Von Willebrand matenda

Matenda a Von Willebrand ndi omwe amafala kwambiri kubadwa kwa magazi.

Matenda a Von Willebrand amayamba chifukwa chosowa kwa von Willebrand factor. Von Willebrand factor imathandiza kuti magazi am'magazi azigundana pamodzi ndikumamatira kukhoma lamitsempha yamagazi, zomwe ndizofunikira kuti magazi azigwirizana bwino. Pali mitundu ingapo ya matenda a von Willebrand.

Mbiri yabanja yokhudza kutuluka magazi ndichomwe chimayambitsa ngozi.

Zizindikiro zimaphatikizapo:

• Kutuluka magazi kosazolowereka
• Kutuluka magazi m'kamwa
• Kulalata
• Kutulutsa magazi m'mphuno
• Ziphuphu pakhungu

Zindikirani: Amayi ambiri omwe amakhala ndi msambo wofika nthawi yayitali alibe matenda a von Willebrand.

Matenda a Von Willebrand atha kukhala ovuta kuwazindikira. Kuchuluka kwa zinthu za Low von Willebrand ndikutuluka magazi sizitanthauza kuti muli ndi matenda a von Willebrand.

Kuyesa komwe kungachitike kuti mupeze matendawa ndi awa:

• Nthawi yokhetsa magazi
• Kulemba magazi
• Mulingo wa VIII
• Kusanthula kwama Platelet
• Kuwerengera kwa Platelet
• Kuyesa kwa Ristocetin cofactor
• Von Willebrand amayesa mayeso ena

Chithandizo chitha kuphatikizira DDAVP (desamino-8-arginine vasopressin). Ndi mankhwala okweza mulingo wa von Willebrand ndikuchepetsa mwayi wakutaya magazi.

Komabe, DDAVP siyigwira ntchito mitundu yonse yamatenda a von Willebrand. Kuyesedwa kuyenera kuchitidwa kuti mudziwe mtundu wa von Willebrand womwe muli nawo. Ngati mukufuna kuchitidwa opaleshoni, dokotala wanu akhoza kukupatsani DDAVP musanachite opareshoni kuti muwone ngati milingo yanu ya von Willebrand ikuwonjezeka.

Mankhwala a Alphanate (antihemophilic factor) amavomerezedwa kuti achepetse magazi mwa anthu omwe ali ndi matendawa omwe amafunika kuchitidwa opaleshoni kapena njira ina iliyonse yovuta.

Madzi a m'magazi kapena chinthu china cha VIII chingagwiritsidwenso ntchito kuchepetsa magazi.

Kutaya magazi kumatha kuchepa panthawi yapakati. Amayi omwe ali ndi vutoli nthawi zambiri samakhala ndi magazi ochulukirapo panthawi yobereka.

Matendawa amapatsirana kudzera m'mabanja. Upangiri wa chibadwa ungathandize oyembekezera kukhala makolo kuti amvetse kuopsa kwa ana awo.

Kuthira magazi kumatha kuchitika mutatha opaleshoni kapena mukakoka dzino.

Aspirin ndi mankhwala ena osakanikirana ndi kutupa (NSAIDs) amatha kukulitsa vutoli. Musamamwe mankhwalawa musanalankhule ndi wothandizira zaumoyo wanu.

Itanani omwe akukuthandizani ngati magazi akutuluka popanda chifukwa.

Ngati muli ndi matenda a von Willebrand ndipo mukuyenera kuchitidwa opaleshoni kapena muli pangozi, onetsetsani kuti inu kapena banja lanu mumauza omwe akukuthandizani za matenda anu.

Kusokonezeka kwa magazi - von Willebrand

• Mapangidwe a magazi
• Kuundana kwamagazi

Chigumula VH, Scott JP. Von Willebrand matenda. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 504.

James P, Rydz N. Kapangidwe, biology, ndi majini a von Willebrand factor. Mu: Hoffman R, Benz EJ, Silberstein LE, et al, olemba. Hematology: Mfundo Zoyambira ndi Zochita. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2018: mutu 138.

Neff AT. Matenda a Von Willebrand ndi zovuta zamagazi zamagazi ndi ntchito yamitsempha. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. 26 wa. Philadelphia, PA: Elsevier; 2020: chap 164.

Samuels P. Zovuta za hematologic za pakati. Mu: Landon MB, Galan HL, Jauniaux ERM et al, eds. Obstetrics a Gabbe: Mimba Yachibadwa ndi Mavuto. 8th ed. Philadelphia, PA: Elsevier; 2021: mutu 49.