Matenda obadwa nawo nephrotic

Congenital nephrotic syndrome ndi matenda omwe amapitilira kudzera m'mabanja momwe mwana amapangira mapuloteni mumkodzo ndikutupa kwa thupi.

Matenda obadwa nawo a nephrotic ndi matenda amisala yodziyimira payokha. Izi zikutanthauza kuti kholo lirilonse liyenera kupereka kachilombo kabwinobwino kuti mwanayo atenge matendawa.

Ngakhale njira zobadwa nazo zimakhalapo kuyambira pakubadwa, ndi matenda obadwa nawo nephrotic, zizindikilo za matendawa zimachitika m'miyezi itatu yoyambirira ya moyo.

Matenda obadwa nawo nephrotic ndi mtundu wosowa kwambiri wa matenda a nephrotic.

Nephrotic syndrome ndi gulu lazizindikiro zomwe zimaphatikizapo:

• Mapuloteni mu mkodzo
• Mapuloteni ochepa m'magazi
• Kuchuluka kwa cholesterol
• Magulu apamwamba a triglyceride
• Kutupa

Ana omwe ali ndi vutoli ali ndi puloteni yotchedwa nephrin. Zosefera za impso (glomeruli) zimafunikira puloteni iyi kuti igwire bwino ntchito.

Zizindikiro za matenda a nephrotic ndi monga:

• Tsokomola
• Kuchepetsa mkodzo
• Kuwonekera kwamatope mkodzo
• Kulemera kochepa kubadwa
• Kulakalaka kudya
• Kutupa (thupi lathunthu)

Ultrasound yomwe yachitika kwa mayi wapakati imatha kuwonetsa placenta wokulirapo kuposa wabwinobwino. Placenta ndi chiwalo chomwe chimakula panthawi yapakati kudyetsa mwana wokula.

Amayi oyembekezera amatha kuyezetsa nthawi yomwe ali ndi pakati kuti adziwe ngati ali ndi pakati. Kuyesaku kumayang'ana milingo yayikulu kuposa yachibadwa ya alpha-fetoprotein mu mtundu wa amniotic fluid. Mayeso a chibadwa amagwiritsidwanso ntchito kutsimikizira kuti ali ndi kachilombo ngati kuyezetsa kwake kuli koyenera.

Akabadwa, khanda limawonetsa zizindikilo zakusungika kwamadzimadzi ndikutupa. Wothandizira zaumoyo amamva mawu osazolowereka akamamvera mtima ndi mapapo a mwana ndi stethoscope. Kuthamanga kwa magazi kumatha kukhala kwakukulu. Pakhoza kukhala zizindikiro zakusowa kwa zakudya m'thupi.

Kuwunika kwamkodzo kumawulula mafuta ndi mapuloteni ambiri mumkodzo. Mapuloteni onse m'magazi atha kukhala otsika.

Chithandizo choyambirira komanso champhamvu chimafunika kuti muchepetse vutoli.

Chithandizo chitha kukhala:

• Maantibayotiki oletsa kuteteza matenda
• Mankhwala a magazi otchedwa angiotensin-converting enzyme (ACE) inhibitors ndi angiotensin receptor blockers (ARBs) kuti achepetse kuchuluka kwa mapuloteni omwe amatuluka mkodzo
• Okodzetsa ("mapiritsi amadzi") kuti achotse madzimadzi owonjezera
• Ma NSAID, monga indomethacin, amachepetsa kuchuluka kwa mapuloteni omwe amatuluka mkodzo

Madzi amatha kuchepa kuthana ndi kutupa.

Wothandizira angalimbikitse kuchotsa impso kuti asiye mapuloteni. Izi zingatsatidwe ndi dialysis kapena kumuika impso.

Matendawa amabweretsa matenda, kuperewera kwa zakudya m'thupi, ndi impso. Zitha kubweretsa imfa pofika zaka zisanu, ndipo ana ambiri amamwalira chaka choyamba. Matenda obadwa nawo a nephrotic amatha kuwongoleredwa nthawi zina ndi chithandizo choyambirira komanso chankhanza, kuphatikiza impso zoyambira.

Mavuto amtunduwu ndi awa:

• Pachimake impso kulephera
• Kuundana kwamagazi
• Kulephera kwa impso
• Matenda omaliza a impso
• Pafupipafupi, matenda opatsirana
• Kuperewera kwa zakudya m'thupi ndi matenda okhudzana ndi matendawa

Itanani omwe akukuthandizani ngati mwana wanu ali ndi zizindikiro za matenda obadwa nawo a nephrotic.

Nephrotic syndrome - kobadwa nako

• Thirakiti lachikazi
• Njira yamkodzo wamwamuna

Matenda a Erkan E. Nephrotic. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 545.

Schlöndorff J, Pollak MR. Matenda obadwa nawo a glomerulus. Mu: Yu ASL, Chertow GM, Luyckx VA, Marsden PA, Skorecki K, Taal MW, olemba. Brenner ndi Rector a Impso. 11th ed. Philadelphia, PA: Elsevier; 2020: chap 43.

Vogt BA, Springel T. Impso ndi kwamikodzo ya mwana wakhanda. Mu: Martin RJ, Fanaroff AA, Walsh MC, olemba., Eds. Fanaroff ndi Martin's Neonatal-Perinatal Medicine: Matenda a Mwana wosabadwa ndi Khanda. 11th ed. Philadelphia, PA: Elsevier; 2020: chap 93.