Mlembi: Laura McKinney
Tsiku La Chilengedwe: 10 Epulo 2021
Sinthani Tsiku: 1 Meyi 2024
Anonim
Hyperviscosity Syndrome | What Is The Cause?
Kanema: Hyperviscosity Syndrome | What Is The Cause?

Zamkati

Kodi hyperviscosity syndrome ndi chiyani?

Matenda a Hyperviscosity ndi momwe magazi samatha kuyenda momasuka kudzera mumitsempha yanu.

Mu matendawa, zotchinga zimatha kuchitika chifukwa cha maselo ofiira ambiri, maselo oyera, kapena mapuloteni m'magazi anu. Zitha kupezekanso ndi maselo ofiira amtundu uliwonse, monga matenda amthupi a sickle cell.

Kutengeka mtima kumachitika mwa ana ndi akulu omwe. Kwa ana, zimatha kukhudza kukula kwawo pochepetsa magazi kupita ku ziwalo zofunika, monga mtima, matumbo, impso ndi ubongo.

Kwa achikulire, zimatha kuchitika ndimatenda amthupi okha monga nyamakazi kapena systemic lupus. Zitha kukhalanso ndi khansa yamagazi monga lymphoma ndi leukemia.

Kodi zizindikiro za matenda a hyperviscosity ndi ziti?

Zizindikiro zomwe zimakhudzana ndi vutoli zimaphatikizapo kupweteka mutu, kugwidwa, ndi khungu lofiira pakhungu.

Ngati khanda lanu liri ndi tulo tofa nato kapena sakufuna kudyetsa bwinobwino, ichi ndi chisonyezo chakuti china chake chalakwika.


Kawirikawiri, zizindikiro zomwe zimakhudzana ndi vutoli zimachitika chifukwa cha zovuta zomwe zimachitika pamene ziwalo zofunika sizilandira mpweya wokwanira kudzera m'magazi.

Zizindikiro zina za matenda a hyperviscosity ndi awa:

  • kutuluka magazi mosazolowereka
  • zosokoneza zowoneka
  • zowoneka
  • kupweteka pachifuwa
  • kupuma movutikira
  • kulanda
  • chikomokere
  • kuyenda movutikira

Kodi chimayambitsa matenda a hyperviscosity?

Matendawa amapezeka mwa makanda pomwe mulingo wama cell ofiira onse upitilira 65 peresenti. Izi zimatha kuyambitsidwa ndi zinthu zambiri zomwe zimachitika panthawi yobereka kapena panthawi yobadwa. Izi zingaphatikizepo:

  • kukanikiza mochedwa kwa umbilical
  • matenda omwe anatengera kwa makolo
  • matenda, monga Down syndrome
  • matenda ashuga

Zingathenso kuyambitsidwa ndi zochitika zomwe mulibe mpweya wokwanira womwe umaperekedwa m'thupi la mwana wanu. Matenda opatsirana mwa mapasa ndi mapasa, momwe mapasa amagawana magazi mosiyana m'chiberekero, ndi chifukwa china.


Matenda a Hyperviscosity amathanso kuyambitsidwa ndi zinthu zomwe zimakhudza kupanga maselo amwazi, kuphatikiza:

  • khansa ya m'magazi, khansa yamagazi yomwe imatulutsa maselo oyera oyera ambiri
  • polycythemia vera, khansa yamagazi yomwe imatulutsa maselo ofiira ochuluka kwambiri
  • thrombocytosis yofunikira, mkhalidwe wamagazi womwe umachitika m'mene mafupa amatulutsa ma platelet amwazi ambiri
  • Matenda a myelodysplastic, gulu lamavuto amwazi omwe amayambitsa kuchuluka kwama cell am'magazi, kutulutsa maselo athanzi m'mfupa ndipo nthawi zambiri kumabweretsa kuchepa kwa magazi m'thupi

Kwa akuluakulu, matenda a hyperviscosity amayambitsa zizindikiritso zakuthambo kwamagazi pakati pa 6 ndi 7, poyerekeza ndi saline, koma amatha kutsika. Makhalidwe abwinobwino amakhala pakati pa 1.6 ndi 1.9.

Pakulandira chithandizo, cholinga ndikuchepetsa mamasukidwe akayendedwe pamlingo wofunikira kuthana ndi zizindikiritso za munthu.

Ndani ali pachiwopsezo cha matenda a hyperviscosity?

Matendawa nthawi zambiri amakhudza makanda, koma amathanso kukula atakula. Izi zimachitika chifukwa chake:


  • Mwana wanu ali pachiwopsezo chachikulu chotenga matendawa ngati muli ndi mbiri yabanja.
  • Komanso, iwo omwe ali ndi mbiri yazovuta zam'mafupa ali pachiwopsezo chachikulu chotenga matenda a hyperviscosity.

