Pityriasis rubra pilaris

Pityriasis rubra pilaris (PRP) ndimatenda akhungu osowa omwe amachititsa kutupa ndikukula (kutulutsa) pakhungu.
Pali mitundu ingapo ya PRP. Choyambitsa sichikudziwika, ngakhale zimayambitsa ma genetic ndi mayankho achilendo amthupi. Gawo limodzi limalumikizidwa ndi HIV / AIDS.
PRP ndi matenda achikopa omwe khungu lawo lalanje kapena la salimoni limakhala ndi khungu lakuda m'manja ndi m'miyendo.
Malo amanjenje amatha kuphimba thupi lonse. Zilumba zazing'ono za khungu labwinobwino (zotchedwa zilumba zosungitsa) zimawoneka mkati mwa khungu la mamba. Madera akhungu akhoza kuyabwa. Pakhoza kukhala kusintha m'misomali.
PRP ikhoza kukhala yovuta. Ngakhale sizowopseza moyo, PRP imatha kuchepetsa kwambiri moyo ndikuchepetsa zochitika zatsiku ndi tsiku.
Wothandizira zaumoyo awunika khungu lanu. Matendawa amadziwika chifukwa cha zotupa zapadera. (Chotupa ndi malo achilendo pakhungu). Wothandizirayo atha kutenga zitsanzo (ma biopsies) a khungu lomwe lakhudzidwa kuti atsimikizire kuti ali ndi vutoli ndikuwonetsa zomwe zingawoneke ngati PRP.
Mavitamini omwe ali ndi urea, lactic acid, retinoids, ndi steroids atha kuthandiza. Nthawi zambiri, mankhwala amaphatikizapo mapiritsi omwe amatengedwa pakamwa monga isotretinoin, acitretin, kapena methotrexate. Kuwonetsa kuwala kwa ultraviolet (kuwala mankhwala) kungathandizenso. Mankhwala omwe amakhudza chitetezo chamthupi pano akuwerengedwa ndipo atha kukhala othandiza kwa PRP.
Izi zitha kupereka zambiri pa PRP:
- National Organisation for Rare Disways - rarediseases.org/rare-diseases/pityriasis-rubra-pilaris
Itanani omwe akukuthandizani ngati mukuyamba kukhala ndi vuto la PRP. Komanso itanani ngati muli ndi matendawa komanso zizindikilo zikuipiraipira.
PRP; Pityriasis pilaris; Ndere yampweya acuminatus; Matenda a Devergie
Pityriasis rubra pilaris pachifuwa
Pityriasis rubra pilaris pamapazi
Pityriasis rubra pilaris pachikhatho
Pityriasis rubra pilaris - kutseka
James WD, Elston DM, Chitani JR, Rosenbach MA, Neuhaus IM. Pityriasis rosea, pityriasis rubra pilaris, ndi matenda ena amtundu wa papulosquamous and hyperkeratotic. Mu: James WD, Elston DM, Tsatirani JR, Rosenbach MA, Neuhaus IM, eds. Matenda a Andrews a Khungu: Clinical Dermatology. Wolemba 13. Philadelphia, PA: Elsevier; 2020: mutu 11.
Patterson JW. Matenda a pigmentation. Mu: Patterson JW, mkonzi. Matenda a Khungu la Weedon. Wolemba 4. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: mutu 10.