Kodi epidermolysis bullosa, zizindikiro ndi chithandizo

Zamkati

• Zizindikiro zazikulu
• Chifukwa cha bullous epidermiolysis
• Mitundu yake ndi iti
• Momwe mankhwalawa amachitikira
• Pamene opaleshoni ikufunika
• Zoyenera kuchita kuti muteteze mawonekedwe a thovu
• Momwe mungapangire mavalidwe
• Kodi zovuta ndizotani

Bullous epidermolysis ndimatenda amtundu wakhungu omwe amachititsa mapangidwe a zotupa pakhungu ndi ntchofu, pambuyo pa kukangana kulikonse kapena kupwetekedwa pang'ono komwe kungayambitsidwe ndi mkwiyo wa chovala pakhungu kapena, kungochotsa wothandizira bandi, Mwachitsanzo. Vutoli limachitika chifukwa cha kusintha kwa majini kuchokera kwa makolo kupita kwa ana awo, zomwe zimapangitsa kusintha kwa zigawo ndi zinthu zomwe zimapezeka pakhungu, monga keratin.

Zizindikiro za matendawa zimalumikizidwa ndi kutuluka kwamatuza opweteka pakhungu komanso mbali iliyonse ya thupi, ndipo amatha kuwonekera pakamwa, mgwalangwa ndi kumapazi. Zizindikirozi zimasiyanasiyana kutengera mtundu ndi kuuma kwa epidermolysis bullosa, koma zimangowonjezereka pakapita nthawi.

Chithandizo cha bullous epidermolysis chimakhala ndi chisamaliro chothandizira, monga kukhala ndi chakudya chokwanira komanso kuvala zotupa pakhungu. Kuphatikiza apo, maphunziro akuchitika kuti apange kupatsira mafuta m'mafupa kwa anthu omwe ali ndi vutoli.

Zizindikiro zazikulu

Zizindikiro zazikulu za bullous epidermolysis ndi:

• Khungu zikungowamba pakakokana pang'ono;
• Matuza amabwera mkamwa ngakhale m'maso;
• Kuchiritsa khungu ndi mawonekedwe owawa ndi mawanga oyera;
• Kukhazikitsa misomali;
• Kupatulira tsitsi;
• Kuchepetsa thukuta kapena thukuta lopitirira.

Kutengera kukula kwa bullous epidermolysis, zipsera zala zala zakumapazi zimathanso kuchitika, zomwe zimabweretsa zolakwika. Ngakhale kukhala ndi zizindikilo za epidermolysis, matenda ena amatha kuyambitsa matuza pakhungu, monga herpes simplex, epidermolytic ichthyosis, bullous impetigo ndi pigmentary incontinence. Dziwani zomwe bullous impetigo ndi chithandizo chake.

Chifukwa cha bullous epidermiolysis

Bullous epidermolysis imayambitsidwa ndi kusintha kwa majini kuchokera kwa kholo kupita kwa mwana, ndipo kumatha kukhala kotsogola, komwe kholo limodzi limakhala ndi jini la matendawa, kapena locheperako, momwe abambo ndi amayi amakhala ndi jini la matendawa koma palibe kuwonekera kwa zizindikilo matendawa.

Ana omwe ali ndi achibale apafupi omwe ali ndi matendawa kapena omwe ali ndi jini ya bullous epidermolysis atha kubadwa ali ndi vutoli, chifukwa chake ngati makolo adziwa kuti ali ndi jini la matendawa poyesa majini, upangiri wamtunduwu umawonetsedwa. Onani kuti upangiri wa majini ndi chiyani komanso momwe umachitikira.

Mitundu yake ndi iti

Bullous epidermolysis itha kugawidwa m'mitundu itatu kutengera khungu lomwe limapanga matuza, monga:

• Bully epidermolysis yosavuta: matuza amapezeka pakhungu lapamwamba, lotchedwa khungu, ndipo ndizofala kuti awonekere m'manja ndi m'mapazi. Mwa mtundu uwu ndizotheka kuwona misomali yolimba komanso yolimba ndipo matuza samachira mwachangu;

• Dystrophic epidermolysis bullosa: matuza amtunduwu amayamba chifukwa cha zolakwika pakupanga mtundu wa V | I collagen ndipo imachitika m'malo osanjikiza pakhungu, otchedwa dermis;
• Kuphatikizana kwa epidermolysis bullosa: wodziwika ndi mapangidwe matuza chifukwa chakutalikirana kwa dera lomwe lili pakatikati kwambiri pakhungu ndipo pankhaniyi, matendawa amapezeka pakusintha kwa majini olumikizidwa ndi dermis ndi epidermis, monga Laminin 332.

Matenda a Kindler nawonso ndi mtundu wa bullous epidermolysis, koma ndi wosowa kwambiri ndipo umakhudza zigawo zonse za khungu, zomwe zimapangitsa kuti pakhale kufooka kwakukulu. Mosasamala mtundu wamatendawa, ndikofunikira kudziwa kuti bullous epidermolysis siyopatsirana, ndiye kuti, siyidutsa kuchokera kwa munthu kupita kukakumana ndi zotupa pakhungu.

Momwe mankhwalawa amachitikira

Palibe mankhwala enieni a epidermolysis bullosa, ndipo ndikofunikira kuti tizilankhulana pafupipafupi ndi dermatologist kuti tione momwe khungu limakhalira ndikupewa zovuta, monga matenda.

