Zotsatira za Pierre Robin

Zotsatira za Pierre Robin (kapena matenda) ndi momwe khanda limakhala ndi nsagwada zochepa, lilime lomwe limagwera pakhosi, komanso kupuma movutikira. Ilipo pakubadwa.

Zomwe zimayambitsa kutsatana kwa Pierre Robin sizikudziwika. Itha kukhala gawo la ma syndromes ambiri amtundu.

Nsagwada zakumunsi zimayamba pang'onopang'ono asanabadwe, koma zimatha kukula msanga mzaka zoyambirira za moyo.

Zizindikiro za matendawa ndi monga:

• Chatsitsa m'kamwa
• M'kamwa mwamphamvu
• Nsagwada zomwe ndi zazing'ono kwambiri ndi chibwano chaching'ono
• Nsagwada zomwe zili kumbuyo kwambiri pakhosi
• Matenda obwereza khutu
• Kutseguka pang'ono padenga pakamwa, komwe kumatha kuyambitsa kutsamwa kapena zakumwa kubwerera kudzera mphuno
• Mano amene amatuluka mwana akabadwa
• Lilime lomwe ndi lalikulu poyerekeza ndi nsagwada

Wopereka chithandizo chamankhwala amatha kuzindikira izi nthawi ya mayeso. Kulankhulana ndi katswiri wamtundu wa zamoyo kumatha kuthana ndi mavuto ena okhudzana ndi matendawa.

Lankhulani ndi dokotala wa mwana wanu za malo ogona otetezeka. Makanda ena omwe ali ndi gawo la Pierre-Robin amafunika kugona m'mimba m'malo mobwerera kuti lilime lawo lisabwererenso kumtunda.

Pazaka zochepa, mwanayo amafunika kuti ayike chubu kupyola m'mphuno komanso munjira yopewera kutsekeka kwa njira yapaulendo. Pazovuta kwambiri, amafunika kuchitidwa opaleshoni kuti ateteze kutsekeka kumtunda kwapamwamba. Ana ena amafunika kuchitidwa opaleshoni kuti apange dzenje panjira yawo kapena kusunthira nsagwada zawo patsogolo.

Kudyetsa kuyenera kuchitidwa mosamala kwambiri kuti tipewe kutsamwitsa ndikupumira zakumwa munjira zopumira. Mwanayo angafunike kudyetsedwa kudzera mu chubu kuti ateteze kutsamwa.

Zida zotsatirazi zitha kupereka zambiri pazotsatira za Pierre Robin:

• Kafukufuku Wosiyanasiyana wa Kubadwa kwa Ana - www.birthdefects.org/pierre-robin-syndrome
• Cleft Palate Foundation - www.cleftline.org
• National Organisation for Rare Disways --rarediseases.org/rare-diseases/pierre-robin- pambuyo

Mavuto obvuta komanso odyetsa amatha okha pazaka zingapo zoyambilira pamene nsagwada zakumunsi zimakula kukula. Pali chiopsezo chachikulu pamavuto ngati mayendedwe apandege a mwana satetezedwa kuti asatsekedwe.

Zovuta izi zitha kuchitika:

• Kupuma kovuta, makamaka mwana akagona
• Magawo okutsamwa
• Kulephera kwa mtima
• Imfa
• Kudyetsa zovuta
• Oxygen wamagazi ochepa komanso kuwonongeka kwa ubongo (chifukwa chovuta kupuma)
• Mtundu wa kuthamanga kwa magazi kotchedwa pulmonary hypertension

Ana obadwa ndi vutoli nthawi zambiri amapezeka kuti amabadwa.

Itanani omwe akukuthandizani ngati mwana wanu akukumana ndi zovuta kapena kupuma movutikira. Kutsekeka kwa njira zapaulendo kumatha kubweretsa phokoso lalikulu mwana akamapuma. Zitha kupanganso khungu labwinopo (cyanosis).

Komanso itanani ngati mwana wanu ali ndi mavuto ena opuma.

Palibe njira yodziwika yopewera. Kuchiza kumachepetsa mavuto opumira komanso kutsamwa.

Matenda a Pierre Robin; Maofesi a Pierre Robin; Pierre Robin wopanda pake

• Khanda lolimba komanso lofewa

Dhar V. Syndromes okhala ndi mawonekedwe amlomo. Mu: Kliegman RM, Stanton BF, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 337.

Purnell CA, Gosain AK. Zotsatira za Pierre Robin. Mu: Rodriguez ED, Losee JE, Neligan PC, eds. Opaleshoni ya Pulasitiki: Gawo Lachitatu: Opaleshoni ya Craniofacial, Mutu ndi Khosi ndi Opaleshoni ya Pulasitiki. Wolemba 4. Philadelphia, PA: Elsevier; 2018: mutu 36.