Zizindikiro za hemophilia, matenda ndi kukayika komwe kumachitika

Zamkati

• Mitundu ya hemophilia
• Zizindikiro za hemophilia
• Momwe mungatsimikizire matendawa
• Mafunso wamba okhudzana ndi hemophilia
• 1. Kodi hemophilia imafala kwambiri mwa amuna?
• 2. Kodi hemophilia nthawi zonse imachokera ku cholowa?
• 3. Kodi hemophilia imafalikira?
• 4. Kodi munthu yemwe ali ndi hemophilia angakhale ndi moyo wabwinobwino?
• 5. Ndani ali ndi hemophilia angatenge ibuprofen?
• 6. Kodi munthu yemwe ali ndi hemophilia angathe kulemba ma tattoo kapena kuchitidwa opaleshoni?

Hemophilia ndi chibadwa komanso matenda obadwa nawo, ndiye kuti, amapatsira kuchokera kwa makolo kupita kwa ana, omwe amadziwika ndi kutuluka magazi kwanthawi yayitali chifukwa chakuchepa kapena kuchepa kwa zinthu za VIII ndi IX m'magazi, zomwe ndizofunikira popanga magazi.

Chifukwa chake, pakakhala zosintha zokhudzana ndi michereyi, ndizotheka kuti pamakhala magazi, omwe amatha kukhala amkati, ndikutuluka magazi, mphuno, mkodzo kapena ndowe, kapena zipsera m'thupi, mwachitsanzo.

Ngakhale kulibe mankhwala, hemophilia imakhala ndi chithandizo, chomwe chimachitika ndi jakisoni wa periodic wokhala ndi chotseketsa chomwe chimasowa mthupi, kupewa magazi kapena nthawi iliyonse yotuluka magazi, yomwe imafunika kuthetsedwa mwachangu. Mvetsetsani momwe chithandizo cha hemophilia chiyenera kukhalira.

Mitundu ya hemophilia

Hemophilia imatha kuchitika m'njira ziwiri, zomwe, ngakhale zili ndi zizindikilo zofananira, zimayambitsidwa chifukwa chosowa magawo osiyanasiyana amwazi:

• Hemophilia A:ndiwo mtundu wofala kwambiri wa hemophilia, wodziwika ndi kusowa kwa coagulation factor VIII;
• Hemophilia B:zimayambitsa kusintha pakupanga kwa coagulation factor IX, ndipo imadziwikanso kuti matenda a Khrisimasi.

Zomwe zimayambitsa kugundana ndi mapuloteni omwe amapezeka m'magazi, omwe amatsegulidwa nthawi iliyonse yomwe mtsempha wamagazi umaphulika, kuti magazi azikhala. Chifukwa chake, anthu omwe ali ndi hemophilia amadwala magazi omwe amatenga nthawi yayitali kuti awongolere.

Pali zoperewera pazinthu zina zam'magazi, zomwe zimayambitsanso magazi ndipo zimatha kusokonezedwa ndi hemophilia, monga kuchepa kwa factor XI, yotchuka yotchedwa mtundu C hemophilia, koma yomwe imasiyana pamitundu pakusintha kwa majini ndi mawonekedwe opatsirana.

Zizindikiro za hemophilia

Zizindikiro za haemophilia zitha kuzindikirika Logos mzaka zoyambirira za kubadwa kwa mwana, komabe amathanso kudziwika pa nthawi yakutha msinkhu, unyamata kapena munthu wamkulu, makamaka ngati hemophilia imakhudzana ndi kuchepa kwa zinthu zowumitsa magazi. Chifukwa chake, zizindikilo zazikulu zomwe zitha kuwonetsa kuti ali ndi hemophilia ndi izi:

• Kuwonekera kwa mawanga ofiira pakhungu;
• Kutupa ndi kupweteka m'malo olumikizirana mafupa;
• Kutuluka mwadzidzidzi, popanda chifukwa, monga chingamu kapena mphuno, mwachitsanzo;
• Magazi pakubadwa kwa mano oyamba;
• Kutuluka magazi kumakhala kovuta kusiya pambuyo pocheka kapena opaleshoni;
• Mabala omwe amatenga nthawi yayitali kuti achiritse;
• Kuchuluka komanso kusamba kwakanthawi.

Mtundu wa hemophilia wovuta kwambiri, kuchuluka kwa zizindikilo komanso kuwonekera msanga, chifukwa chake, hemophilia yayikulu imapezeka mwa mwana, m'miyezi yoyambirira ya moyo, pomwe hemophilia wowerengeka nthawi zambiri amakayikiridwa miyezi ingapo yoyambirira ya moyo wazaka 5, kapena mwana akayamba kuyenda ndikusewera.

Haemophilia wofatsa, komano, amatha kupezeka atakula, pomwe munthuyo amenyedwa mwamphamvu kapena pambuyo pochita monga kuchotsera mano, komwe kutuluka magazi kumatchulidwa bwino.

