Mucopolysaccharides

Mucopolysaccharides ndi maunyolo ataliatali a mamolekyulu a shuga omwe amapezeka mthupi lonse, nthawi zambiri amakhala mamina ndi madzi ozungulira mafupa. Amatchedwa glycosaminoglycans.

Thupi likalephera kuwononga mucopolysaccharides, vuto lotchedwa mucopolysaccharidoses (MPS) limachitika. MPS imatanthawuza gulu la zovuta zobadwa nazo zamagetsi. Anthu omwe ali ndi MPS alibe chilichonse, kapena chokwanira, cha mankhwala (enzyme) omwe amafunikira kuti athetse maunyolo a shuga.

Mafomu a MPS ndi awa:

• MPS I (Matenda a Hurler; Matenda a Hurler-Scheie; Matenda a Scheie)
• MPS II (matenda a Hunter)
• MPS III (matenda a Sanfilippo)
• MPS IV (matenda a Morquio)

Zamgululi GAG

Kumar V, Abbas AK, Aster JC. Matenda a chibadwa. Mu: Kumar V, Abbas AK, Aster JC, olemba, eds. Ma Robbins ndi Matenda a Cotran Pathologic. 9th ed. Philadelphia, PA: Elsevier Saunders; 2015: mutu 5.

Pyeritz RE. Matenda obadwa nawo a minofu yolumikizana. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. 26 wa. Philadelphia, PA: Elsevier; 2020: chap 244.

Wolemba JW. Mucopolysaccharidoses. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: mutu 107.