Mlembi: Janice Evans
Tsiku La Chilengedwe: 28 Kulayi 2021
Sinthani Tsiku: 22 Kuni 2024
Anonim
Kuyesa kwa Porphyrin - Mankhwala
Kuyesa kwa Porphyrin - Mankhwala

Zamkati

Kodi kuyesa kwa porphyrin ndi chiyani?

Kuyesedwa kwa Porphyrin kumayeza kuchuluka kwa ma porphyrins m'magazi anu, mkodzo, kapena chopondapo. Porphyrins ndi mankhwala omwe amathandiza kupanga hemoglobin, mtundu wa mapuloteni m'maselo anu ofiira amwazi. Hemoglobin imanyamula mpweya kuchokera m'mapapu anu kupita nawo mthupi lanu lonse.

Sizachilendo kukhala ndi ma porphyrin ochepa m'magazi mwanu ndi madzi ena amthupi. Koma porphyrin wochuluka angatanthauze kuti muli ndi mtundu wa porphyria. Porphyria ndi matenda osowa omwe angayambitse matenda aakulu. Porphyria imagawidwa m'magulu awiri:

  • Ma porphyrias abwino, yomwe imakhudza kwambiri mantha am'mimba ndipo imayambitsa matenda am'mimba
  • Ma porphyrias odulidwa, zomwe zimayambitsa khungu pakakhala kuwala kwa dzuwa

Ma porphyrias ena amakhudza dongosolo lamanjenje komanso khungu.

Mayina ena: protoporphyrin; protoporphyrin, magazi; protoporhyrin, chopondapo; porphyrins, ndowe; kuwombera; porphyrins, mkodzo; Mayeso a Mauzerall-Granick; asidi; ALA; porphobilinogen; PBG; protoporphyrin yaulere ya erythrocyte; magawo a erythrocyte porphyrins; FEP


Kodi amagwiritsa ntchito chiyani?

Mayeso a Porphyrin amagwiritsidwa ntchito pozindikira kapena kuwunika porphyria.

Chifukwa chiyani ndikufuna mayeso a porphyrin?

Mungafunike kuyesa porphyrin ngati muli ndi zizindikiro za porphyria. Pali zizindikiro zosiyanasiyana zamitundu yosiyanasiyana ya porphyria.

Zizindikiro za pachimake porphyria ndizo:

  • Kupweteka m'mimba
  • Kudzimbidwa
  • Nseru ndi kusanza
  • Mkodzo wofiira kapena wofiirira
  • Kuyika kapena kupweteka m'manja ndi / kapena mapazi
  • Minofu kufooka
  • Kusokonezeka
  • Ziwerengero

Zizindikiro za cutaneous porphyria ndizo:

  • Kutengeka kwambiri ndi dzuwa
  • Matuza pakhungu lowala ndi dzuwa
  • Kufiira ndi kutupa pakhungu lowonekera
  • Kuyabwa
  • Kusintha kwa khungu

Mungafunenso kuyesa porphyrin ngati wina m'banja mwanu ali ndi porphyria. Mitundu yambiri ya porphyria ndi yotengera, kutanthauza kuti vutoli limaperekedwa kuchokera kwa kholo kupita kwa mwana.

Kodi chimachitika ndi chiyani poyesedwa kwa porphyrin?

Porphyrins amatha kuyesedwa m'magazi, mkodzo, kapena chopondapo. Mitundu yodziwika kwambiri ya mayeso a porphyrin alembedwa pansipa.


