Glanzmann thrombasthenia

Glanzmann thrombasthenia ndimatenda achilendo amwazi wamagazi. Ma Platelet ndi gawo la magazi omwe amathandiza pakumanga magazi.

Glanzmann thrombasthenia imayamba chifukwa cha kusowa kwa mapuloteni omwe nthawi zambiri amakhala pamwamba pa ma platelet. Izi zimafunikira kuti ma platelet agwirizane kuti apange magazi.

Matendawo ndi obadwa nawo, zomwe zikutanthauza kuti adakhalapo kuyambira pomwe adabadwa. Pali zovuta zingapo zamtundu zomwe zingayambitse vutoli.

Zizindikiro zimatha kuphatikizira izi:

• Kutaya magazi kwambiri panthawi yochita opaleshoni komanso pambuyo pake
• Kutuluka magazi m'kamwa
• Kulalata mosavuta
• Kutaya magazi kwambiri
• Kutulutsa magazi m'mphuno komwe sikumatha mosavuta
• Kutuluka magazi kwa nthawi yayitali ndikuvulala pang'ono

Mayesero otsatirawa angagwiritsidwe ntchito kuzindikira vutoli:

• Kuwerengera kwathunthu kwa magazi (CBC)
• Kuyesedwa kwa ma Platelet
• Kusanthula kwama Platelet function (PFA)
• Nthawi ya Prothrombin (PT) ndi nthawi yochepa ya thromboplastin (PTT)

Mayesero ena angafunike. Achibale angafunikirenso kuyesedwa.

Palibe mankhwala enieni a vutoli. Kuika magazi m'maplatelet kungaperekedwe kwa anthu omwe akutuluka magazi kwambiri.

Mabungwe otsatirawa ndi zida zabwino zothandiza kudziwa za Glanzmann thrombasthenia:

• Chidziwitso cha Matenda a Genetic and Rare (GARD) - rarediseases.info.nih.gov/diseases/2478/glanzmann-thrombasthenia
• National Organisation for Rare Disways (NORD) - rarediseases.org/rare-diseases/glanzmann-thrombasthenia

Glanzmann thrombasthenia ndimakhalidwe amoyo wonse, ndipo palibe mankhwala. Muyenera kuchitapo kanthu kuti mupewe magazi ngati muli ndi vutoli.

Aliyense amene ali ndi vuto lakutuluka magazi ayenera kupewa kumwa ma aspirin ndi mankhwala ena osagwiritsa ntchito zotupa (NSAIDs) monga ibuprofen ndi naproxen. Mankhwalawa amatha kupititsa nthawi yamagazi popewa ma platelet kuti asagundane.

Zovuta zingaphatikizepo:

• Kutaya magazi kwambiri
• Kuperewera kwa magazi m'thupi mwa azimayi akusamba chifukwa chakutuluka magazi kwambiri

Imbani wothandizira zaumoyo wanu ngati:

• Mukutha magazi kapena kuvulaza chinthu chosadziwika
• Kutuluka magazi sikuima pambuyo poti mwalandira chithandizo chamankhwala

Glanzmann thrombasthenia ndi cholowa chobadwa nacho. Palibe njira yodziwika yopewera.

Matenda a Glanzmann; Thrombasthenia - Glanzmann

[Adasankhidwa] Bhatt MD, Ho K, Chan AKC. Zovuta zakusokonekera kwa mwana wakhanda. Mu: Hoffman R, Benz EJ, Silberstein LE, et al, olemba. Hematology: Mfundo Zoyambira ndi Zochita. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2018: chap 150.

Nichols WL. Matenda a Von Willebrand ndi zovuta zamagazi zamagazi ndi ntchito yamitsempha. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. Wolemba 25. Philadelphia, PA: Elsevier Saunders; 2016: chap 173.