Mlembi: Eugene Taylor
Tsiku La Chilengedwe: 14 Ogasiti 2021
Sinthani Tsiku: 18 Kuni 2024
Anonim
Hemolytic Uremic Syndrome (HUS)
Kanema: Hemolytic Uremic Syndrome (HUS)

Zamkati

Kodi Hemolytic Uremic Syndrome Ndi Chiyani?

Matenda a Hemolytic uremic (HUS) ndi ovuta pomwe chitetezo cha mthupi, makamaka pambuyo pamagazi am'mimba, chimayambitsa ma cell ofiira ofiira, kuchuluka kwamagazi, komanso kuvulala kwa impso.

Matenda am'mimba (m'mimba mwanu ndi m'matumbo) ndizomwe zimayambitsa matendawa. Chitetezo cha mthupi chimagwira poizoni wotulutsidwa m'matenda a m'matumbo. Izi zimayambitsa kuwonongeka ndi kuwonongeka kwa maselo amwazi momwe amayenda kudzera mumitsempha yamagazi. Izi zikuphatikiza ma cell ofiira ofiira (RBC) ndi ma platelets, omwe amawapangitsa kufa msanga. Impso zimakhudzidwa m'njira ziwiri. Chitetezo cha mthupi chimatha kuwononga mwachindunji maselo amphongo omwe amawononga impso. Kapenanso, kumangidwanso kwa ma RBC kapena ma platelet omwe awonongedwa kumatsekereza zosefera za impso ndikupangitsa kuvulala kwa impso kapena kuchuluka kwa zinyalala mthupi, popeza impso sizingathenso kutaya zinyalala zamagazi.


Kuvulala kwa impso kumatha kukhala koopsa ngati mutapanda kuchiritsidwa. Impso kulephera, kukwera kowopsa kwa kuthamanga kwa magazi, mavuto amtima, ndi sitiroko ndizodandaula ngati HUS apita patsogolo popanda chithandizo mwachangu.

HUS ndiye chifukwa chofala kwambiri cha kulephera kwa impso kwa ana.Amakonda kwambiri ana osakwana zaka 5, ngakhale ana okalamba komanso achikulire amathanso kudwala matendawa.

Mwamwayi, anthu ambiri omwe amalandira chithandizo mwachangu amatha kuchira popanda kuwonongeka kwa impso.

Kuzindikira Zizindikiro Za Hemolytic Uremic Syndrome

Zizindikiro za HUS zimasiyana. Zizindikiro zingaphatikizepo:

  • kutsegula m'mimba kwamagazi
  • kupweteka m'mimba
  • khungu lotumbululuka
  • kupsa mtima
  • kutopa
  • malungo
  • mikwingwirima yosadziwika kapena kutuluka magazi
  • kuchepa pokodza
  • kutupa m'mimba
  • magazi mkodzo
  • chisokonezo
  • kusanza
  • nkhope yotupa
  • miyendo yotupa
  • kugwidwa (kosazolowereka)

Kodi Chimayambitsa Hemolytic Uremic Syndrome Ndi Chiyani?

HUS imachitika pomwe chitetezo chamthupi chimayambitsa kuwonongeka kwa maselo amwazi. Izi zimabweretsa kuchuluka kwama cell ofiira ofiira, kuchuluka kwamagazi, komanso kuvulala kwa impso


ANTHU mwa Ana

Zomwe zimayambitsa HUS mwa ana ndi matenda EscherichiaColi (E. coli). Pali mitundu yosiyanasiyana ya E. coli, ndipo zambiri sizimayambitsa mavuto. Pamenepo, E. coli mabakiteriya amapezeka m'matumbo a anthu athanzi komanso nyama. Komabe, mitundu ina ya E. coli, omwe amapatsidwa chakudya chodetsedwa, amachititsa matenda omwe angayambitse HUS. Matupi amadzi omwe adetsedwa ndi ndowe amathanso kunyamula E. coli.

Mabakiteriya ena monga Chinthakamatenda opatsirana ndipo Salmonella typhi zingamupangitse IYE.

HUS mwa Akuluakulu

HUS mwa akuluakulu amathanso kuyambitsidwa ndi matenda E. coli.. Palinso zifukwa zambiri zomwe sizimayambitsa bakiteriya za HUS mwa akulu zomwe sizodziwika bwino, kuphatikizapo:

  • mimba
  • Matenda a HIV / AIDS
  • quinine (yogwiritsira ntchito kukokana kwa minofu)
  • chemotherapy ndi mankhwala a immunosuppressant
  • mapiritsi olera
  • anti-platelet mankhwala
  • khansa
  • systemic lupus ndi glomerulonephritis

Kuzindikira Hemolytic Uremic Syndrome

Mayeso ofunikira kwambiri amatha kulamulidwa kuti adziwe ngati maselo a magazi awonongeka kapena ntchito ya impso yasokonekera:


Zamgululi

Kuwerengera kwathunthu kwa magazi (CBC) kumayesa kuchuluka ndi kuchuluka kwa ma RBC ndi ma platelet m'mwazi wamagazi.

