhudzidwa, pakhoza kukhala masomphenya kapena kumva kwakumva
  • Ngati fupa la mwendo likukhudzidwa, pakhoza kukhala zovuta kuyenda komanso zovuta zamagulu monga nyamakazi

Itanani omwe akukuthandizani ngati mwana wanu ali ndi zizindikiro za izi, monga kuphwanya mafupa mobwerezabwereza komanso kufooka kwa mafupa osadziwika.

Akatswiri a mafupa, endocrinology, ndi majini atha kukhala nawo pakuwunika ndi chisamaliro cha mwana wanu.

Palibe njira yodziwika yotetezera fibrous dysplasia. Chithandizochi chimathandiza kupewa zovuta, monga mafupa obwerezabwereza, kuti zithandizire kuchepa.

Yotupa yotupa ya hyperplasia; Idiopathic fibrous hyperplasia; Matenda a McCune-Albright

  • Anterior mafupa anatomy

Czerniak B. Fibrous dysplasia ndi zotupa zokhudzana nazo. Mu: Czerniak B, mkonzi. Mafupa a Dorfman ndi Czerniak. Wachiwiri ed. Philadelphia, PA: Elsevier Saunders; 2016: mutu 8.


Heck RK, PC Yoseweretsa. Zizindikiro za mafupa a Benign ndi zinthu zosatuluka zomwe zimafanana ndi zotupa zamafupa. Mu: Azar FM, Beaty JH, Canale ST, eds. Opaleshoni ya Campbell. Wolemba 13. Philadelphia, PA: Elsevier; 2017: chap 25.

Wogulitsa SN, Nadol JB. Mawonekedwe a Otologic a systemic matenda. Mu: Flint PW, Haughey BH, Lund V, et al, olemba. Cummings Otolaryngology: Opaleshoni ya Mutu ndi Khosi. Lachisanu ndi chimodzi. Philadelphia, PA: Elsevier Saunders; 2015: mutu 149.

Shiflett JM, Perez AJ, kholo la AD. Zilonda za zigaza mwa ana: dermoids, langerhans cell histiocytosis, fibrous dysplasia, ndi lipomas. Mu: Winn HR, mkonzi. Opaleshoni ya Youmans ndi Winn Neurological. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2017: mutu 219.

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