Mlembi: John Stephens
Tsiku La Chilengedwe: 26 Jayuwale 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
Zonse Zokhudza Antiphospholipid Syndrome (Hughes Syndrome) - Thanzi
Zonse Zokhudza Antiphospholipid Syndrome (Hughes Syndrome) - Thanzi

Zamkati

Chidule

Matenda a Hughes, omwe amadziwikanso kuti "sticky blood syndrome" kapena antiphospholipid syndrome (APS), ndimatenda okhaokha omwe amakhudza momwe maselo amwazi wanu amamangirira pamodzi, kapena kuphimba. Hughes syndrome imatengedwa kawirikawiri.

Azimayi omwe amapita padera mobwerezabwereza komanso anthu omwe ali ndi sitiroko asanakwanitse zaka 50 nthawi zina amapeza kuti vuto la Hughes ndi lomwe limayambitsa. Akuti matenda a Hughes amakhudza azimayi katatu kuposa kasanu azimayi.

Ngakhale zomwe zimayambitsa matenda a Hughes sizikudziwika bwinobwino, ofufuza amakhulupirira kuti zakudya, moyo, komanso majini zimatha kuthandizira kukulitsa vutoli.

Zizindikiro za matenda a Hughes

Zizindikiro za matenda a Hughes ndizovuta kuziwona, chifukwa kuundana kwamagazi sichinthu chomwe mutha kuzindikira mosavuta popanda zovuta zina kapena zovuta zina. Nthawi zina matenda a Hughes amayambitsa kuphulika kofiira kapena kutuluka magazi m'mphuno ndi m'kamwa.

Zizindikiro zina zomwe mungakhale ndi Hughes syndrome ndi monga:

  • padera pobereka kapena pobereka mwana
  • magazi aundana m'miyendo mwanu
  • kusokonezeka kwa ischemic (TIA) (kofanana ndi sitiroko, koma popanda zotsatira zaminyewa zaminyewa)
  • sitiroko, makamaka ngati simunakwanitse zaka 50
  • kuchuluka kwa magazi m'magazi ochepa
  • matenda amtima

Anthu omwe ali ndi lupus amakhala ndi matenda a Hughes.


Nthawi zambiri, matenda a Hughes osachiritsidwa amatha kukulira ngati muli ndi zochitika munthawi yomweyo thupi lonse. Izi zimatchedwa matenda oopsa a antiphospholipid, ndipo amatha kuwononga ziwalo zanu komanso kufa.

Zimayambitsa matenda Hughes

Ofufuzawa akugwirabe ntchito kuti amvetsetse zomwe zimayambitsa matenda a Hughes. Koma atsimikiza kuti pamakhala chibadwa chomwe chimasewera.

Matenda a Hughes samaperekedwa mwachindunji kuchokera kwa kholo, momwe magazi ena, monga hemophilia, angakhalire. Koma kukhala ndi wachibale yemwe ali ndi matenda a Hughes kumatanthauza kuti mumatha kukhala ndi vutoli.

N'zotheka kuti jini yolumikizidwa ndi zinthu zina zomwe zimadzichiritsira yokha imayambitsanso matenda a Hughes. Izi zitha kufotokoza chifukwa chake anthu omwe ali ndi vutoli nthawi zambiri amakhala ndi zovuta zina.

Kukhala ndi matenda ena a ma virus kapena bakiteriya, monga E. coli kapena parvovirus, imatha kuyambitsa matenda a Hughes kuti matendawa athe. Mankhwala oletsa khunyu, komanso njira zakulera zakumwa, zitha kuthandizanso kuyambitsa vutoli.


Zinthu zachilengedwezi zimatha kulumikizananso ndi zinthu zina pamoyo wawo - monga kusachita masewera olimbitsa thupi mokwanira komanso kudya zakudya zamafuta ambiri - komanso kuyambitsa matenda a Hughes.

Koma ana ndi akulu omwe alibe matendawa, zochitika pamoyo wawo, kapena kugwiritsa ntchito mankhwala amatha kukhala ndi matenda a Hughes nthawi iliyonse.

Kafukufuku wowonjezereka amafunikira kuti athetse zomwe zimayambitsa matenda a Hughes.

