Mlembi: Tamara Smith
Tsiku La Chilengedwe: 26 Jayuwale 2021
Sinthani Tsiku: 19 Meyi 2025
Anonim
Dziwani matenda omwe amachepetsa mafuta m'thupi - Thanzi
Dziwani matenda omwe amachepetsa mafuta m'thupi - Thanzi

Zamkati

Berardinelli-Seipe Syndrome, yomwe imadziwikanso kuti congenital lipodystrophy, ndi matenda osowa omwe amabwera chifukwa chogwiritsa ntchito kwamafuta amthupi mthupi, ndikupangitsa kuti pasakhale mafuta ambiri mthupi, chifukwa amayamba kusungidwa mwa ena monga chiwindi ndi minofu.

Chimodzi mwazinthu zazikuluzikulu za matendawa ndikukula kwa matenda ashuga omwe amayamba nthawi yakutha msinkhu, azaka pafupifupi 8 mpaka 10, ndipo amayenera kuthandizidwa ndi zakudya zopanda mafuta komanso shuga komanso mankhwala omwe amathandiza kuchepetsa matenda a shuga komanso cholesterol.

Zizindikiro

Zizindikiro za Berardinelli-Seipe Syndrome zimalumikizidwa ndi kuchepa kwa minofu yabwinobwino m'thupi, zomwe zimabweretsa mawonekedwe omwe angawonekere mchaka choyamba cha moyo, monga:


  • Cholesterol wambiri ndi triglycerides;
  • Kukaniza kwa insulin ndi matenda ashuga;
  • Chin, manja ndi mapazi akulu ndi otalikirapo;
  • Kuchuluka minofu;
  • Kukulitsa kwa chiwindi ndi ndulu, kuchititsa kutupa m'mimba;
  • Mavuto amtima;
  • Kukula mwachangu;
  • Kuchulukitsa kwakulakalaka, koma ndi kuonda;
  • Kusamba kosasamba;
  • Tsitsi lakuthwa, louma.

Kuphatikiza apo, zizindikilo monga kuthamanga kwa magazi, zotupa m'mimba mwake komanso zotupa m'mbali mwa khosi, pafupi ndi kamwa, zitha kuwonekeranso. Zizindikirozi zimatha kuwonedwa kuyambira ali mwana, zimawonekera kwambiri kutha msinkhu.

Kuzindikira ndi Chithandizo

Kuzindikira kwa matendawa kutengera kuwunika kwa zomwe wodwalayo ali nazo komanso mayeso omwe angazindikire mavuto a cholesterol, chiwindi, impso ndi matenda ashuga.

Kuchokera kutsimikiziridwa kwa matendawa, chithandizochi makamaka chimangoyang'anira matenda a shuga ndi cholesterol komanso kupewa zovuta za matendawa, ndipo mankhwala monga Metformin, insulin ndi Simvastatin atha kugwiritsidwa ntchito.


Kuphatikiza apo, muyeneranso kudya chakudya chamafuta ochepa, omega-3 chothandizira kuchepetsa mafuta m'thupi, kuphatikiza pakuwongolera kumwa shuga ndi chakudya chosavuta, monga mpunga, ufa ndi pasitala, kuti muthandizire kuchepetsa matenda ashuga. Onani zomwe mungadye mu matenda ashuga.

Zovuta

Zovuta za Berardinelli-Seipe Syndrome zimadalira kutsatira kwa chithandizo ndi kuyankha kwa thupi la wodwalayo kumankhwala omwe amagwiritsidwa ntchito, ndi mafuta ochulukirapo m'chiwindi ndi chiwindi, kukulitsa kukula muubwana, kutha msinkhu kutha msana ndi zotupa zam'mafupa, zomwe zimayambitsa kusweka pafupipafupi .

Kuphatikiza apo, zimakhalanso zachidziwikire kuti matenda ashuga omwe amapezeka munthendayi amatsogolera ku zovuta monga masomphenya, mavuto a impso komanso chiopsezo chowonjezeka cha matenda amtima.

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