Dulani matenda am'mimba

Prune belly syndrome ndi gulu la zofooka zobadwa nazo zomwe zimakhudza mavuto atatu awa:

• Kukula bwino kwa minofu yam'mimba, ndikupangitsa khungu la m'mimba kuti linyinyire ngati prune
• Machende osatsitsidwa
• Mavuto a thirakiti

Zomwe zimayambitsa matumbo a prune sizikudziwika. Matendawa amakhudza makamaka anyamata.

Ali m'mimba, m'mimba mwa mwana amene akukula amatupa ndi madzi. Kawirikawiri, chifukwa chake chimakhala vuto m'matope. Timadzimadzi timasowa pambuyo pobadwa, ndikupita kumimba yamakwinya yomwe imawoneka ngati prune. Maonekedwewa amawonekera kwambiri chifukwa cha kuchepa kwa minofu yam'mimba.

Minofu yofooka m'mimba imatha kuyambitsa:

• Kudzimbidwa
• Chedwerani kukhala ndi kuyenda
• Zovuta kutsokomola

Mavuto am'mitsinje angayambitse kukodza.

Mayi yemwe ali ndi pakati ndi mwana yemwe ali ndi matenda a prune m'mimba sangakhale ndi amniotic fluid yokwanira (madzi omwe amazungulira mwana wosabadwa). Izi zitha kupangitsa khanda kukhala ndi mavuto am'mapapo chifukwa chofinyidwa m'mimba.

Ultrasound yomwe imachitika panthawi yapakati imatha kuwonetsa kuti mwanayo ali ndi chikhodzodzo chotupa kapena impso zokulitsa.

Nthawi zina, kutenga mimba kwa ultrasound kumathandizanso kudziwa ngati mwanayo ali:

• Mavuto amtima
• Mafupa kapena minofu yachilendo
• Mimba ndi mavuto am'mimba
• Mapapu osatukuka

Mayeso otsatirawa atha kuchitidwa kwa mwana atabadwa kuti apeze vutoli:

• Kuyesa magazi
• Mitsempha yotchedwa pyelogram (IVP)
• Ultrasound
• Kutulutsa cystourethrogram (VCUG)
• X-ray
• Kujambula kwa CT
  

Kuchita opaleshoni koyambirira kumalimbikitsidwa kukonza minofu yofooka ya m'mimba, mavuto am'mikodzo, ndi machende osavomerezeka.

Mwana atha kupatsidwa maantibayotiki kuti azichiza kapena kuthandiza kupewa matenda amkodzo.

Zida zotsatirazi zitha kukupatsirani zambiri za prune belly syndrome:

• Prune Belly Syndrome Network - prunebelly.org
• National Organisation for Rare Disways - rarediseases.org/rare-diseases/prune-belly-syndrome

Prune belly syndrome ndi vuto lalikulu ndipo nthawi zambiri limawopseza moyo.

Makanda ambiri omwe ali ndi vutoli amabadwa akufa kapena kufa m'milungu ingapo yoyambirira. Choyambitsa imfa chimachokera ku mavuto akulu am'mapapo kapena impso, kapena mavuto ena obadwa nawo.

Ana ena akhanda amatha kukhala ndi moyo ndipo amakula bwinobwino. Ena akupitilizabe kukhala ndi mavuto azachipatala ndi chitukuko.

Zovuta zimadalira zovuta zomwe zikugwirizana. Ambiri ndi awa:

• Kudzimbidwa
• Zofooka za mafupa (phazi lamiyendo, chiuno chosweka, chiwalo chosowa, chala, kapena chala, chifuwa)
• Matenda am'mikodzo (angafunike dialysis ndi kumuika impso)

Machende osatsitsidwa angayambitse kusabereka kapena khansa.

Matenda am'mimba a Prune nthawi zambiri amapezeka asanabadwe kapena pamene mwana wabadwa.

Ngati muli ndi mwana yemwe ali ndi matenda a prune belly syndrome, itanani woyang'anira wanu pachizindikiro choyamba cha matenda amkodzo kapena zina zamikodzo.

Ngati mimba ya ultrasound ikuwonetsa kuti mwana wanu ali ndi chikhodzodzo chotupa kapena impso zokulitsa, lankhulani ndi katswiri wazowopsa za mimba kapena perinatology.

Palibe njira yodziwika yopewera vutoli. Ngati mwana amapezeka kuti ali ndi zotupa m'mimba asanabadwe, nthawi zambiri, kuchitidwa opaleshoni panthawi yapakati kumathandiza kuti vutoli lisapite patsogolo mpaka kudulira matenda am'mimba.

Matenda a Eagle-Barrett; Matenda a Triad

Caldamone AA, Amuna FT. Matenda a Prune-m'mimba. Mu: Wein AJ, Kavoussi LR, Partin AW, Peters CA, olemba. Urology wa Campbell-Walsh. 11th ed. Philadelphia, PA: Elsevier; 2016: chap 140.

Mkulu JS. Kutsekedwa kwa thirakiti. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 555.

Merguerian PA, Rowe CK. Zovuta zopititsa patsogolo dongosolo la genitourinary. Mu: Gleason CA, Juul SE, olemba. Matenda a Avery a Mwana Wongobadwa kumene. 10th ed. Philadelphia, PA: Elsevier; 2018: chap 88.