Kodi Chiyembekezo cha Moyo Ndi Chiyani Kwa Anthu Omwe Ali Ndi Cystic Fibrosis?

Zamkati

• Kodi cystic fibrosis ndi chiyani?
• Kodi zaka za moyo ndizotani?
• Amachizidwa bwanji?
• Kodi cystic fibrosis ndi yofala motani?
• Zizindikiro ndi zovuta zake ndi ziti?
• Kukhala ndi cystic fibrosis

Kodi cystic fibrosis ndi chiyani?

Cystic fibrosis ndizovuta zomwe zimayambitsa matenda opatsirana m'mapapo ndipo zimapangitsa kuti zikhale zovuta kupuma. Zimayambitsidwa ndi chilema mu jini la CFTR. Zovuta zimakhudza ma gland omwe amatulutsa ntchofu ndi thukuta. Zizindikiro zambiri zimakhudza kupuma komanso kugaya chakudya.

Anthu ena amakhala ndi jini lopunduka, koma samakhala ndi cystic fibrosis. Mutha kungopeza matendawa ngati mungalandire jini lolakwika kuchokera kwa makolo onse.

Onyamula awiri akakhala ndi mwana, pamangokhala mwayi wa 25 peresenti kuti mwanayo atha kukhala ndi cystic fibrosis. Pali mwayi wa 50 peresenti kuti mwanayo adzakhala wonyamula, ndipo 25% ali ndi mwayi kuti mwanayo sangalandire kusintha konse.

Pali kusintha kosiyanasiyana kwa jini la CFTR, chifukwa chake zizindikilo ndi kuuma kwa matenda zimasiyanasiyana malinga ndi munthu.

Pitilizani kuwerenga kuti mudziwe zambiri za omwe ali pachiwopsezo, njira zabwino zochiritsira, komanso chifukwa chake anthu omwe ali ndi cystic fibrosis akukhala motalikirapo kuposa kale.

Kodi zaka za moyo ndizotani?

M'zaka zaposachedwa, pakhala kupita patsogolo kwamankhwala omwe amapezeka kwa anthu omwe ali ndi cystic fibrosis. Makamaka chifukwa cha mankhwalawa, nthawi ya moyo ya anthu omwe ali ndi cystic fibrosis yakhala ikukula bwino kwazaka 25 zapitazi. Zaka makumi angapo zapitazo, ana ambiri omwe ali ndi cystic fibrosis sanakhalebe ndi moyo mpaka atakula.

Ku United States ndi United Kingdom masiku ano, moyo wamba ndi zaka 35 mpaka 40. Anthu ena amakhala moyo wopyola pamenepo.

Kutalika kwa moyo kumakhala kotsika kwambiri m'maiko ena, kuphatikiza El Salvador, India, ndi Bulgaria, komwe ndi zaka zosakwana 15.

Amachizidwa bwanji?

Pali njira zingapo komanso zochiritsira zomwe zimagwiritsidwa ntchito pochizira cystic fibrosis. Cholinga chimodzi chofunikira ndikutulutsa mamina ndikusunga mayendedwe apandege. Cholinga china ndikuthandizira kuyamwa kwa michere.

Popeza pali zizindikiro zosiyanasiyana komanso kuopsa kwa zizindikilo, chithandizo chimakhala chosiyana ndi munthu aliyense. Chithandizo chanu chimadalira msinkhu wanu, zovuta zilizonse, komanso momwe mumayankhira ndi mankhwala ena. Zowonjezera mwina pangafunike kuphatikiza mankhwala, omwe atha kukhala:

• kuchita masewera olimbitsa thupi komanso kulimbitsa thupi
• mankhwala owonjezera pakamwa kapena IV
• mankhwala ochotsera ntchofu m'mapapu
• bronchodilators
• corticosteroids
• mankhwala ochepetsa zidulo m'mimba
• mankhwala opatsirana pakamwa kapena opumira
• michere ya pancreatic
• insulini

Ma modulators a CFTR ali m'gulu la mankhwala atsopano omwe amalimbana ndi vuto la chibadwa.

Masiku ano, anthu ambiri omwe ali ndi cystic fibrosis akulandila mapapu. Ku United States, anthu 202 omwe ali ndi matendawa adadulidwa m'mapapo mu 2014. Ngakhale kumuika mapapu sikuchiritsa, kumatha kukonza thanzi ndikutalikitsa moyo. M'modzi mwa anthu asanu ndi m'modzi omwe ali ndi cystic fibrosis omwe ali ndi zaka zopitilira 40 adapanga mapapu.

Kodi cystic fibrosis ndi yofala motani?

Padziko lonse lapansi, anthu 70,000 mpaka 100,000 ali ndi cystic fibrosis.

Ku United States, anthu pafupifupi 30,000 akukhala ndi matendawa. Chaka chilichonse madokotala amapezanso anthu ena 1,000.