Chithandizo cha matendawa chimakhala ndi njira zothandizirana, monga kuvala mabala ndikuthana ndi ululu ndipo, nthawi zina, kulandila anthu kuchipatala ndikofunikira kuti apange mavalidwe osabala, opanda tizilombo, kuti mankhwala alowetsedwe mwachindunji mumitsempha, monga maantibayotiki mu vuto la matenda, ndikuthira matuza pakhungu. Komabe, kafukufuku wina akupangidwa kuti akwaniritse ma cell a stem pochiza dystrophic bullous epidermolysis.

Mosiyana ndi zotupa zomwe zimayambitsidwa ndi zotentha, matuza omwe amayamba chifukwa cha epidermolysis bullosa amayenera kuponyedwa ndi singano inayake, pogwiritsa ntchito ma compress osabereka, kuti isafalikire ndikuwononga khungu. Pambuyo pokhetsa, ndikofunikira kugwiritsa ntchito chinthu, monga utsi antibacterial, kupewa matenda.

Pamene opaleshoni ikufunika

Opaleshoni yoopsa ya dermatitis imawonetsedwa pamlandu womwe zipsera zotsalira zimalepheretsa kuyenda kwa thupi kapena zimayambitsa zolakwika zomwe zimachepetsa moyo. Nthawi zina, opaleshoni imatha kugwiritsidwanso ntchito popanga khungu, makamaka mabala omwe akutenga nthawi yayitali kuti apole.

Zoyenera kuchita kuti muteteze mawonekedwe a thovu

Popeza palibe mankhwala, chithandizo amangochita kuti athetse zizindikiro ndikuchepetsa mwayi wamatuza atsopano. Gawo loyamba ndikukhala ndi chisamaliro kunyumba, monga:

• Valani zovala za thonje, pewani nsalu zopangira;
• Chotsani ma tag pazovala zonse;
• Valani kabudula wamkati atatembenuzidwira pansi kuti asalumikizane ndi khungu;
• Valani nsapato zopepuka komanso zokulirapo kuti muvale bwino masokosi opanda msoko;
• Samalani mukamagwiritsa ntchito matawulo mukatha kusamba, ndikudina khungu mosamala ndi thaulo lofewa;
• Thirani Vaselini mochuluka musanachotse mavalidwe ndipo musakakamize kuti achotsedwe;
• Zovalazi zikamamamatira pakhungu, siyani dera lanu lonyowa m'madzi mpaka zovala zitatuluka pakhungu lokha;
• Phimbani mabalawo ndi chovala chosamatira komanso chopukutira choluka;
• Gonani ndi masokosi ndi magolovesi kuti mupewe kuvulala komwe kumachitika mukamagona.

Kuphatikiza apo, ngati pali khungu loyabwa, adokotala atha kugwiritsa ntchito corticosteroids, monga prednisone kapena hydrocortisone, kuti athetse kutupa kwa khungu ndikuchepetsa zizindikilo, kupewa kukanda khungu, kutulutsa zotupa zatsopano. Ndikofunikanso kusamala mukasamba, kupewa kuti madzi amatentha kwambiri.

Kugwiritsa ntchito botox pamapazi akuwoneka kuti ndi othandiza popewera matuza mderali, ndipo gastrostomy imawonetsedwa pomwe sizingatheke kudya bwino popanda matuza pakamwa kapena pammero.

Momwe mungapangire mavalidwe

Mavalidwewa ndi amodzi mwa omwe ali ndi bully epidermolysis ndipo mavalidwe awa ayenera kuchitidwa mosamala kuti athandize kuchiritsa, amachepetsa kukangana komanso kupewa magazi pakhungu, chifukwa ndikofunikira kugwiritsa ntchito mankhwala osakakamira pakhungu , ndiye kuti, alibe guluu wolimba kwambiri.

Kuti muvale mabala omwe ali ndi katulutsidwe kambiri, ndikofunikira kugwiritsa ntchito mavalidwe opangidwa ndi thovu la polyurethane, chifukwa amalowetsa zamadzimadzi izi ndikuteteza ku tizilombo tating'onoting'ono.

Pomwe mabala amakhala owuma kale, tikulimbikitsidwa kugwiritsa ntchito mavitamini a hydrogel, chifukwa amathandizira kuchotsa minofu yakufa ndikuthana ndi ululu, kuyabwa komanso kusapeza bwino m'deralo. Mavalidwe ayenera kukhazikitsidwa ndi ma tubular kapena zotanuka, osavomerezeka kugwiritsa ntchito zomatira pakhungu.

Kodi zovuta ndizotani

Bullous epidermolysis imatha kubweretsa zovuta zina monga matenda, chifukwa mapangidwe amatuza amasiya khungu kuti litengeke ndi mabakiteriya ndi bowa, mwachitsanzo. Nthawi zina zovuta kwambiri, mabakiteriyawa omwe amalowa pakhungu la munthu yemwe ali ndi bullous epidermolysis amatha kufikira magazi ndikufalikira thupi lonse, ndikupangitsa sepsis.

Anthu omwe ali ndi epidermolysis bullosa amathanso kudwala chifukwa cha kuperewera kwa zakudya m'thupi, komwe kumabwera chifukwa cha zotupa mkamwa kapena kuchepa kwa magazi m'thupi, komwe kumachitika chifukwa chotuluka m'magazi. Mavuto ena amano, monga caries, amatha kuwoneka, chifukwa akalowa pakamwa ndi osalimba kwambiri mwa anthu omwe ali ndi matendawa. Komanso, mitundu ina ya epidermolysis bullosa imawonjezera chiopsezo cha munthu kukhala ndi khansa yapakhungu.