  • Kuyesa Magazi
    • Katswiri wa zamankhwala adzatenga magazi kuchokera mumtsinje uli m'manja mwanu, pogwiritsa ntchito singano yaying'ono. Singanoyo italowetsedwa, magazi ang'onoang'ono amatengedwa mu chubu choyesera. Mutha kumva kuluma pang'ono singano ikamalowa kapena kutuluka. Izi nthawi zambiri zimatenga mphindi zosakwana zisanu.
  • Zitsanzo za Mkodzo wa maola 24
    • Mudzatenga mkodzo wanu wonse mkati mwa maola 24. Pama mayeso awa, omwe amakuthandizani pa zaumoyo kapena labotale azikupatsani chidebe ndi malangizo amomwe mungatengere zitsanzo zanu kunyumba. Onetsetsani kutsatira malangizo onse mosamala. Kuyesa kwa mkodzo kwa maola 24 kumagwiritsidwa ntchito chifukwa kuchuluka kwa zinthu mumkodzo, kuphatikiza porphyrin, kumatha kusiyanasiyana tsiku lonse. Chifukwa chake kusonkhanitsa zitsanzo zingapo patsiku kumatha kupereka chithunzi cholondola cha mkodzo wanu.
  • Mayeso Osawerengeka a Mkodzo
    • Mutha kupereka zitsanzo zanu nthawi iliyonse patsiku, popanda kukonzekera kapena kusamalira zofunikira. Kuyesaku kumachitika nthawi zambiri muofesi ya othandizira azaumoyo kapena labu.
  • Kuyesa kopondera (komwe kumatchedwanso protoporphyrin mu chopondapo)
    • Muzisonkhanitsa chopondapo chanu ndikuziyika mu chidebe chapadera. Wothandizira zaumoyo wanu amakupatsani malangizo amomwe mungakonzekerere zitsanzo zanu ndikuzitumiza ku labu.

Kodi ndiyenera kuchita chilichonse kukonzekera mayeso?

Simukusowa kukonzekera kwapadera kokayezetsa magazi kapena mkodzo.


Kuti muyesedwe, mutha kulangizidwa kuti musadye nyama kapena kumwa mankhwala aliwonse a aspirin masiku atatu musanayesedwe.

Kodi pali zoopsa zilizonse poyesedwa kwa porphyrin?

Pali chiopsezo chochepa kwambiri choyesedwa magazi. Mutha kukhala ndi ululu pang'ono kapena kuvulala pamalo pomwe singano idayikidwapo, koma zizindikiro zambiri zimatha msanga.

Palibe zowopsa paziyeso za mkodzo kapena chopondapo.

Kodi zotsatirazi zikutanthauza chiyani?

Ngati kuchuluka kwa porphyrin kumapezeka m'magazi anu, mkodzo, kapena chopondapo, wothandizira zaumoyo wanu atha kuyitanitsa mayeso ena kuti atsimikizire matenda anu ndikupeza mtundu wa porphyria womwe muli nawo. Ngakhale kulibe mankhwala a porphyria, vutoli limatha kuyendetsedwa. Zosintha zina pamoyo komanso / kapena mankhwala amatha kuthandiza kupewa zizindikilo ndi zovuta za matendawa. Mankhwala apadera amatengera mtundu wa porphyria womwe muli nawo. Ngati muli ndi mafunso okhudzana ndi zotsatira zanu kapena za porphyria, lankhulani ndi omwe amakuthandizani.

Dziwani zambiri zamayeso a labotale, magawo owerengera, ndi zotsatira zakumvetsetsa.

Kodi pali china chilichonse chomwe ndiyenera kudziwa pamayeso a porphyrin?

Ngakhale mitundu yambiri ya porphyria idachokera, mitundu ina ya porphyria imapezekanso. Kupeza porphyria kumatha kuyambitsidwa ndi zinthu zosiyanasiyana, kuphatikiza kuwunika kwambiri kutsogolera, HIV, hepatitis C, kudya kwambiri chitsulo, komanso / kapena kumwa kwambiri.

