Momwe mungachiritse phenylketonuria komanso momwe mungapewere zovuta

Zamkati

• 1. Thanzi
• Momwe mungaperekere mkaka wa m'mawere mosamala
• 2. Kugwiritsa ntchito zowonjezera zakudya
• Zotheka zovuta za phenylketonuria
• Momwe mungapewere

Chisamaliro ndi chithandizo cha phenylketonuria mwa mwana chiyenera kutsogozedwa ndi dokotala wa ana, koma chisamaliro chachikulu ndikupewa zakudya zokhala ndi phenylalanine, zomwe ndizakudya zambiri zamapuloteni, monga nyama, nsomba, mkaka, tchizi ndi mazira. Chifukwa chake, makolo a makanda omwe ali ndi phenylketonuria ayenera kukhala tcheru ndi chakudya cha mwana wawo, kunyumba komanso kusukulu.

Kuphatikiza apo, kuyamwitsa mwana yekha kuyeneranso kukhala kotsogola kwa dokotala wa ana, popeza mkaka wa m'mawere uli ndi phenylalanine, ngakhale ndi wocheperako poyerekeza ndi womwe umapezeka munjira zambiri zamankhwala. Momwemo, kuchuluka kwa phenylalanine kwa mwana mpaka miyezi isanu ndi umodzi kuyenera kusungidwa pakati pa 20 mpaka 70 mg wa phenylalanine pa kg ya kulemera kwa thupi.

Ndikofunikira kuti chithandizo cha phenylketonuria chitsatidwe molingana ndi malangizo a dokotala wa ana komanso wazakudya zopewetsa zovuta kuti zisawonongeke, zomwe zimakhudzana kwambiri ndikukula kwamanjenje.

1. Thanzi

Chithandizo cha zakudya ndi njira yofunika kwambiri yopewera zovuta zamatendawa, chifukwa ndi kudzera pachakudya chomwe chimatha kuwongolera kuchuluka kwa phenylalanine m'magazi, motero kupewa zovuta za matendawa. Ndikofunikira kuti chakudyacho chizitsogoleredwa ndi wopatsa thanzi malinga ndi zotsatira za mayeso a mwana omwe amayenera kuchitidwa pafupipafupi kuti awone kuchuluka kwa phenylalanine m'magazi.

Phenylalanine amapezeka muzakudya zingapo, zanyama ndi zamasamba. Chifukwa chake, kuti muchepetse matendawa ndikupewa zovuta ndikofunikira kupewa zakudya zina, monga:

• Zakudya zanyama: nyama, mkaka ndi nyama, mazira, nsomba, nsomba, ndi nyama monga soseji, soseji, nyama yankhumba, nyama.
• Zakudya zoyambira: tirigu, soya ndi zotumphukira, nandolo, nyemba, nandolo, mphodza, mtedza, mtedza, mtedza, maamondi, mtedza, pistachios, mtedza wa paini;
• Zokometsera zokhala ndi aspartame;
• Zida zomwe zili ndi zakudya zoletsedwa monga chophatikiziramonga makeke, makeke, ayisikilimu ndi buledi.

Zipatso ndi ndiwo zamasamba zitha kudyedwa ndi phenylketonurics, komanso shuga ndi mafuta. Ndikothekanso kupeza pamsika zinthu zingapo zapadera zomwe zimapangidwira omvera, monga mpunga, pasitala ndi ma crackers, ndipo pali maphikidwe angapo omwe angagwiritsidwe ntchito popanga zakudya zochepa mu phenylalanine.

Onani mndandanda wazakudya zolemera mu phenylalanine.

