Matenda a Medullary Cystic

Zamkati

• Mitundu ya MCKD
• Zomwe zimayambitsa MCKD
• Zizindikiro za MCKD
• Kuyesera ndikuzindikira MCKD
• Kuwerengera kwathunthu kwa magazi
• BUN mayeso
• Kutola mkodzo
• Mayeso a creatinine wamagazi
• Uric acid mayeso
• Kupenda kwamadzi
• Kuyesa mayeso
• Chisokonezo
• Kodi MCKD imathandizidwa bwanji?
• Zovuta zakutali za MCKD
• Kodi malingaliro a MCKD ndi otani?

Kodi matenda a impso a medullary cystic ndi chiyani?

Matenda a impso a Medullary cystic (MCKD) ndichinthu chosowa pomwe timatumba tating'onoting'ono todzaza madzi timatchedwa cysts timapanga pakatikati pa impso. Kuphulika kumapezekanso m'matubules a impso. Mkodzo umayenda mu ma tubules kuchokera ku impso komanso kudzera mu dongosolo la mkodzo. Kupunduka kumayambitsa ma tubules osagwira bwino ntchito.

Pofuna kumvetsetsa MCKD, zimathandiza kudziwa pang'ono za impso zanu ndi zomwe amachita. Impso zanu ndi ziwalo ziwiri zooneka ngati nyemba za kukula kwa nkhonya yotsekedwa. Amapezeka mbali zonse za msana wanu, pafupi ndi pakati pa msana wanu.

Impso zanu zimasefa ndikuyeretsa magazi anu - tsiku lililonse, pafupifupi malita 200 amwazi amadutsa mu impso zanu. Magazi oyera amabwerera m'thupi lanu. Zinyalala ndi madzi owonjezera amakhala mkodzo. Mkodzo umatumizidwa ku chikhodzodzo ndipo pamapeto pake umachotsedwa mthupi lanu.

Zowonongeka zoyambitsidwa ndi MCKD zimapangitsa impso kutulutsa mkodzo wosakhazikika mokwanira. Mwanjira ina, mkodzo wanu ndi wamadzi kwambiri ndipo mulibe zinyalala zokwanira. Zotsatira zake, mutha kukodza madzi ambiri kuposa momwe zimakhalira (polyuria) momwe thupi lanu limayesera kutaya zinyalala zonse zowonjezera. Ndipo impso zikatulutsa mkodzo wochuluka, ndiye kuti madzi, sodium, ndi mankhwala ena ofunikira amatayika.

Popita nthawi, MCKD imatha kudzetsa impso.

Mitundu ya MCKD

Juvenile nephronophthisis (NPH) ndi MCKD ndizogwirizana kwambiri. Zonsezi zimayambitsidwa ndi kuwonongeka kwa impso komweko ndipo zimabweretsa zizindikilo zomwezo.

Kusiyanitsa kwakukulu ndi zaka zoyambira. NPH nthawi zambiri imachitika pakati pa zaka 10 mpaka 20, pomwe MCKD ndimatenda oyambira achikulire.

Kuphatikiza apo, pali magawo awiri a MCKD: mtundu wachiwiri (womwe umakhudza achikulire azaka zapakati pa 30 ndi 35) ndikulemba mtundu 1 (umakhudza kwambiri achikulire azaka 60 mpaka 65).

Zomwe zimayambitsa MCKD

NPH ndi MCKD zonse ndizoyambitsa matenda. Izi zikutanthauza kuti muyenera kungopeza jini kuchokera kwa kholo limodzi kuti mukhale ndi vutoli. Ngati kholo lili ndi jini, mwana amakhala ndi mwayi wokwanira 50% kuti alandire ndikukula kwa vutoli.

Kupatula zaka zoyambira, kusiyana kwina kwakukulu pakati pa NPH ndi MCKD ndikuti amayambitsidwa ndi zolakwika zosiyanasiyana zamtundu.

Pomwe timayang'ana kwambiri pa MCKD pano, zambiri zomwe timakambirana zimagwiranso ntchito ku NPH.

Zizindikiro za MCKD

Zizindikiro za MCKD zimawoneka ngati zizindikilo zina zambiri, zomwe zimapangitsa kuti zikhale zovuta kuti munthu adziwe matenda ake. Zizindikirozi ndi monga:

• kukodza kwambiri
• kuchuluka pafupipafupi pokodza usiku (nocturia)
• kuthamanga kwa magazi
• kufooka
• zolakalaka zamchere (chifukwa cha kutayika kwambiri kwa sodium chifukwa cha kukodza kwambiri)

Matendawa akamakula, kulephera kwa impso (komwe kumadziwikanso kuti matenda aimpso) Zizindikiro za kulephera kwa impso zitha kukhala izi:

• kuvulala kapena kutuluka magazi
• kutopa mosavuta
• hiccups pafupipafupi
• mutu
• kusintha kwa khungu (chikaso kapena bulauni)
• kuyabwa pakhungu
• kuphwanya minofu kapena kugwedezeka
• nseru
• kutaya kumverera m'manja kapena m'mapazi
• kusanza magazi
• mipando yamagazi
• kuonda
• kufooka
• kugwidwa
• kusintha kwa malingaliro (chisokonezo kapena kusinthasintha)
• chikomokere

Kuyesera ndikuzindikira MCKD

Ngati muli ndi zizindikiro za MCKD, dokotala wanu atha kuyitanitsa mayeso osiyanasiyana kuti atsimikizire kuti mukudwala. Kuyezetsa magazi ndi mkodzo ndikofunikira kwambiri pozindikira MCKD.

