Kodi kobadwa nako myasthenia, zizindikiro ndi chithandizo

Zamkati

• Zizindikiro za Kubadwa kwa Myasthenia
• Momwe matendawa amapangidwira
• Kuchiza kwa Congenital Myasthenia
• Kodi kubadwa kwa myasthenia kungachiritsidwe?

Congenital Myasthenia ndi matenda omwe amakhudza kulumikizana kwa mitsempha yam'mimba motero amachititsa kufooka kwa minofu pang'onopang'ono, nthawi zambiri kumamupangitsa kuti ayende pa njinga ya olumala. Matendawa amatha kupezeka muunyamata kapena munthu wamkulu ndipo kutengera mtundu wamitundu yomwe munthuyo ali nayo, amatha kuchiritsidwa pogwiritsa ntchito mankhwala.

Kuphatikiza pa mankhwala omwe adanenedwa ndi a neurologist, physiotherapy imafunikanso kuti ipezenso mphamvu zamankhwala ndikuyendetsa kayendedwe, koma munthuyo amatha kuyenda bwinobwino, osafunikira njinga ya olumala kapena ndodo.

Congenital myasthenia siyofanana ndendende ndi myasthenia gravis chifukwa pa nkhani ya Myasthenia Gravis chomwe chimayambitsa kusintha kwa chitetezo chamthupi cha munthu, pomwe kobadwa nako myasthenia komwe kumayambitsa kusinthika, komwe kumachitika kawirikawiri mwa anthu am'banja limodzi.

Zizindikiro za Kubadwa kwa Myasthenia

Zizindikiro za kubadwa kwa Myasthenia nthawi zambiri zimawoneka mwa makanda kapena azaka zapakati pa 3 ndi 7, koma mitundu ina imawonekera pakati pa zaka 20 mpaka 40, zomwe zingakhale:

Mwa mwana:

• Zovuta kuyamwitsa kapena kuyamwitsa botolo, kutsamwa mosavuta komanso mphamvu zochepa zoyamwa;
• Hypotonia yomwe imadziwonetsera kudzera kufooka kwa manja ndi miyendo;
• Kutulutsa chikope;
• Mgwirizano wolumikizana (kobadwa nako arthrogryposis);
• Kuchepetsa nkhope;
• Kuvuta kupuma ndi kupindika zala ndi milomo;
• Kukula kwachitukuko kukhala, kukwawa ndi kuyenda;
• Ana okulirapo angavutike kukwera masitepe.

Kwa ana, achinyamata kapena achikulire:

• Kufooka kwa miyendo kapena mikono ndikumverera kofewa;
• Zovuta kuyenda ndikufunika kukhala pansi kuti mupumule;
• Pakhoza kukhala kufooka mu minofu ya diso yomwe imatsitsa chikope;
• Kutopa pamene mukuyesetsa pang'ono;
• Pakhoza kukhala scoliosis mu msana.

Pali mitundu 4 yosiyanasiyana yobadwa ndi myasthenia: njira yocheperako, njira yolumikizirana yotsika, kusowa kwakukulu kwa AChR kapena kusowa kwa AChE. Popeza kubadwa kwa njira yocheperako myasthenia kumatha kuwonekera zaka 20 mpaka 30 zakubadwa. Mtundu uliwonse uli ndi mawonekedwe ake ndipo chithandizocho chimatha kusiyanasiyana pakati pa anthu ena chifukwa si onse omwe ali ndi zisonyezo zomwezo.

Momwe matendawa amapangidwira

Kuzindikira kwa Congenital Myasthenia kuyenera kupangidwa kutengera zomwe zawonetsedwa ndipo zitha kutsimikiziridwa ndi mayeso monga kuyesa magazi a CK ndi kuyesa kwa majini, mayeso a antibody kuti atsimikizire kuti si Myasthenia Gravis, komanso electromyography yomwe imayesa mtundu wa chidule. minofu, mwachitsanzo.