Momwe mungaperekere mkaka wa m'mawere mosamala

Ngakhale malingaliro ake ndikuchotsa mkaka wa m'mawere kuchokera pazakudya za mwana, pogwiritsa ntchito mkaka wokhawo wopanda mankhwala wa phenylalanine, ndikotheka kuyamwitsa mwana phenylketonuric, komabe pakufunika izi:

• Kuyezetsa magazi kwa mwana sabata iliyonse kuti muwone kuchuluka kwa phenylalanine m'magazi;
• Werengani kuchuluka kwa mkaka wa m'mawere wopatsa mwana, malinga ndi zomwe phenylalanine amaganiza m'magazi a mwana komanso malinga ndi malangizo a dotolo;
• Kuwerengetsa kuchuluka kwa mankhwala mkaka popanda phenylalanine, kumaliza mwana kudyetsa;
• Ndi pampu, chotsani kuchuluka kwa mkaka wa m'mawere womwe mayi angapatse mwana;
• Gwiritsani ntchito botolo kapena njira yolumikizirana kudyetsa mwana.

Ndikofunikira kupatula amino acid phenylalanine pachakudya, kuti mwana asakhale ndi zovuta pakukula kwakuthupi ndi kwamaganizidwe, monga kuchepa kwamaganizidwe. Onani momwe chakudya chiyenera kukhalira mu phenylketonuria.

2. Kugwiritsa ntchito zowonjezera zakudya

Popeza zakudya za munthu yemwe ali ndi phenylketonuria ndizoletsedwa, ndizotheka kuti alibe mavitamini ndi michere yofunikira kuti thupi lizigwira bwino ntchito komanso kuti mwanayo akule bwino. Chifukwa chake, katswiri wazakudya atha kulimbikitsa kugwiritsa ntchito zowonjezera mavitamini ndi njira zopatsa thanzi kuti zitsimikizire kukula kwa mwana ndikulimbikitsa thanzi lake.

Chowonjezera chomwe chiyenera kugwiritsidwa ntchito chikuwonetsedwa ndi katswiri wazakudya malinga ndi msinkhu, kulemera kwa munthuyo ndi mphamvu yakudya kwa mwana, ndipo amayenera kusungidwa moyo wonse.

Zotheka zovuta za phenylketonuria

Mavuto a phenylketonuria amabwera ngati matendawa sanapangidwe msanga kapena ngati mankhwala satsatiridwa molingana ndi malangizo a dokotala wa ana, ndikupeza kwa phenylalanine m'magazi, omwe amatha kufikira madera ena aubongo ndikupangitsa kuti pakhale kusintha kosatha, monga monga:

• Kuchedwa mu chitukuko cha psychomotor;
• Kukula pang'ono kwaubongo;
• Yaying'onocephaly;
• Kusakhudzidwa;
• Khalidwe losokonezeka;
• Kuchepetsa IQ;
• Kusowa kwakukulu kwamalingaliro;
• Kupweteka;
• Kugwedezeka.

Pakapita nthawi, ngati mwanayo sakuchiritsidwa moyenera, pakhoza kukhala zovuta kukhala pansi ndikuyenda, zovuta zamakhalidwe ndikuchedwa kuyankhula komanso kukulitsa nzeru, kuphatikiza kukhumudwa, khunyu ndi ataxia, zomwe ndikulephera kudziletsa.

Momwe mungapewere

Pofuna kupewa zovuta, nkofunika kuti matendawa apangidwe m'masiku oyamba atabadwa mwanayo kudzera pachiwopsezo cha chidendene. Zotsatira zake ndi zabwino, ndikofunikira kuti chithandizocho chichitike molingana ndi malangizo a adotolo.

Kuphatikiza apo, panthawiyi ndikofunikira kuti mayeso azichitidwa nthawi zonse kuti awone thanzi la mwanayo, motero, kuwonetsa kusintha kwa zakudya ndi zowonjezera zakudya.

Mayeso otsatira amatsatiridwa sabata iliyonse mpaka mwana atakwanitsa chaka chimodzi. Ana azaka zapakati pa 2 ndi 6 amabwereza mayeso masiku 15 aliwonse ndipo, kuyambira zaka 7, mayeso amachitika kamodzi pamwezi.