Momwe mungatsimikizire matendawa

Kuzindikira kwa hemophilia kumachitika pambuyo pofufuza ndi a hematologist, yemwe amafunsa mayeso omwe amafufuza momwe magazi angagwiritsire ntchito magazi, monga nthawi yotseka, yomwe imayang'ana nthawi yomwe magazi amatenga magazi, komanso kuyeza kwa kupezeka kwa zinthu oundana ndi milingo yake m'magazi.

Zinthu zotseka ndizofunikira mapuloteni amwazi, omwe amayamba kugwira ntchito pakakhala magazi, kuti asiye. Kupezeka kwa zinthu izi kumayambitsa matenda, monga mtundu wa A hemophilia, womwe umayamba chifukwa chakusowa kapena kuchepa kwa factor VIII, kapena mtundu wa B hemophilia, momwe IX ilili yochepa. Mvetsetsani momwe coagulation imagwirira ntchito.

Mafunso wamba okhudzana ndi hemophilia

Mafunso ena okhudzana ndi hemophilia ndi awa:

1. Kodi hemophilia imafala kwambiri mwa amuna?

Ma hemophilia osakwanira kugundana amapezeka pa X chromosome, yomwe imadziwika mwa amuna komanso yophunzitsidwa ndi akazi. Chifukwa chake, kuti akhale ndi matendawa, mwamunayo amangofunika kulandira 1 chromosome X yokhudzidwa, kuchokera kwa mayi, pomwe mkazi kuti adziwe matendawa, ayenera kulandira ma chromosomes awiri omwe akhudzidwa, chifukwa chake, matendawa amapezeka kwambiri amuna.

Ngati mayiyo ali ndi 1 chokha chokhacho cha X chromosome, chotengera kwa kholo lililonse, adzakhala wonyamula, koma sangakhale ndi matendawa, popeza X chromosome ina imalipira kulumala, komabe, ali ndi mwayi wokhala ndi mwana 25% matendawa.

2. Kodi hemophilia nthawi zonse imachokera ku cholowa?

Pafupifupi 30% yamatenda a hemophilia, palibe mbiri yabanja yamatendawa, omwe atha kukhala chifukwa chakusintha kwachilengedwe mu DNA ya munthuyo. Zikatere, akuti munthuyo watenga hemophilia, koma kuti atha kupatsirabe ana ake, monganso wina aliyense amene ali ndi hemophilia.

3. Kodi hemophilia imafalikira?

Hemophilia siyopatsirana, ngakhale itagwirizana mwachindunji ndi magazi a munthu wonyamula kapena ngakhale kuthiridwa magazi, chifukwa izi sizimasokoneza mapangidwe amwazi wa munthu aliyense kudzera m'mafupa.

4. Kodi munthu yemwe ali ndi hemophilia angakhale ndi moyo wabwinobwino?

Mukamamwa njira yodzitetezera, m'malo mwa zinthu zowumitsa magazi, munthu yemwe ali ndi hemophilia amatha kukhala ndi moyo wabwinobwino, kuphatikiza masewera.

Kuphatikiza pa chithandizo chopewa ngozi, chithandizo chitha kuchitidwa pakakhala magazi, kudzera mu jakisoni wazinthu zotseka, zomwe zimapangitsa kuti magazi aziundana komanso kupewa magazi ambiri, kuchitidwa molingana ndi malangizo a hematologist.

Kuphatikiza apo, nthawi iliyonse yomwe munthu achite opaleshoni, kuphatikiza kuchotsa mano ndi kudzaza, mwachitsanzo, ndikofunikira kupanga milingo yopewa.

5. Ndani ali ndi hemophilia angatenge ibuprofen?

Mankhwala monga Ibuprofen kapena omwe ali ndi acetylsalicylic acid omwe akupangidwa sayenera kulowetsedwa ndi anthu omwe amapezeka kuti ali ndi hemophilia, chifukwa mankhwalawa amatha kusokoneza kutsekedwa kwa magazi ndikusilira kutuluka kwa magazi, ngakhale kugwirana kwagwiritsidwa ntchito.

6. Kodi munthu yemwe ali ndi hemophilia angathe kulemba ma tattoo kapena kuchitidwa opaleshoni?

Yemwe amapezeka ndi hemophilia, mosatengera mtundu ndi kuuma kwake, atha kupeza ma tattoo kapena njira zochitira opareshoni, komabe malingaliro ake ndikuti mulumikizane ndi akatswiri anu ndikuwapatsa coagulant factor isanachitike, kupewa magazi ambiri, mwachitsanzo.

Kuphatikiza apo, pankhani yolemba ma tattoo, anthu ena omwe ali ndi hemophilia adanenanso kuti njira yochiritsira ndikumva kuwawa pambuyo pochita izi zidali zochepa pomwe adazigwiritsa ntchito asanalembe tattoo. Ndikofunikanso kufunafuna kukhazikitsidwa kosavomerezeka ndi ANVISA, zoyera komanso zopanda kanthu komanso zoyera, popewa zovuta zilizonse.