Polycythemia - wakhanda
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Polycythemia imatha kuchitika ngati pali maselo ofiira ambiri (RBCs) m'magazi a khanda.
Kuchuluka kwa ma RBC m'magazi a khanda amatchedwa "hematocrit." Izi zikaposa 65%, polycythemia imakhalapo.
Polycythemia imatha chifukwa cha zinthu zomwe zimayamba asanabadwe. Izi zingaphatikizepo:
- Chedwerani pakumenyetsa chingwe cha umbilical
- Matenda ashuga mwa mayi wobala mwana
- Matenda obadwa nawo komanso mavuto amtundu
- Oxygen yochepa kwambiri yofika pamatenda amthupi (hypoxia)
- Matenda a mapasa amapasa magazi (amapezeka magazi akamayenda kuchokera kumapasa awiri kupita kumzake)
Ma RBC owonjezera amatha kuchepetsa kapena kuletsa kuyenda kwa magazi m'mitsempha yaying'ono kwambiri yamagazi. Izi zimatchedwa hyperviscosity. Izi zitha kubweretsa kufa kwa minofu chifukwa chosowa mpweya. Magazi otsekedwawa amatha kukhudza ziwalo zonse, kuphatikizapo impso, mapapo, ndi ubongo.
Zizindikiro zimaphatikizapo:
- Kugona kwambiri
- Mavuto akudya
- Kugwidwa
Pakhoza kukhala zizindikilo za mavuto a kupuma, kulephera kwa impso, shuga wotsika magazi, kapena jaundice wakhanda.
Ngati mwanayo ali ndi zizindikilo zakusokonekera kwa magazi, ayesedwa magazi kuti awerenge kuchuluka kwa ma RBCs. Mayesowa amatchedwa hematocrit.
Mayesero ena atha kuphatikizira:
- Mpweya wamagazi kuti muwone kuchuluka kwa oxygen m'magazi
- Shuga wamagazi (glucose) kuti muwone ngati shuga wamagazi ochepa
- Blood urea nitrogen (BUN), chinthu chomwe chimapangidwa mapuloteni akawonongeka
- Zachilengedwe
- Kupenda kwamadzi
- Bilirubin
Mwanayo amayang'aniridwa chifukwa cha zovuta zakukhudzidwa. Madzi amatha kuperekedwa kudzera mumitsempha. Kusinthana magazi pang'ono nthawi zina kumachitabe nthawi zina. Komabe, palibe umboni wochepa wosonyeza kuti izi ndizothandiza. Ndikofunikira kwambiri kuthana ndi zomwe zimayambitsa polycythemia.
Malingaliro ake ndiabwino kwa makanda omwe ali ndi chidwi chochepa. Zotsatira zabwino ndizothekanso kwa makanda omwe amalandila chithandizo chifukwa cha kukhudzika mtima kwambiri. Malingaliro adzadalira makamaka chifukwa cha vutoli.
Ana ena atha kusintha pang'ono pang'ono. Makolo ayenera kulumikizana ndi omwe amawasamalira ngati akuganiza kuti mwana wawo akuwonetsa kuti akuchedwa kukula.
Zovuta zingaphatikizepo:
- Imfa ya minofu yamatumbo (necrotizing enterocolitis)
- Kuchepetsa kuyendetsa bwino kwamagalimoto
- Impso kulephera
- Kugwidwa
- Kukwapula
Neonatal polycythemia; Hyperviscosity - wakhanda
Maselo amwazi
Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM. Matenda amwazi. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 124.
Letterio J, Pateva I, Petrosiute A, Ahuja S.Hematologic ndi zovuta za oncologic m'mimba mwa mwana wosabadwayo. Mu: Martin RJ, Fanaroff AA, Walsh MC, olemba., Eds. Fanaroff ndi Martin's Neonatal-Perinatal Medicine. 11th ed. Philadelphia, PA: Elsevier; 2020: chap 79.
Tashi T, Prchal JT. Polycythemia. Mu: Lanzkowsky P, Lipton JM, Fish JD, olemba. Lanzkowsky's Manual of Pediatric Hematology ndi Oncology. Lachisanu ndi chimodzi. Cambridge, MA: Atolankhani a Elsevier Academic; 2016: chap 12.