Fasciitis wachisoni

Eosinophilic fasciitis (EF) ndi matenda omwe minofu yomwe ili pansi pa khungu komanso paminyewa, yotchedwa fascia, imayamba kutupa, kutupa komanso kukhuthala. Khungu lomwe lili m'manja, miyendo, khosi, pamimba kapena pamapazi limatha kutupa msanga. Matendawa ndi osowa kwambiri.

EF imatha kuwoneka yofanana ndi scleroderma, koma siyokhudzana. Mosiyana ndi scleroderma, mu EF, zala sizikukhudzidwa.

Chifukwa cha EF sichidziwika. Nthawi zambiri zachitika mutatenga ma L-tryptophan supplements. Mwa anthu omwe ali ndi vutoli, maselo oyera am'magazi, otchedwa eosinophil, amakhala m'misempha ndi minyewa. Eosinophils amalumikizidwa ndi zovuta zomwe zimachitika. Matendawa amapezeka kwambiri kwa anthu azaka 30 mpaka 60.

Zizindikiro zimaphatikizapo:

• Chikondi ndi kutupa kwa khungu m'manja, miyendo, kapena nthawi zina (nthawi zambiri mbali zonse za thupi)
• Nyamakazi
• Matenda a Carpal
• Kupweteka kwa minofu
• Khungu lakuthwa lomwe limawoneka ngati lophimbidwa

Mayeso omwe angachitike ndi awa:

• CBC ndi masiyanidwe
• Gamma globulins (mtundu wa chitetezo cha mthupi)
• Mlingo wa sedimentation wa erythrocyte (ESR)
• MRI
• Kutulutsa minofu
• Chikopa cha khungu (biopsy iyenera kuphatikizira minofu yakuya ya fascia)

Corticosteroids ndi mankhwala ena opondereza chitetezo cha mthupi amagwiritsidwa ntchito kuthetsa zizindikilo. Mankhwalawa ndi othandiza kwambiri mukayamba matendawa koyambirira. Mankhwala osagwiritsidwa ntchito poletsa kutupa (NSAIDs) amathanso kuthandizira kuchepetsa zizindikilo.

Nthawi zambiri, vutoli limatha pakatha zaka 1 mpaka 3. Komabe, zizindikilo zimatha kukhala nthawi yayitali kapena kubwerera.

Matenda a nyamakazi ndi vuto losowa la EF. Anthu ena amatha kudwala matenda a magazi kapena khansa yokhudzana ndi magazi, monga aplastic anemia kapena leukemia. Maganizo ake ndi oyipa kwambiri ngati matenda amwazi atuluka.

Itanani omwe akukuthandizani ngati muli ndi zodabwitsazi.

Palibe njira yodziwika yopewera.

Matenda a Shulman

• Minofu yakunja yakunja

Aronson JK. Yesani. Mu: Aronson JK, mkonzi. Zotsatira zoyipa za Meyler za Mankhwala Osokoneza bongo. Wolemba 16. Waltham, MA: Elsevier BV ;; 2016: 220-221.

James WD, Elston DM, Chitani JR, Rosenbach MA, Neuhaus IM. Matenda othandizira. Mu: James WD, Elston DM, Tsatirani JR, Rosenbach MA, Neuhaus IM, eds. Matenda a Andrews a Khungu: Clinical Dermatology. Wolemba 13. Philadelphia, PA: Elsevier; 2020: mutu 8.

Lee LA, Werth VP. Khungu ndi matenda enaake ophwanya. Mu: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, olemba. Kelley ndi Firestein's Bookbook of Rheumatology. 10th ed. Philadelphia, PA: Elsevier; 2017: mutu 43.

Pinal-Fernandez I, Selva-O 'Callaghan A, Grau JM. Kuzindikira ndi kugawa kwa eosinophilic fasciitis. Pangani Auto Rev. 2014; 13 (4-5): 379-382. PMID: 24424187 www.ncbi.nlm.nih.gov/pubmed/24424187. (Adasankhidwa)

National Organisation for Rare Disrupt. Fasciitis wachisoni. rarediseases.org/rare-diseases/eosinophilic-fasciitis/. Idasinthidwa 2016. Idapezeka pa Marichi 6, 2017.