Kodi matenda a hyperviscosity amapezeka bwanji?

Ngati dokotala akukayikira kuti khanda lanu lili ndi matendawa, amalamula kuti akayezetse magazi kuti adziwe kuchuluka kwa maselo ofiira m'magazi a mwana wanu.

Mayesero ena atha kukhala ofunikira kuti athe kuzindikira. Izi zingaphatikizepo:

  • kuwerengera magazi kwathunthu (CBC) kuti muwone zigawo zonse zamagazi
  • kuyesa kwa bilirubin kuti muwone kuchuluka kwa bilirubin mthupi
  • urinalysis kuyeza shuga, magazi, ndi mapuloteni mumkodzo
  • kuyesa magazi m'magazi kuti muwone kuchuluka kwa shuga wamagazi
  • creatinine kuyesa kuyeza kwa impso
  • kuyesa magazi kwa magazi kuti muwone ngati mpweya uli m'magazi
  • kuyesa kwa chiwindi kuti muwone kuchuluka kwa mapuloteni a chiwindi
  • kuyesa magazi kuti muwone kuchuluka kwa magazi m'magazi

Komanso, dokotala wanu atha kupeza kuti khanda lanu likukumana ndi zinthu monga jaundice, impso kulephera, kapena mavuto apuma chifukwa cha matendawa.

Kodi matenda a hyperviscosity amathandizidwa bwanji?

Ngati dokotala wa mwana wanu atsimikiza kuti mwana wanu ali ndi matenda a hyperviscosity, mwana wanu amayang'aniridwa pazovuta zomwe zingachitike.

Ngati vutoli ndilolimba, dokotala akhoza kukulangizani kusinthana pang'ono. Pochita izi, magazi ochepa amachotsedwa pang'onopang'ono. Nthawi yomweyo, kuchuluka komwe kumachotsedwa kumachotsedwa m'malo mwa mchere wamchere. Izi zimachepetsa maselo ofiira onse, ndikupangitsa magazi kukhala ochepa, osataya magazi.

Dokotala wanu amathanso kulangiza kudyetsa pafupipafupi kwa mwana wanu kuti athe kusintha madzi komanso kuchepetsa makulidwe amwazi. Ngati mwana wanu sakuyankha kukudyetsani, angafunikire kupeza madzi kudzera m'mitsempha.

Kwa achikulire, matenda a hyperviscosity nthawi zambiri amayamba chifukwa cha matenda monga khansa ya m'magazi. Vutoli liyenera kuchitidwa moyenera koyamba kuti liwone ngati izi zikuwonjezera kukhudzika kwa thupi. Nthawi zovuta, plasmapheresis itha kugwiritsidwa ntchito.

Kodi chiyembekezo chanthawi yayitali ndichotani?

Ngati mwana wanu ali ndi vuto lochepa la matenda osokoneza bongo ndipo alibe zisonyezo, mwina sangasowe chithandizo mwachangu. Pali mwayi wabwino wochira, makamaka ngati chifukwa chake chikuwoneka kwakanthawi.

Ngati vutoli likukhudzana ndi chibadwa kapena cholowa, zingafune chithandizo chanthawi yayitali.

Ana ena omwe amapezeka kuti ali ndi vutoli amakhala ndi zovuta zakukula kapena kwaminyewa pambuyo pake. Izi nthawi zambiri zimakhala chifukwa chosowa magazi ndi mpweya kuubongo ndi ziwalo zina zofunika.

Lumikizanani ndi dokotala wa mwana wanu ngati muwona kusintha kulikonse pamakhalidwe a khanda lanu, momwe amadyetsera, kapena magonedwe.

Zovuta zimatha kuchitika ngati vutoli ndilolimba kapena ngati mwana wanu sakuyankha chithandizo. Zovuta izi zitha kuphatikiza:

  • sitiroko
  • impso kulephera
  • kuchepa kwa kuyendetsa magalimoto
  • kusayenda
  • kufa kwa minofu yamatumbo
  • kugwidwa mobwerezabwereza

Onetsetsani kuti munene zizindikiro zilizonse zomwe mwana wanu akukumana ndi dokotala nthawi yomweyo.

Kwa achikulire, matenda a hyperviscosity nthawi zambiri amakhala okhudzana ndi vuto lazachipatala.

Kusamalira moyenera matenda aliwonse omwe akupitilizidwa, kuphatikizapo zomwe katswiri wodziwa zamagazi amalemba, ndi njira zabwino zochepetsera zovuta zamtunduwu.

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