Mlembi: Christy White
Tsiku La Chilengedwe: 6 Meyi 2021
Sinthani Tsiku: 3 Epulo 2025
Anonim
Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology
Kanema: Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology

Zamkati

Phenylalanine amatha kuthandizira kuchepetsa kuwonda chifukwa amatenga nawo gawo pazakudya zomwe zimapangitsa kuti thupi likhale lokhuta. Phenylalanine ndi amino acid yemwe amapezeka mwachilengedwe mu zakudya zokhala ndi zomanga thupi zambiri, monga nyama, nsomba ndi mkaka ndi zopangidwa ndi mkaka, komanso mitundu yama supplements yomwe imagulitsidwa m'masitolo ndi malo ogulitsa zakudya.

Kugwiritsa ntchito zowonjezera zowonjezera za phenylalanine kuyenera kulembedwa ndi dokotala kapena katswiri wazakudya ndipo ndizotsutsana ndi anthu omwe ali ndi mavuto monga matenda oopsa, matenda amtima komanso amayi apakati.

Zochita za phenylalanine pothana ndi njala

Phenylalanine amateteza njala chifukwa imagwira nawo ntchito yopanga dopamine ndi norepinephrine, zinthu zomwe ndizofunikira pakuwongolera kudya komanso zomwe zimathandizanso pakuwongolera kuphunzira, kusangalala komanso kukumbukira. Kuphatikiza apo, phenylalanine imathandizira kupanga cholecystokinin hormone, yomwe imagwira ntchito m'matumbo ndikupatsa thupi kukhuta.


Nthawi zambiri mlingo woyenera wa phenylalanine umakhala 1000 mpaka 2000 mg patsiku, koma umasiyanasiyana kutengera mawonekedwe amunthu, monga zaka, zolimbitsa thupi komanso kupezeka kwamavuto monga kupsinjika ndi nkhawa. Komabe, kuwonjezera kwa phenylalanine kokha sikokwanira kuchepa thupi, chifukwa kuchepa thupi kumachitika pokhapokha pakakhala chakudya chabwino.

Zakudya zokhala ndi phenylalaninePhenylalanine chowonjezera

Chisamaliro chomwe chiyenera kutengedwa ndi phenylalanine supplementation

Muyenera kusamala ndi phenylalanine supplementation chifukwa kuchuluka kwa amino acid kumatha kukhala ndi zovuta zina monga kutentha pa chifuwa, mseru komanso kupweteka mutu. Phenylalanine imatsutsananso pakakhala:


  • Matenda a mtima;
  • Matenda oopsa;
  • Amayi oyembekezera kapena oyamwitsa;
  • Anthu omwe amamwa mankhwala osokoneza bongo kuti athetse kukhumudwa kapena zovuta zina zamaganizidwe;
  • Anthu omwe ali ndi phenylketonuria.

Chifukwa chake, supplementation ya phenylalanine iyenera kutsogozedwa ndi dokotala kapena katswiri wazakudya kuti awonetsetse zabwino zake.

Zakudya zokhala ndi phenylalanine

Phenylalanine mwachilengedwe amapezeka mu zakudya zokhala ndi mapuloteni ambiri, monga nyama, nsomba, mkaka ndi mkaka, mtedza, soya, nyemba ndi chimanga. Kugwiritsa ntchito phenylalanine mu zakudya sikuyambitsa mavuto azaumoyo ndipo okhawo omwe ali ndi phenylketonuria ndi omwe ayenera kupewa zakudya izi. Onani mndandanda wathunthu wazakudya za Phenylalanine.

Ngati mukufuna kuchepetsa thupi, onaninso:

  • Kuchepetsa thupi mwachangu
  • Momwe mungapangire zakudya zopatsa thanzi kuti muchepetse kunenepa

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