Zolemba

  1. American Porphyria Foundation [Intaneti]. Houston: Maziko a American Porphyria; c2010–2017. Za Porphyria; [adatchula 2019 Dec 26]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: https://www.porphyriafoundation.org/for-patients/about-porphyria
  2. American Porphyria Foundation [Intaneti]. Houston: Maziko a American Porphyria; c2010–2017. Kuzindikira kwa Porphyrins ndi Porphyria; [adatchula 2019 Dec 26]; [pafupifupi zowonetsera 6]. Ipezeka kuchokera: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
  3. American Porphyria Foundation [Intaneti]. Houston: Maziko a American Porphyria; c2010–2017. Mayeso Oyambira Oyambirira; [adatchula 2019 Dec 26]; [pafupifupi zowonetsera 4]. Ipezeka kuchokera: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
  4. Hepatitis B Foundation [Intaneti]. Doylestown (PA): Hepb.org; c2017. Matenda Amatenda Amankhwala; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 11]. Ipezeka kuchokera: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
  5. Hinkle J, Cheever K. Brunner & Suddarth's Handbook of Laboratory and Diagnostic Test. 2nd Ed, Wokoma. Philadelphia: Wolters Kluwer Health, Lippincott Williams & Wilkins; c2014. Magulu a Erythrocyte Porphyrins (FEP); p. 308.
  6. Kuyesa kwa Labu Paintaneti [Intaneti]. American Association for Chipatala Chemistry; c2001–2017. Zakumapeto: Zitsanzo Zachilendo za Mkodzo; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3].Ipezeka kuchokera: https://labtestsonline.org/glossary#r
  7. Kuyesa kwa Labu Paintaneti [Intaneti]. American Association for Chipatala Chemistry; c2001–2017. Kuyesa kwa Porphyrin; [yasinthidwa 2017 Dec 20; yatchulidwa 2017 Dis 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: https://labtestsonline.org/tests/porphyrin-tests
  8. Chipatala cha Mayo [Intaneti]. Mayo Foundation for Medical Education and Research; c1998–2017. Porphyria: Zizindikiro ndi Zomwe Zimayambitsa; 2017 Nov 18 [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
  9. Chipatala cha Mayo: Mayo Medical Laboratories [Internet]. Mayo Foundation for Medical Education and Research; c1995–2017. ID Yoyesa: FQPPS: Porphyrins, Ndowe: Mwachidule; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 2]. Ipezeka kuchokera: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
  10. Chipatala cha Mayo: Mayo Medical Laboratories [Internet]. Mayo Foundation for Medical Education and Research; c1995–2017. ID Yoyesa: FQPPS: Porphyrins, Ndowe: Chitsanzo; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
  11. Merck Manual Consumer Version [Intaneti]. Kenilworth (NJ): Merck & Co. Inc. .; c2017. Porphyria; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/acute-intermittent-porphyria
  12. Merck Manual Consumer Version [Intaneti]. Kenilworth (NJ): Merck & Co. Inc. .; c2017. Chidule cha Porphyria; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 2]. Ipezeka kuchokera: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/overview-of-porphyria
  13. Merck Manual Consumer Version [Intaneti]. Kenilworth (NJ): Merck & Co. Inc. .; c2017. Porphyria Cutanea Tarda; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/porphyria-cutanea-tarda
  14. National Heart, Lung, ndi Blood Institute [Internet]. Bethesda (MD): Dipatimenti ya Zaumoyo ndi Zantchito ku U.S. Kuyesa Magazi; [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 3]. Ipezeka kuchokera: https://www.nhlbi.nih.gov/health-topics/blood-tests
  15. National Institute of Diabetes and Digestive and Impso Diseases [Intaneti]. Bethesda (MD): Dipatimenti ya Zaumoyo ndi Zantchito ku U.S. Chimfine; 2014 Feb [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 4]. Ipezeka kuchokera: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
  16. University of Rochester Medical Center [Intaneti]. Rochester (NY): Yunivesite ya Rochester Medical Center; c2017. Health Encyclopedia: Porphyrins (Mkodzo); [yotchulidwa 2017 Dec 20]; [pafupifupi zowonetsera 2]. Ipezeka kuchokera: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine

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