Mlembi: Clyde Lopez
Tsiku La Chilengedwe: 17 Kulayi 2021
Sinthani Tsiku: 6 Kuguba 2025
Anonim
Kuluka kwa zala kapena zala zakumapazi - Mankhwala
Kuluka kwa zala kapena zala zakumapazi - Mankhwala

Kuluka kwa zala kapena zala kumatchedwa syndactyly. Limatanthauza kulumikizana kwa zala ziwiri kapena zala ziwiri kapena zochulukirapo. Nthawi zambiri, malowa amalumikizidwa ndi khungu lokha. Nthawi zambiri, mafupa amatha kulumikizana.

Syndactyly amapezeka nthawi zambiri pakuyesa kwa mwana. Mwachizolowezi chake, ukonde umapezeka pakati pa zala zachiwiri ndi zachitatu. Fomuyi nthawi zambiri imachokera kwa makolo ndipo si yachilendo. Syndactyly amathanso kuchitika limodzi ndi zovuta zina zobadwa zokhudzana ndi chigaza, nkhope, ndi mafupa.

Ma intaneti omwe amalumikizidwa nthawi zambiri amapita ku gawo loyamba la chala kapena chala. Komabe, amatha kuthamanga kutalika kwa chala kapena chala.

"Polysyndactyly" imalongosola ulusi komanso kupezeka kwa zala kapena zala zakumaso zowonjezera.

Zina mwazomwe zimayambitsa ndi monga:

  • Matenda a Down
  • Cholowa cholandirana

Zomwe zimachitika kawirikawiri zimaphatikizapo:

  • Matenda a Apert
  • Matenda a Carpenter
  • Matenda a Cornelia de Lange
  • Matenda a Pfeiffer
  • Matenda a Smith-Lemli-Opitz
  • Kugwiritsa ntchito mankhwala a hydantoin panthawi yapakati (fetal hydantoin effect)

Vutoli limapezeka nthawi yobadwa mwanayo ali mchipatala.


Wothandizira zaumoyo adzayesa thupi ndikufunsa za mbiri ya zamankhwala ya mwanayo. Mafunso angaphatikizepo:

  • Ndi zala ziti (zala) zomwe zikukhudzidwa?
  • Kodi pali abale ena omwe ali ndi vutoli?
  • Ndi zisonyezo zina ziti kapena zodetsa nkhawa zomwe zilipo?

Khanda lomwe lili ndi nsalu limatha kukhala ndi zisonyezo zina zomwe palimodzi zitha kukhala zizindikilo za matenda kapena chikhalidwe chimodzi. Vutoli limapezeka chifukwa cha mbiri ya banja, mbiri yazachipatala, komanso kuyezetsa thupi.

Mayesero otsatirawa akhoza kuchitika:

  • Maphunziro a Chromosome
  • Kuyesa kwa labu kuti mufufuze mapuloteni enaake (ma enzyme) ndi zovuta zamagetsi
  • X-ray

Opaleshoni itha kuchitidwa kuti tilekanitse zala kapena zala.

Mgwirizano; Polysyndactyly

Zamgululi RB. Chiwalo chapamwamba. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 701.

Mauck BM, Jobe MT. Kobadwa nako anomalies a dzanja. Mu: Azar FM, Beaty JH, Canale ST, eds. Opaleshoni ya Campbell. Wolemba 13. Philadelphia, PA: Elsevier; 2017: mutu 79.


Mwana-Hing JP, Thompson GH. Matenda obadwa nawo kumtunda ndi kumunsi ndi msana. Mu: Martin RJ, Fanaroff AA, Walsh MC, olemba., Eds. Fanaroff ndi Martin's Neonatal-Perinatal Medicine. 11th ed. Philadelphia, PA: Elsevier; 2020: chap 99.

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