Kwa ana okalamba, achinyamata komanso achikulire, adotolo kapena physiotherapist amathanso kuyesa mayeso kuofesi kuti azindikire kufooka kwa minofu, monga:

• Yang'anani padenga kwa mphindi ziwiri, mosasunthika ndikuwona ngati pali kukulirakulira kwavuto loteteza zikope;
• Kwezani manja anu patsogolo, mpaka kutalika kwa phewa, mutagwira malowa kwa mphindi ziwiri ndikuwona ngati ndizotheka kukhalabe ndi chidutswachi kapena mikono yanu ikugwa;
• Kwezani machirawo popanda kuthandizidwa ndi mikono yanu kuposa nthawi imodzi kapena kwezani pampando nthawi zopitilira 2 kuti muwone ngati pali zovuta zochulukirapo pakuchita izi.

Ngati kufooka kwa minofu kukuwonedwa ndipo ndikovuta kuyesa mayeserowa, ndizotheka kuti pali kufooka kwa minofu, komwe kumawonetsa matenda monga myasthenia.

Kuti muwone ngati zolankhulidwazo zakhudzidwanso, mutha kufunsa munthuyo kuti atchule manambala kuyambira 1 mpaka 100 ndikuwona ngati pali kusintha kwa kamvekedwe ka mawu, kulephera kwamawu kapena kuchuluka kwa nthawi pakati pa mawu a nambala iliyonse.

Kuchiza kwa Congenital Myasthenia

Mankhwala amasiyana malinga ndi mtundu wobadwa nawo wa myasthenia womwe munthuyo amakhala nawo koma nthawi zina mankhwala monga acetylcholinesterase inhibitors, Quinidine, Fluoxetine, Ephedrine ndi Salbutamol atha kuwonetsedwa motsogozedwa ndi a neuropediatrician kapena neurologist. Physiotherapy imawonetsedwa ndipo imatha kumuthandiza kuti azimva bwino, kulimbana ndi kufooka kwa minofu ndikupuma bwino, koma sizingathandize popanda mankhwala.

Ana amatha kugona ndi chigoba cha oxygen chotchedwa CPAP ndipo makolo ayenera kuphunzira kupereka chithandizo choyamba pakagwidwa kupuma.

Mu physiotherapy zolimbitsa thupizo ziyenera kukhala zam'mutu komanso zobwerezabwereza koma zimafunikira magulu angapo am'mimba, kuphatikiza opumira ndipo ndi othandiza kwambiri kukulitsa kuchuluka kwa mitochondria, minofu, capillaries ndikuchepetsa ndende ya lactate, osakokana pang'ono.

Kodi kubadwa kwa myasthenia kungachiritsidwe?

Nthawi zambiri, kobadwa nako myasthenia sikungachiritsidwe, komwe kumafunikira chithandizo chamoyo wonse. Komabe, mankhwala ndi physiotherapy zimathandizira kukonza moyo wamunthu, kulimbana ndi kutopa komanso kufooka kwa minofu ndikupewa zovuta monga kuphwanya kwa manja ndi miyendo komanso kutsamwa komwe kumatha kutuluka ndikapuma, ndiye chifukwa chake, moyo ndi wofunikira.

Anthu omwe ali ndi Congenital Myasthenia omwe amabwera chifukwa cha chilema mumtundu wa DOK7 atha kukhala ndi thanzi labwino, ndipo mwachidziwikire akhoza 'kuchiritsidwa' pogwiritsa ntchito mankhwala omwe amagwiritsidwa ntchito kwambiri motsutsana ndi mphumu, salbutamol, koma mwa mapiritsi kapena lozenges. Komabe, mungafunikirebe kuchiritsa mobwerezabwereza.

Munthuyo atakhala ndi Congenital Myasthenia ndipo samalandira chithandizo, amayamba kuchepa mphamvu minyewa, kuyamba kuchepa thupi, kufunikira kugona pakama ndipo amatha kufa chifukwa cholephera kupuma ndichifukwa chake chithandizo chamankhwala ndi physiotherapeutic ndikofunikira chifukwa zonse zitha kusintha moyo wa munthuyo ndi moyo wake wautali.

Njira zina zomwe zimawonjezera vuto la Congenital Myasthenia ndi Ciprofloxacin, Chloroquine, Procaine, Lithium, Phenytoin, Beta-blockers, Procainamide ndi Quinidine motero mankhwala onse ayenera kugwiritsidwa ntchito mothandizidwa ndi azachipatala atazindikira mtundu womwe munthuyo ali nawo.