Kudula porphyria

Zamkati

• Zizindikiro za cutaneous porphyria
• Chithandizo cha cutaneous porphyria

Kuchedwa kwa khungu porphyria ndi mtundu wofala kwambiri wa porphyria womwe umayambitsa zilonda zazing'ono kuti ziwonekere pakhungu lowonekera padzuwa, monga kumbuyo kwa dzanja, nkhope kapena khungu, chifukwa chosowa enzyme yopangidwa ndi chiwindi chomwe chimatsogolera ku kudzikundikira kwa chitsulo pakhungu magazi ndi khungu. Cutaneous porphyria ilibe mankhwala, koma imatha kuwongoleredwa pogwiritsa ntchito mankhwala omwe adalamulidwa ndi dermatologist.

Nthawi zambiri, khungu lochedwa porphyria limapezeka munthu akamakula, makamaka kwa odwala omwe amakonda kumwa mowa kapena omwe ali ndi vuto la chiwindi, monga hepatitis C, mwachitsanzo.

Kuchedwa kwa khungu porphyria nthawi zambiri sikumakhala kobadwa nako, komabe, nthawi zina kumatha kuchoka kwa makolo kupita kwa ana, ndipo upangiri wamtunduwu umalimbikitsidwa musanakhale ndi pakati, ngati pangakhale milandu ingapo m'banjamo.

Zizindikiro za cutaneous porphyria

Chizindikiro choyamba cha cutaneous porphyria ndikuwonekera kwa matuza ang'ono pakhungu lomwe lakhala padzuwa, zomwe zimatenga nthawi kuti zichiritse, komabe, zizindikiro zina zimaphatikizapo:

• Kukula kwakukulu kwa tsitsi pamaso;
• Khungu lolimba m'malo ena, monga mikono kapena nkhope;
• Mkodzo wamdima.

Matuza akatha, mabala kapena mabala angaoneke omwe amatenga nthawi yayitali kuti apole.

Kuzindikira kwa porphyria yocheperako kuyenera kupangidwa ndi dermatologist kudzera m'mayeso amwazi, mkodzo ndi ndowe kuti mutsimikizire kupezeka kwa porphyrin m'maselo, chifukwa ndichinthu chomwe chimapangidwa ndi chiwindi panthawi yamatenda.

Chithandizo cha cutaneous porphyria

Chithandizo cha cutaneous porphyria chiyenera kutsogozedwa ndi dermatologist mogwirizana ndi hepatologist, chifukwa ndikofunikira kuwongolera kuchuluka kwa porphyrin wopangidwa ndi chiwindi. Chifukwa chake, kutengera zomwe wodwalayo ali nazo, chithandizo chitha kuchitidwa ndi mankhwala a khungu, monga chloroquine kapena hydroxychloroquine, kuchotsa magazi pafupipafupi kuti muchepetse ma iron m'maselo kapena kuphatikiza zonse ziwiri.

Kuphatikiza apo, akamalandira chithandizo chake ndikulimbikitsidwa kuti wodwalayo apewe kumwa mowa komanso kuwonekera padzuwa, ngakhale atadziteteza ku dzuwa, ndipo njira yabwino yotetezera khungu ku dzuwa ndikugwiritsa ntchito mathalauza, zoluka zazitali, chipewa ndi magolovesi, mwachitsanzo .