Kuwerengera kwathunthu kwa magazi

Kuwerengera kwathunthu kwamagazi kumayang'ana manambala anu ofiira ofiira, maselo oyera am'magazi, ndi ma platelet. Kuyezetsa kumeneku kumayang'ana kuchepa kwa magazi m'thupi ndi zizindikiro za matenda.

BUN mayeso

Kuyezetsa magazi urea nitrogen (BUN) kumayang'ana kuchuluka kwa urea, mankhwala owonongeka a protein, omwe amakwezedwa pamene impso sizigwira bwino ntchito.

Kutola mkodzo

Kutola kwamikodzo kwamaola 24 kumatsimikizira kukodza kwambiri, kulemba kuchuluka ndi kutayika kwa ma electrolyte, ndikuyeza chilolezo cha creatinine. Chilolezo cha creatinine chidzaulula ngati impso zikuyenda bwino.

Mayeso a creatinine wamagazi

Kuyesedwa kwa magazi kwa creatinine kudzachitika kuti muwone kuchuluka kwanu. Creatinine ndi mankhwala osokoneza bongo omwe amapangidwa ndi minofu, yomwe imasefedwa kunja kwa thupi ndi impso zanu. Izi zimagwiritsidwa ntchito kuyerekezera mulingo wa creatinine wamagazi ndi chilolezo cha impso creatinine.

Uric acid mayeso

Kuyesedwa kwa uric acid kudzachitika kuti muwone kuchuluka kwa uric acid. Uric acid ndi mankhwala omwe amapangidwa thupi lanu likawononga zakudya zina. Uric acid amatuluka mthupi kudzera mumkodzo. Mlingo wa uric acid nthawi zambiri umakhala waukulu mwa anthu omwe ali ndi MCKD.

Kupenda kwamadzi

Kuyeza kwamikodzo kudzachitika pofufuza mtundu, mphamvu yokoka, ndi pH (asidi kapena zamchere) mkodzo wanu. Kuphatikiza apo, malo anu amkodzo adzawunika magazi, mapuloteni, ndi maselo. Kuyesaku kumathandizira adotolo kutsimikizira kuti ali ndi vuto kapena kuthana ndi zovuta zina zomwe zingachitike.

Kuyesa mayeso

Kuphatikiza pa kuyesa magazi ndi mkodzo, dokotala wanu amathanso kuyitanitsa m'mimba / impso CT scan. Kuyesaku kumagwiritsa ntchito kulingalira kwa X-ray kuwona impso ndi mkati mwa mimba. Izi zitha kuthandiza kuthana ndi zina zomwe zingayambitse matenda anu.

Dokotala wanu angafunenso kupanga ultrasound ya impso kuti muwonetse ma cysts pa impso zanu. Izi ndikuzindikira kukula kwa impso.

Chisokonezo

Pofufuza za impso, adotolo kapena akatswiri ena azaumoyo amachotsa kanyama kakang'ono ka impso kuti kakuyese mu labu, pogwiritsa ntchito microscope. Izi zitha kuthandizira kuthana ndi zina zomwe zingayambitse matenda anu, kuphatikiza matenda, kusowa kwachilendo, kapena mabala.

Biopsy imathandizanso dokotala wanu kudziwa gawo la matenda a impso.

Kodi MCKD imathandizidwa bwanji?

Palibe mankhwala a MCKD. Chithandizo cha vutoli chimakhala ndi njira zomwe zimayesetsa kuchepetsa zizindikilo ndikuchepetsa kukula kwa matendawa.

Kumayambiriro kwa matendawa, dokotala angakulimbikitseni kuwonjezera kumwa madzi. Mwinanso mungafunike kutenga chowonjezera mchere kuti mupewe kutaya madzi m'thupi.

Matendawa akamakula, impso zimatha chifukwa. Izi zikachitika, mungafunike kuti mupeze dialysis. Dialysis ndi njira yomwe makina amachotsera zinyalala mthupi zomwe impso sizingathenso kuzisefa.

Ngakhale dialysis ndimankhwala opatsa moyo, anthu omwe ali ndi impso amalephera kuthandizanso impso.

Zovuta zakutali za MCKD

Zovuta za MCKD zimatha kukhudza ziwalo ndi machitidwe osiyanasiyana. Izi zikuphatikiza:

• kuchepa kwa magazi m'thupi (chitsulo chochepa m'magazi)
• kufooka kwa mafupa, komwe kumabweretsa mafupa
• Kupanikizika kwa mtima chifukwa chamadzi am'madzi (mtima tamponade)
• kusintha kwa kagayidwe ka shuga
• congestive mtima kulephera
• impso kulephera
• zilonda zam'mimba ndi m'matumbo
• kutaya magazi kwambiri
• kuthamanga kwa magazi
• osabereka
• mavuto akusamba
• kuwonongeka kwa mitsempha

Kodi malingaliro a MCKD ndi otani?

MCKD imabweretsa matenda a impso kumapeto kwake - mwa kuyankhula kwina kuti kulephera kwa impso kumachitika pamapeto pake. Panthawiyo, muyenera kukhala ndi impso kapena kuikidwa dialysis pafupipafupi kuti thupi lanu liziyenda bwino. Lankhulani ndi dokotala wanu za zomwe mungachite.