Mlembi: Joan Hall
Tsiku La Chilengedwe: 5 Febuluwale 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
Cholowa elliptocytosis - Mankhwala
Cholowa elliptocytosis - Mankhwala

Hereditary elliptocytosis ndi vuto lomwe limadutsa m'mabanja momwe maselo ofiira amapangidwa modabwitsa. Ndizofanana ndi mikhalidwe ina yamagazi monga cholowa cha spherocytosis ndi cholowa cha ovalocytosis.

Elliptocytosis imakhudza pafupifupi 1 mwa anthu 2,500 aliwonse ochokera kumpoto kwa Europe. Ndizofala kwambiri mwa anthu ochokera ku Africa ndi ku Mediterranean. Mutha kukhala ndi izi ngati wina m'banja mwanu adakhalapo.

Zizindikiro zimaphatikizapo:

  • Kutopa
  • Kupuma pang'ono
  • Khungu lachikaso ndi maso (jaundice). Pitirizani kwa nthawi yayitali khanda.

Kuyesedwa ndi wothandizira zaumoyo wanu kumatha kuwonetsa ntchentche zokulitsa.

Zotsatira zotsatirazi zingathandize kuzindikira vutoli:

  • Mulingo wa Bilirubin ukhoza kukhala wapamwamba.
  • Kupaka magazi kumatha kuwonetsa maselo ofiira ofiira elliptical.
  • Kuwerengera kwathunthu kwa magazi (CBC) kumatha kuwonetsa kuchepa kwa magazi kapena zizindikiritso zakufa kwa maselo ofiira.
  • Lactate dehydrogenase mulingo akhoza kukhala wokwera.
  • Kujambula kwa ndulu kumatha kuwonetsa ndulu.

Palibe chithandizo chofunikira pamavuto pokhapokha kuchepa kwa kuchepa kwa magazi m'thupi kapena kuchepa kwa magazi m'thupi. Kuchita opaleshoni kuchotsa ndulu kumachepetsa kuchepa kwa maselo ofiira a magazi.


Anthu ambiri omwe ali ndi cholowa cha elliptocytosis alibe mavuto. Nthawi zambiri samadziwa kuti ali ndi vutoli.

Elliptocytosis nthawi zambiri imakhala yopanda vuto. Nthawi zochepa, osachepera 15% yama cell ofiira ofiira amakhala ngati elliptical. Komabe, anthu ena atha kukhala ndi zovuta zomwe maselo ofiira amang'ambika. Izi zimatha kuchitika ngati ali ndi kachilombo ka HIV. Anthu omwe ali ndi matendawa amatha kuchepa magazi, jaundice, ndi ndulu.

Itanani omwe akukuthandizani ngati muli ndi matenda a jaundice omwe samatha kapena zizindikiro za kuchepa kwa magazi m'thupi kapena ma gallstones.

Upangiri wa chibadwa ungakhale woyenera kwa anthu omwe ali ndi mbiri yakubadwa ya matendawa omwe akufuna kukhala makolo.

Elliptocytosis - cholowa

  • Maselo ofiira ofiira - elliptocytosis
  • Maselo amwazi

Gallagher PG. Hemolytic anemias: maselo ofiira am'magazi komanso zopindika zamagetsi. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. 26 wa. Philadelphia, PA: Elsevier; 2020: chap 152.


Gallagher PG. Matenda ofiira a khungu la magazi. Mu: Hoffman R, Benz EJ, Silberstein LE, et al, olemba. Hematology: Mfundo Zoyambira ndi Zochita. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2018: mutu 45.

Merguerian MD, Gallagher PG. Cholowa elliptocytosis, cholowa cha pyropoikilocytosis, ndi zovuta zina. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 486.

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