Matenda a Wiskott-Aldrich

Zamkati

• Zizindikiro za Wiskott-Aldrich Syndrome
• Chithandizo cha Wiskott-Aldrich Syndrome

Matenda a Wiskott-Aldrich ndimatenda amtundu, omwe amalepheretsa chitetezo cha mthupi chokhudzana ndi ma lymphocyte a T ndi B, komanso maselo amwazi omwe amathandizira kupewa magazi, ma platelet.

Zizindikiro za Wiskott-Aldrich Syndrome

Zizindikiro za matenda a wiskott-Aldrich atha kukhala:

Chizoloŵezi chakutuluka magazi:

• Kuchepetsa kuchuluka ndi kukula kwa ma platelet m'magazi;
• Kutuluka kwa magazi kosiyanasiyana komwe kumadziwika ndi madontho ofiira ofiira kukula kwa mutu wa pini, wotchedwa "petechiae", kapena atha kukhala okulirapo ndipo amafanana ndi mikwingwirima;
• Zimbudzi zamagazi (makamaka muubwana), kutuluka magazi m'kamwa komanso kutuluka magazi m'mphuno nthawi yayitali.

Matenda omwe amapezeka pafupipafupi ndi mitundu yonse ya tizilombo monga:

• Otitis media, sinusitis, chibayo;
• Meninjaitisi, chibayo chifukwa cha Pneumocystis jiroveci;
• Matenda a khungu la kachilombo koyambitsa matenda a molluscum contagiosum.

Chikanga:

• Pafupipafupi matenda a khungu;
• Mawanga akuda pakhungu.

Mawonekedwe osasintha:

• Vasculitis;
• Kuchepa kwa magazi;
• Idiopathic thrombocytopenic purpura.

Kuzindikira kwa matendawa kumatha kuchitidwa ndi dokotala wa ana pambuyo pakuwona zizindikilo ndi mayeso ena. Kuwona kukula kwa ma platelet ndi njira imodzi yodziwira matendawa, chifukwa matenda ochepa ali ndi izi.

Chithandizo cha Wiskott-Aldrich Syndrome

Chithandizo choyenera kwambiri cha matenda a Wiskott-Aldrich ndikufikitsa mafuta m'mafupa. Njira zina zochiritsira ndikuchotsa ndulu, chifukwa chiwalo ichi chimawononga magazi ochepa omwe anthu omwe ali ndi matendawa, kugwiritsa ntchito hemoglobin komanso kugwiritsa ntchito maantibayotiki.

Kutalika kwa moyo kwa anthu omwe ali ndi vutoli ndikotsika, omwe amakhala ndi moyo atakwanitsa zaka khumi amakhala ndi zotupa monga lymphoma ndi leukemia.