Matenda a Hughes syndrome

Hughes syndrome imapezeka kudzera m'mayeso angapo amwazi. Kuyezetsa magazi uku kumawunika ma antibodies omwe maselo amthupi anu amapanga kuti awone ngati akuchita bwino kapena ngati akulimbana ndi maselo ena athanzi.

Kuyesa magazi wamba komwe kumazindikira matenda a Hughes kumatchedwa antibody immunoassay. Mungafunike kuchita zingapo izi kuti muthetse zina.

Matenda a Hughes atha kuzindikirika molakwika ngati multiple sclerosis chifukwa zinthu ziwirizi zimakhala ndi zofananira. Kuyezetsa bwino kuyenera kudziwa momwe mukudziwira, koma zimatenga nthawi.


Chithandizo cha matenda a Hughes

Matenda a Hughes amatha kuthandizidwa ndi opopera magazi (mankhwala omwe amachepetsa chiopsezo chanu chamagazi).

Anthu ena omwe ali ndi matenda a Hughes samapereka zisonyezo zamagazi ndipo safuna chithandizo chilichonse kupatula aspirin kuti ateteze ngozi yomwe ingayambike.

Mankhwala a Anticoagulant, monga warfarin (Coumadin) atha kulembedwa, makamaka ngati muli ndi mbiri ya thrombosis yakuya.

Ngati mukuyesera kutenga mimba mpaka nthawi yayitali ndikukhala ndi matenda a Hughes, mutha kupatsidwa mankhwala ochepetsa mphamvu ya aspirin kapena mulingo wa tsiku ndi tsiku wa magazi ochepera a heparin.

Amayi omwe ali ndi matenda a Hughes ali ndi mwayi wokwanira 80% kuti abereke mwana mpaka nthawi yomwe angapezeke ndikuyamba mankhwala osavuta.

Zakudya ndi zolimbitsa thupi za matenda a Hughes

Ngati mwapezeka ndi matenda a Hughes, zakudya zopatsa thanzi zimatha kuchepetsa ngozi zomwe zingachitike, monga stroke.

Kudya zakudya zomwe zili ndi zipatso ndi ndiwo zamasamba komanso mafuta ochepa kwambiri ndi shuga zimakupatsani thanzi lamtima, ndikupangitsa magazi kuundana pang'ono.

Ngati mukuchiza matenda a Hughes ndi warfarin (Coumadin), chipatala cha Mayo chimakulangizani kuti musafanane ndi kuchuluka kwa vitamini K komwe mumadya.

Ngakhale mavitamini K ochepa sangakhudze chithandizo chanu, kusiyanasiyana kwa mavitamini K kungapangitse kuti mankhwala anu asinthe moopsa. Broccoli, masamba a Brussels, nyemba za garbanzo, ndi peyala ndi zina mwazakudya zomwe zili ndi vitamini K.

Kuchita masewera olimbitsa thupi nthawi zonse kumathandizanso kuthana ndi vuto lanu. Pewani kusuta ndikukhala ndi kulemera koyenera kwa mtundu wa thupi lanu kuti mtima wanu ndi mitsempha ikhale yolimba komanso yolimbana ndi kuwonongeka.

Maganizo ake

Kwa anthu ambiri omwe ali ndi matenda a Hughes, zizindikilo zimatha kuyang'aniridwa ndi opopera magazi komanso mankhwala a anticoagulant.

Pali zochitika zina zomwe mankhwalawa sagwira ntchito, ndipo njira zina zimafunikira kugwiritsidwa ntchito kuti magazi anu asamange.

Ngati sanalandire chithandizo, matenda a Hughes amatha kuwononga mtima wanu komanso kuwonjezera chiopsezo cha matenda ena, monga kupita padera komanso kupwetekedwa. Chithandizo cha matenda a Hughes ndi cha moyo wonse, chifukwa palibe njira yothetsera vutoli.

Ngati mwakhalapo ndi izi, lankhulani ndi dokotala wanu za kukayezetsa matenda a Hughes:

  • magazi opezeka m'modzi adatsimikizira omwe adayambitsa zovuta
  • kuperewera m'modzi kapena angapo pambuyo pa sabata la 10 la mimba
  • 3 kapena kuposa padera oyambirira mu trimester woyamba wa mimba

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