Mlembi: Joan Hall
Tsiku La Chilengedwe: 1 Febuluwale 2021
Sinthani Tsiku: 13 Meyi 2025
Anonim
Anencephaly Explained
Kanema: Anencephaly Explained

Anencephaly ndiko kupezeka kwa gawo lalikulu la ubongo ndi chigaza.

Anencephaly ndi imodzi mwazofala kwambiri za neural tube zolakwika. Zolakwika za Neural chubu ndizobadwa zobadwa zomwe zimakhudza minofu yomwe imakhala msana ndi ubongo.

Anencephaly imachitika koyambirira kwamwana wosabadwa. Zimachitika pamene gawo lapamwamba la neural chubu lalephera kutseka. Zomwe zimayambitsa sizikudziwika. Zomwe zingayambitse ndi izi:

  • Poizoni wachilengedwe
  • Kutsika kochepa kwa folic acid ndi mayi panthawi yapakati

Chiwerengero chenicheni cha milandu ya anencephaly sichidziwika. Ambiri mwa mimba zimabweretsa kupita padera. Kukhala ndi khanda limodzi lokhala ndi vutoli kumawonjezera chiopsezo chokhala ndi mwana wina yemwe ali ndi vuto la neural tube.

Zizindikiro za anencephaly ndi:

  • Kupezeka kwa chigaza
  • Kupezeka kwa ziwalo zaubongo
  • Zovuta pankhope
  • Kuchedwa kwakukula kwakukula

Zofooka zamtima zitha kupezeka m'modzi mwa milandu isanu.

Ultrasound panthawi yoyembekezera yachitika kuti mutsimikizire matendawa. Ultrasound imatha kuwulula madzimadzi ochulukirapo m'chiberekero. Matendawa amatchedwa polyhydramnios.


Amayi amathanso kuyesedwa pamimba:

  • Amniocentesis (kuyang'ana kuchuluka kwa alpha-fetoprotein)
  • Mulingo wa Alpha-fetoprotein (kuchuluka kowonjezeka kumawonetsa vuto la neural tube)
  • Mlingo wamkodzo estriol

Kuyezetsa magazi asanakhale ndi pakati kumatha kuchitidwanso.

Palibe chithandizo chamakono. Lankhulani ndi wothandizira zaumoyo wanu pazisankho.

Matendawa amayambitsa imfa m'masiku ochepa atabadwa.

Wopezera chithandizo nthawi zambiri amawona izi panthawi yoyezetsa magazi asanabadwe komanso ultrasound. Apo ayi, imadziwika pobadwa.

Ngati anencephaly amapezeka asanabadwe, pamafunika upangiri wina.

Pali umboni wabwino wosonyeza kuti folic acid imathandizira kuchepetsa chiopsezo cha zovuta zina zobadwa, kuphatikizapo anencephaly. Amayi omwe ali ndi pakati kapena akukonzekera kutenga pakati ayenera kumwa multivitamin ndi folic acid tsiku lililonse. Zakudya zambiri tsopano zalimbikitsidwa ndi folic acid kuti zithandizire kupewa zovuta zamtunduwu.


Kupeza folic acid wokwanira kumachepetsa mwayi wopunduka m'mitsempha ya theka.

Aprosencephaly yokhala ndi cranium yotseguka

  • Ultrasound, yachibadwa mwana wosabadwayo - ventricles ubongo

Huang SB, Doherty D. Kubadwa kopanda tanthauzo kwa dongosolo lamanjenje lamkati. Mu: Gleason CA, Juul SE, olemba. Matenda a Avery a Mwana Wongobadwa kumene. 10th ed. Philadelphia, PA: Elsevier; 2018: mutu 59.

Wachibale SL, Johnston MV. Kobadwa nako anomalies chapakati mantha dongosolo. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 609.

Sarnat HB, Flores-Sarnat L.Kukula kwa dongosolo lamanjenje. Mu: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, olemba. Neurology ya Bradley mu Kuchita Zachipatala. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2016: chap 89.


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