Kodi chithandizo cha hemophilia chimakhala bwanji

Zamkati

• Mitundu ya chithandizo
• Chithandizo cha haemophilia ndi choletsa
• Kusamalira panthawi ya chithandizo

Chithandizo cha hemophilia chimachitika posintha zinthu zomwe zimagunditsa munthu zomwe sizili bwino, zomwe ndi factor VIII, ngati hemophilia mtundu A, ndi factor IX, ngati hemophilia mtundu B, chifukwa ndizotheka kupewa Kutaya magazi kwambiri.

Hemophilia ndi matenda amtundu momwe kuchepa kwa zochitika kapena kusowa kwa zinthu zowumitsa, zomwe ndi mapuloteni omwe amapezeka m'magazi omwe amatsegulidwa pakaphulika chotengera magazi, kupewa magazi ochulukirapo. Chifukwa chake, mukamagwiritsa ntchito m'malo mwa zotseka, ndizotheka kuti munthu yemwe ali ndi hemophilia azikhala moyo wabwinobwino, popanda zoletsa zambiri. Dziwani zambiri za hemophilia.

Mitundu ya chithandizo

Ngakhale kulibe mankhwala, chithandizo cha haemophilia chimathandiza kupewa kutuluka kwa magazi pafupipafupi, ndipo kuyenera kutsogozedwa ndi hematologist ndipo kumachitika m'njira ziwiri:

• Chithandizo cha kupewa: imakhala ndi kusintha kwa zinthu zowumitsa nthawi ndi nthawi, kuti nthawi zonse zizikhala zowonjezeka m'thupi, komanso kupewa kutaya magazi. Chithandizo chamtunduwu sichingakhale chofunikira pakagwa haemophilia wofatsa, ndipo mwina ndikofunikira kulimbikitsidwa pokhapokha ngati pali mtundu wina wamagazi.
• Chithandizo pambuyo magazi: ndi mankhwala omwe amafunidwa, omwe amachitika munthawi zonse, ndikugwiritsa ntchito gawo logwirana pakagwa magazi, zomwe zimapangitsa kuti zithetsedwe mwachangu.

Pazithandizo zilizonse, Mlingo uyenera kuwerengedwa molingana ndi kulemera kwa thupi, kuopsa kwa hemophilia komanso magwiridwe antchito a magazi omwe munthu aliyense amakhala nawo m'magazi ake. Makina a Factor VIII kapena IX amakhala ndi ampoule ya ufa yomwe imasungunuka ndi madzi osungunuka kuti mugwiritse ntchito.

Kuphatikiza apo, mitundu ina ya ma hemostatic wothandizila amatha kugwiritsidwa ntchito pathandizidwe, monga cryoprecipitate, prothrombin complex ndi desmopressin, mwachitsanzo. Mankhwalawa amachitika kwaulere ndi SUS, m'malo opatsirana magazi, potumizidwa ndi dokotala kapena hematologist.

Chithandizo cha haemophilia ndi choletsa

Ma hemophiliac ena amatha kupanga ma antibodies motsutsana ndi factor VIII kapena IX concentrate yomwe imagwiritsidwa ntchito pochizira, yotchedwa inhibitors, yomwe imatha kusokoneza mayankho amankhwala.

Zikatero, pangafunike kuthandizidwa ndi miyezo yayikulu, kapena kuphatikiza kwa zigawo zina zamagazi.

Kusamalira panthawi ya chithandizo

Anthu omwe ali ndi hemophilia ayenera kutsatira izi:

• Yesetsani kuchita masewera olimbitsa thupi, kulimbitsa minofu ndi mafupa, kuchepetsa mwayi wotuluka magazi. Komabe, ndikofunikira kupewa masewera okhudzidwa kapena kukhudzana mwachiwawa;
• Onetsetsani mawonekedwe atsopano, makamaka kwa ana, ndi kuchepa ndi chithandizo;
• Nthawi zonse muzikhala ndi mankhwala pafupi, makamaka ngati paliulendo;
• Khalani ndi ID, ngati chibangili, chosonyeza matendawa, pakagwa zoopsa;
• Fotokozerani vutoli nthawi iliyonse mukamachita chilichonse, monga kugwiritsa ntchito katemera, opaleshoni yamano kapena njira zamankhwala;
• Pewani mankhwala omwe amachititsa kuti magazi atuluke, monga aspirin, anti-inflammatories ndi anticoagulants, mwachitsanzo.

Kuphatikiza apo, kulimbitsa thupi kuyeneranso kukhala mbali yothandizira hemophilia, chifukwa imathandizira kuyendetsa bwino kwamagalimoto, kumachepetsa chiopsezo cha zovuta, monga pachimake hemolytic synovitis, komwe ndikutupa kwa cholumikizira chifukwa chamagazi, komanso kumawongolera kamvekedwe ka minofu, ndipo zitha kuchepetsa kuchepa kwa zinthu zotseka magazi ndikupangitsa kuti moyo ukhale wabwino.