Mayeso Ena Amwazi

Pofuna kuyesa kuchepa kwa ntchito ya impso, dokotala wanu atha kuyitanitsa mayeso a BUN (omwe amayang'ana urea zopangidwa mwapamwamba) ndi mayeso a creatinine (kufunafuna zotumphukira zam'mimba). Zotsatira zachilendo zitha kuwonetsa mavuto a impso.

Mayeso Amkodzo

Dokotala wanu adzafuna kuyesa magazi kapena mapuloteni mumkodzo wanu.

Zitsulo chopondapo

Mabakiteriya kapena magazi mu mpando wanu amatha kuthandiza dokotala kuti athetse chomwe chimayambitsa matenda anu.

Kodi Hemolytic Uremic Syndrome Amachita Bwanji?

Mankhwala ochiritsira a HUS atha kukhala:

Kusintha kwamadzimadzi

Chithandizo chofunikira cha HUS ndikubwezeretsa madzi. Mankhwalawa amalowa m'malo mwa ma elekitirodi omwe thupi liyenera kugwira ntchito. Electrolyte ndi mchere monga calcium, potaziyamu, ndi magnesium. Kusintha kwamadzimadzi kumawonjezeranso magazi kudzera mu impso .. Dotolo wanu amakupatsani madzi am'mitsempha, koma angakulimbikitseninso kuti muzilimbikitsa kumwa madzi mwakumwa madzi kapena ma electrolyte solution.

Kuika Magazi

Kuikidwa magazi kofiira kungakhale kofunikira ngati muli ndi ma RBC ochepa. Anthu amaikidwa magazi m'chipatala. Kuika magazi kumatha kuthetsa zizindikilo zomwe zimakhudzana ndi kuchuluka kwa RBC, monga kupuma movutikira komanso kutopa kwambiri.

Zizindikirozi ndizofanana ndi kuchepa kwa magazi m'thupi, momwe thupi lanu silimatha kupanga maselo ofiira okwanira kupatsa ziwalo zathupi mpweya wabwino wokwanira kuti thupi lizichita bwino. Izi zimachitika chifukwa cha kutayika kwa RBC's.

Mankhwala Ena

Dokotala wanu adzakuchotsani pamankhwala aliwonse omwe angakhale oyambitsa HUS.

Kuika ma platelet kungakhale kofunikira ngati mulibe kuchuluka kwa ma platelet.

Kusinthana kwa plasma ndi njira ina yothandizira, momwe dokotala wanu amalowetsa plasma m'madzi anu ndi plasma kuchokera kwa woperekayo. Mudzalandira plasma yathanzi kuti muthandizire kufalitsa kwa maselo abwinobwino, magazi ofiira ndi ma platelets.

Kodi Pali Mavuto Otani a Hemolytic Uremic Syndrome?

Zikakhala zovuta kwambiri ngati impso zanu zalephera, dialysis ya impso itha kugwiritsidwa ntchito kusefa zinyalala mthupi lanu. Awa ndi chithandizo chakanthawi mpaka impso zitha kugwira bwino ntchito. Ngati sangayambenso kugwira ntchito, mungafunike kumuika impso.

Zovuta Zakale

Vuto lalikulu la HUS ndi kulephera kwa impso. Komabe, HUS amathanso kuyambitsa:

  • kuthamanga kwa magazi
  • kapamba
  • kusintha kwa malingaliro
  • kugwidwa
  • matenda a mtima
  • sitiroko
  • chikomokere

Mwamwayi, anthu ambiri amatha kuchira kwathunthu kuchokera kwa HUS.

Kodi Chiyembekezo cha Hemolytic Uremic Syndrome Ndi Chiyani?

HUS akhoza kukhala vuto lalikulu kwambiri. Komabe, mukuyenera kuti mupezenso bwino ngati mutapezeka kuti mwayamba matendawa ndikuyamba kulandira chithandizo nthawi yomweyo. Itanani dokotala wanu nthawi iliyonse mukakhala ndi zizindikiro zomwe mumakhudzidwa nazo.

Kodi Mungapewe Bwanji Hemolytic Uremic Syndrome?

Chifukwa chofala kwambiri cha HUS ndimatenda E. coli. Ngakhale simungapewe mabakiteriyawa kwathunthu, mutha kuchepetsa chiopsezo chotenga kachilombo ka:

  • kusamba m'manja nthawi zonse
  • kutsuka bwino ziwiya
  • kusunga malo okonzera chakudya ali oyera
  • kusunga chakudya chosaphika chosiyana ndi chakudya chokonzedweratu
  • kubisa nyama mufiriji m'malo moyikapo pa kauntala
  • osasiya nyama firiji (izi zingayambitse kukula kwa bakiteriya).
  • kuphika nyama mpaka madigiri 160 Fahrenheit kuti iphe mabakiteriya owopsa
  • kutsuka zipatso ndi ndiwo zamasamba bwinobwino
  • osasambira m'madzi owonongeka
  • kupewa kupezeka kwa madzi kapena mkaka wosasamalidwa

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