Ndizofala kwambiri kwa anthu ochokera kumpoto kwa Europe kuposa mafuko ena. Imapezeka kamodzi pa ana obadwa azungu 2,500 mpaka 3,500. Mwa anthu akuda, mlingowu ndi m'modzi mwa 17,000 ndipo aku Asia America, ndi m'modzi mwa 31,000.

Akuti pafupifupi munthu mmodzi mwa anthu 31 ku United States amakhala ndi jini lopunduka. Ambiri sakudziwa ndipo adzapitilizabe pokhapokha ngati wachibale wawo wapezeka ndi cystic fibrosis

Ku Canada pafupifupi mwana mmodzi mwa makanda 3,600 aliwonse amadwala. Cystic fibrosis imakhudza ana obadwa kumene ku European Union komanso mwana m'modzi mwa ana 2,500 obadwira ku Australia.

Matendawa ndi osowa ku Asia. Matendawa amatha kupezeka kuti sapezeka komanso sadziwika kwenikweni m'malo ena padziko lapansi.

Amuna ndi akazi amakhudzidwa pamlingo wofanana.

Zizindikiro ndi zovuta zake ndi ziti?

Ngati muli ndi cystic fibrosis, mumataya mchere wambiri kudzera mu ntchofu ndi thukuta lanu, ndichifukwa chake khungu lanu limatha kulawa mchere. Kutayika kwa mchere kumatha kupanga kuchepa kwa mchere m'magazi anu, zomwe zingayambitse:

• mikhalidwe yachilendo ya mtima
• kuthamanga kwa magazi
• kugwedezeka

Vuto lalikulu ndiloti ndizovuta kuti mapapu akhalebe opanda mamina. Amamanga ndikutseka mapapu komanso njira zopumira. Kuphatikiza pakupanga kupuma movutikira, imalimbikitsa matenda opatsirana a bakiteriya kuti agwire.

Cystic fibrosis imakhudzanso kapamba. Kuchuluka kwa ntchofu kumeneko kumasokoneza ma enzyme am'mimba, kupangitsa kuti zikhale zovuta kuti thupi likonze chakudya ndikutenga mavitamini ndi michere ina.

Zizindikiro za cystic fibrosis zitha kuphatikiza:

• zala ndi zala zakumapazi
• kupuma kapena kupuma movutikira
• nkusani matenda kapena tizilombo ting'onoting'ono m'mphuno
• kukhosomola komwe nthawi zina kumatulutsa phlegm kapena kumakhala magazi
• mapapo anakomoka chifukwa cha kutsokomola kwanthawi yayitali
• Matenda am'mapapo monga bronchitis ndi chibayo
• kusowa kwa zakudya m'thupi komanso kuchepa kwa mavitamini
• kukula kosauka
• mafuta, mipando yayikulu
• kusabereka mwa amuna
• matenda ashuga okhudzana ndi cystic fibrosis
• kapamba
• miyala yamtengo wapatali
• matenda a chiwindi

Popita nthawi, mapapo akamapitilira kuwonongeka, amatha kupumira.

Kukhala ndi cystic fibrosis

Palibe mankhwala odziwika a cystic fibrosis. Ndi matenda omwe amafunikira kuwunika mosamala ndi chithandizo chamoyo wonse. Chithandizo cha matendawa chimafunikira mgwirizano wapafupi ndi dokotala komanso ena omwe ali mgulu lanu lazaumoyo.

Anthu omwe amayamba kulandira chithandizo msanga amakhala ndi moyo wapamwamba, komanso amakhala ndi moyo wautali. Ku United States, anthu ambiri omwe ali ndi cystic fibrosis amawapeza asanakwanitse zaka ziwiri. Makanda ambiri tsopano amawazindikira akayesedwa atangobadwa kumene.

Kuwononga mpweya wanu ndi mapapo opanda mamina kumatha kutenga maola ambiri patsiku lanu. Nthawi zonse pamakhala chiopsezo cha zovuta zazikulu, chifukwa chake ndikofunikira kuyesa kupewa majeremusi. Izi zikutanthauzanso kuti musakumane ndi ena omwe ali ndi cystic fibrosis. Mabakiteriya osiyanasiyana ochokera m'mapapu anu angayambitse matenda aakulu kwa nonse.

Ndikusintha konseku pa zamankhwala, anthu omwe ali ndi cystic fibrosis akukhala moyo wathanzi komanso wautali.

Zina mwa njira zopitilira kafukufuku zikuphatikizapo mankhwala amtundu ndi mankhwala omwe amatha kuchepetsa kapena kuyimitsa kukula kwa matenda.

Mu 2014, oposa theka la anthu omwe adalembedwa mu cystic fibrosis odwala registry anali azaka zopitilira 18. Zinali zoyambirira. Asayansi ndi madotolo akuyesetsa kuti izi zitheke.