Chilichonse Chimene Muyenera Kudziwa Zokhudza Porphyria Cutanea Tarda

Zamkati

• Zizindikiro
• Zithunzi za porphyria cutanea tarda
• Zoyambitsa
• Zowopsa
• Zochitika
• Matendawa
• Chithandizo
• Chiwonetsero

Chidule

Porphyria cutanea tarda (PCT) ndi mtundu wa porphyria kapena matenda amwazi omwe amakhudza khungu. PCT ndi imodzi mwamitundu yodziwika kwambiri ya porphyria. Nthawi zina amatchedwa colloquially ngati matenda a vampire. Izi ndichifukwa choti anthu omwe ali ndi vutoli nthawi zambiri amakhala ndi zizindikilo pambuyo powonekera padzuwa.

Zizindikiro

Zizindikiro zambiri za porphyria cutanea tarda zimawoneka pakhungu. Zizindikiro zodziwika ndizo:

• matuza pakhungu lomwe lili padzuwa, kuphatikizapo manja, nkhope, ndi mikono
• photosensitivity, zomwe zikutanthauza kuti khungu lanu limazindikira dzuwa
• khungu lowonda kapena losalimba
• kukula kwa tsitsi, nthawi zambiri kumaso
• crusting ndi mabala a khungu
• kufiira, kutupa, kapena kuyabwa pakhungu
• zilonda zomwe zimayamba pambuyo povulala pang'ono pakhungu
• hyperpigmentation, kutanthauza kuti zigamba za khungu zimakhala zakuda
• mkodzo womwe ndi wakuda kuposa wabwinobwino kapena pabira ofiira
• kuwonongeka kwa chiwindi

Matuza atuluka pakhungu lanu, khungu limatha. Zimakhalanso zachilendo kuti zipsera ziwonekere matuza atachira.

Zigawo zotsekemera nthawi zambiri zimawoneka pankhope, m'manja, ndi m'khosi.

Zithunzi za porphyria cutanea tarda

Zoyambitsa

Porphyria cutanea tarda imatha kuyambitsidwa ndi zinthu zosiyanasiyana. Zomwe zimayambitsa zimayikidwa m'magulu amtundu wamtundu kapena zopezeka.

Zomwe zimayambitsa matendawa ndi monga:

• mbiri ya banja la porphyria cutanea tarda
• kusowa kwa cholowa cha enzyme ya chiwindi uroporphyrinogen decarboxylase
• mbiri yabanja yamatenda a chiwindi kapena khansa ya chiwindi
• chitsulo cha chiwindi kuposa chizolowezi

Zomwe zimapezeka kwambiri ndi izi:

• kumwa mowa
• kugwiritsa ntchito mankhwala a estrogen
• kugwiritsa ntchito njira zolerera
• kuwonetsedwa pazinthu zina zachilengedwe kapena mankhwala, monga Agent Orange
• kutenga chitsulo chochuluka
• kusuta
• kukhala ndi chiwindi C
• kukhala ndi HIV

Nthawi zina, sizingatheke kudziwa chomwe chimayambitsa porphyria cutanea tarda.

Zowopsa

Muli pachiwopsezo chachikulu cha porphyria cutanea tarda ngati mumasuta kapena kumwa mowa. Mwinanso mumakhala ndi vutoli ngati muli ndi hepatitis C kapena HIV.

Kuwonetsedwa ndi mankhwala ena, monga Agent Orange, kumathanso kuwonjezera ngozi yanu. Muyenera kuti mwakumana ndi mankhwalawa ngati ndinu wachikulire yemwe mudatumikira kudera lomwe linali ndi Agent Orange.

Zochitika

Porphyria cutanea tarda imatha kukhudza amuna ndi akazi. Nthawi zambiri zimawonekera atakwanitsa zaka 30, chifukwa chake sizachilendo pakati pa ana kapena achinyamata.

Porphyria cutanea tarda imakhudza anthu padziko lonse lapansi ndipo sikuti imangokhala kudera kapena dziko linalake. Akuti munthu mmodzi mwa anthu 10,000 mpaka 25,000 ali ndi vutoli.

Matendawa

Dokotala wanu amatha kuyezetsa thupi, kuwona ngati ali ndi matenda, ndikulemba mbiri yanu yazachipatala. Kuphatikiza apo, atha kugwiritsa ntchito mayeso otsatirawa kuti apeze porphyria cutanea tarda:

• kuyesa magazi
• kuyesa mkodzo
• mayesedwe a chopondapo
• biopsy khungu

Dokotala adzawona kuchuluka kwanu kwa porphyrin ndi michere ya chiwindi. Kuyezetsa magazi kumatha kulimbikitsidwa kwa anthu omwe ali ndi mbiri yakubadwa ya vutoli.

Chithandizo

Chithandizo cha porphyria cutanea tarda chimayang'ana pakuwongolera ndi kuyimitsa zizindikirazo. Kusintha kwa moyo, monga kuchepetsa kumwa mowa komanso kusasuta, kumathandizanso.

Njira zochiritsira zomwe mungapeze ndizo:

• phlebotomy, komwe ndiko kuchotsa magazi kuti achepetse chitsulo
• chloroquine (Aralen)
• hydroxychloroquine (Plaquenil)
• mankhwala opweteka
• zitsulo zachitsulo
• kuchiza matenda omwe amayambitsa porphyria cutanea tarda, monga HCV kapena HIV

Phlebotomy ndi imodzi mwazithandizo zodziwika bwino za porphyria cutanea tarda. Mapiritsi a antimalarial amagwiritsidwanso ntchito pafupipafupi.

Njira zomwe anthu amasinthira pochiza porphyria cutanea tarda ndi monga:

• kupewa mowa
• osasuta
• kupewa kuwala kwa dzuwa
• pogwiritsa ntchito zoteteza ku dzuwa
• kupewa kuvulala pakhungu
• osatenga ma estrogens

Muyenera kuvala zoteteza ku dzuwa, manja ataliatali, ndi chipewa kuti mupewe dzuwa.

Porphyria cutanea tarda imatha kuwonjezera chiopsezo cha khansa ya chiwindi kapena cirrhosis, yomwe ndi zotupa pachiwindi. Ichi ndichifukwa chake ndikofunikira kuti musamamwe mowa ngati muli ndi vutoli.

Chiwonetsero

Porphyria cutanea tarda nthawi zambiri imakhudza achikulire omwe ali ndi zaka zoposa 30. Ndi matenda am'magazi omwe amakhudza kwambiri khungu. Khungu lanu limatha kuzindikira dzuwa, chifukwa chake mungafunike kusamala kwambiri kuti musapewe dzuwa. Matuza amakhala ofala chifukwa cha vutoli.

Dokotala wanu angakulimbikitseni mankhwala osiyanasiyana a porphyria cutanea tarda. Mapiritsi a phlebotomy ndi antimalarial ndiwo njira zodziwika bwino kwambiri zothandizira.

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