Matenda a Klippel-Trenaunay

Matenda a Klippel-Trenaunay (KTS) ndimavuto ochepa omwe amapezeka pakubadwa. Matendawa nthawi zambiri amakhala ndimadontho a vinyo wapa doko, kukula kwambiri kwa mafupa ndi minofu yofewa, ndi mitsempha ya varicose.

Milandu yambiri ya KTS imachitika popanda chifukwa chomveka. Komabe, milandu ingapo imaganiziridwa kuti imaperekedwa kudzera m'mabanja (obadwa nawo).

Zizindikiro za KTS ndi izi:

• Madontho ambiri a vinyo padoko kapena mavuto ena am'mitsempha yamagazi, kuphatikiza mawanga pakhungu
• Mitsempha ya Varicose (imatha kuwonedwa kuyambira ali wakhanda, koma imatha kuwonedwa pambuyo paubwana kapena unyamata)
• Kusakhazikika kosakhazikika chifukwa cha kutalika kwa kutalika kwa miyendo (gawo lomwe likukhudzidwa ndi lalitali)
• Mafupa, mitsempha, kapena kupweteka kwa mitsempha

Zizindikiro zina zotheka:

• Magazi kuchokera kumatumbo
• Magazi mkodzo

Anthu omwe ali ndi vutoli atha kukula kwambiri mafupa ndi minofu yofewa. Izi zimachitika makamaka m'miyendo, komanso zimakhudza mikono, nkhope, mutu, kapena ziwalo zamkati.

Njira zosiyanasiyana zongoyerekeza zitha kugwiritsidwa ntchito kuti mupeze kusintha kwamthupi chifukwa cha izi. Izi zimathandizanso posankha dongosolo la chithandizo. Izi zingaphatikizepo:

• MRA
• Mankhwala osokoneza bongo a Endoscopic
• X-ray
• Makina a CT kapena CT venography
• MRI
• Mtundu wa duplex ultrasonography

Ultrasound panthawi yoyembekezera ingathandize kupeza vutoli.

Mabungwe otsatirawa amapereka zambiri pa KTS:

• Gulu la Klippel-Trenaunay Syndrome Support Group - k-t.org
• Vascular Birthmark Foundation - www.birthmark.org

Anthu ambiri omwe ali ndi KTS amachita bwino, ngakhale matendawa atha kusintha mawonekedwe awo. Anthu ena ali ndi mavuto amisala chifukwa cha vutoli.

Nthawi zina pamakhala mitsempha yachilendo pamimba, yomwe imafunikira kuwunika.

Matenda a Klippel-Trenaunay-Weber; KTS; Angio-osteohypertrophy; Ma hypertrophicans a hemangiectasia; Nevus verucosus hypertrophicans; Matenda a capillary-lymphatico-venous malformation (CLVM)

Greene AK, Mulliken JB. Zovuta zam'mimba. Mu: Rodriguez ED, Losee JE, Neligan PC, eds. Opaleshoni ya Pulasitiki: Voliyumu 3: Opaleshoni ya Craniofacial, Mutu ndi Khosi ndi Opaleshoni ya Pulasitiki ya Ana. Wolemba 4. Philadelphia, PA: Elsevier; 2018: mutu 39.

Tsamba la KT Support Group. Malangizo azachipatala a Klippel-Trenaunaysyndrome (KTS). k-t.org/assets/images/content/BCH-Klippel-Trenaunay-Syndrome-Management-Guidelines-1-6-2016.pdf. Idasinthidwa pa Januware 6, 2016. Idapezeka Novembala 5, 2019.

Longman RE. Matenda a Klippel-Trenaunay-Weber. Mu: Copel JA, D'Alton ME, Feltovich H, et al, olemba. Kujambula Kwam'mimba. Wachiwiri ed. Philadelphia, PA: Elsevier; 2018: mutu 131.

McCormick AA, Grundwaldt LJ. Zovuta zam'mimba. Mu: Zitelli BJ, McIntire SC, Nowalk AJ, eds. Zitelli ndi Davis ’Atlas of Pediatric Physical Diagnosis. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2018: mutu 10.