Mlembi: Morris Wright
Tsiku La Chilengedwe: 26 Epulo 2021
Sinthani Tsiku: 24 Kuni 2024
Anonim
Cholowa cha angioedema: ndi chiyani, zizindikiro ndi chithandizo - Thanzi
Cholowa cha angioedema: ndi chiyani, zizindikiro ndi chithandizo - Thanzi

Zamkati

Hereditary angioedema ndi matenda amtundu omwe amayambitsa zizindikilo monga kutupa mthupi lonse, komanso kupweteka kwam'mimba mobwerezabwereza komwe kumatha kutsagana ndi nseru ndi kusanza. Nthawi zina, kutupa kumatha kukhudzanso ziwalo monga kapamba, m'mimba ndi ubongo.

Mwambiri, izi zimawoneka asanakwanitse zaka 6 ndipo kutupa kumatha pafupifupi masiku 1 mpaka 2, pomwe kupweteka kwam'mimba kumatha kukhala masiku asanu. Matendawa amatha kukhala nthawi yayitali osayambitsa mavuto kapena zovuta kwa wodwalayo, mpaka mavuto ena atayamba.

Hereditary angiedema ndi matenda osowa, omwe amatha kuchitika ngakhale atakhala kuti alibe banja, ali m'magulu atatu a angiedema: mtundu 1, mtundu wachiwiri ndi mtundu wachitatu, malinga ndi puloteni yomwe imakhudzidwa mthupi.

Zizindikiro zake ndi ziti

Zina mwazizindikiro za angioedema ndikutupa mthupi lonse, makamaka kumaso, manja, mapazi ndi maliseche, kupweteka m'mimba, nseru, kusanza ndipo, pakavuta kwambiri, kutupa kwa ziwalo monga kapamba, m'mimba ndi ubongo.


Zomwe zingayambitse

Angioedema imayambitsidwa ndi kusintha kwa majini mu jini lomwe limapanga mapuloteni okhudzana ndi chitetezo cha mthupi, zomwe zimapangitsa kuti pakhale kutupa nthawi iliyonse yomwe chitetezo chamthupi chimayatsidwa.

Mavuto amathanso kukulitsidwa pakagwa vuto, kupsinjika, kapena panthawi yolimbitsa thupi. Kuphatikiza apo, azimayi amatha kugwidwa ndi msambo komanso msambo.

Ndizovuta ziti zomwe zingabuke

Vuto lalikulu la cholowa cha angiedema ndikutupa pakhosi, komwe kumatha kupha chifukwa chobanika. Kuphatikiza apo, kutupa kwa ziwalo zina kumachitika, matendawa amathanso kusokoneza kagwiritsidwe kake.

Zovuta zina zimatha kukhalanso chifukwa cha zovuta zamankhwala omwe amagwiritsidwa ntchito poletsa matendawa, komanso mavuto monga:

  • Kunenepa;
  • Mutu;
  • Kusintha kwa malingaliro;
  • Kuchuluka ziphuphu;
  • Matenda oopsa;
  • Cholesterol wambiri;
  • Kusamba kwa msambo;
  • Magazi mkodzo;
  • Mavuto a chiwindi.

Mukamalandira chithandizo, odwala amayenera kukayezetsa magazi miyezi isanu ndi umodzi iliyonse kuti aone momwe chiwindi chimagwirira ntchito, ndipo ana ayenera kuyezetsa miyezi iwiri kapena iwiri iliyonse, kuphatikiza kuyesa m'mimba kwa ultrasound miyezi isanu ndi umodzi iliyonse.


Kodi matendawa ndi ati?

Kuzindikira kwa matendawa kumapangidwa kuchokera kuzizindikiro ndikuyezetsa magazi komwe kumayesa mapuloteni a C4 mthupi, omwe amakhala otsika kwambiri ngati angiedema wobadwa nawo.

Kuphatikiza apo, adotolo amathanso kuyitanitsa kuchuluka kwa C1-INH, ndipo kungafunikire kubwereza mayesowo panthawi yamavuto a matendawa.

Momwe mankhwalawa amachitikira

Chithandizo cha angiedema cholowa chimachitidwa molingana ndi kuuma kwake komanso kuchuluka kwa zizindikilo zake, komanso mankhwala opangira mahomoni, monga danazol, stanozolol ndi oxandrolone, kapena mankhwala a antifibrinolytic, monga epsilon-aminocaproic acid ndi tranexamic acid, atha kugwiritsidwa ntchito. mavuto.

Pakakhala zovuta, adotolo amatha kuwonjezera kuchuluka kwa mankhwala ndikulimbikitsanso kugwiritsa ntchito mankhwala osokoneza bongo kuthana ndi kupweteka m'mimba ndi mseru.

Komabe, ngati vutoli limayambitsa kutupa pakhosi, wodwalayo ayenera kumwedwa nthawi yomweyo kuchipinda chadzidzidzi, chifukwa kutupa kumatha kuletsa njira yapaulendo ndikuletsa kupuma, komwe kumatha kubweretsa imfa.


Zomwe muyenera kuchita mukakhala ndi pakati

Pakati pa mimba, odwala omwe ali ndi cholowa cha angiedema ayenera kusiya kugwiritsa ntchito mankhwala, makamaka asanakhale ndi pakati, chifukwa amatha kuyambitsa zovuta m'mimba. Pakabuka mavuto, ayenera kuchitidwa mogwirizana ndi malangizo a dokotala.

Pakubereka kwabwinobwino, kuyambika kwazovuta kumakhala kosowa, koma zikawonekera, nthawi zambiri zimakhala zovuta. Pankhani yobereka mwachisawawa, kugwiritsa ntchito anesthesia yakomweko ndikoyenera, kupewa anesthesia wamba.

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