Mlembi: Frank Hunt
Tsiku La Chilengedwe: 18 Kuguba 2021
Sinthani Tsiku: 17 Ogasiti 2025
Anonim
Matenda a Crouzon: ndi chiyani, zizindikiro zazikulu ndi chithandizo - Thanzi
Matenda a Crouzon: ndi chiyani, zizindikiro zazikulu ndi chithandizo - Thanzi

Zamkati

Matenda a Crouzon, omwe amadziwikanso kuti craniofacial dysostosis, ndi matenda osowa pomwe pali kutsekedwa msanga kwa zigaza za chigaza, zomwe zimabweretsa zolakwika zingapo zakumaso ndi nkhope. Zofooka izi zitha kupanganso kusintha kwamachitidwe ena amthupi, monga masomphenya, kumva kapena kupuma, ndikupangitsa kuti zizikhala zofunikira kuchita maopareshoni amoyo wonse.

Akakayikira, matendawa amapangidwa kudzera mu mayeso a majini omwe amachitika panthawi yapakati, mwina pobadwa kapena mchaka choyamba cha moyo, koma nthawi zambiri amapezeka pokhapokha ali ndi zaka 2 zakubadwa pomwe zolakwika zimadziwika kwambiri.

Zizindikiro zazikulu

Makhalidwe a mwana wokhudzidwa ndi matenda a Crouzon amasiyana kuyambira wofatsa mpaka wolimba, kutengera kukula kwa zopundazo, ndikuphatikizanso:


  • Zowonongeka mu chigaza, mutu umakhala ndi nsanja ndipo nape imakhala yosalala;
  • Kusintha kwamaso monga kutuluka kwa maso komanso kutalikirapo kuposa kwachibadwa, kukulitsa mphuno, strabismus, keratoconjunctivitis, kusiyana kukula kwa ana;
  • Kuyenda mwachangu komanso kubwereza;
  • IQ pansipa yachibadwa;
  • Ogontha;
  • Zovuta zophunzirira;
  • Kusokonezeka kwa mtima;
  • Matenda osowa chidwi;
  • Khalidwe limasintha;
  • Brown mpaka mawanga akuda owoneka bwino pakhungu, khosi ndi / kapena pansi pa mkono.

Zomwe zimayambitsa matenda a Crouzon ndizabadwa, koma zaka za makolo zimatha kusokoneza ndikuwonjezera mwayi wobadwa ndi matendawa, chifukwa makolo amakula, pamakhala mwayi waukulu wopunduka.

Matenda ena omwe angayambitse zizindikiro zofananira ndi matendawa ndi Apert syndrome. Dziwani zambiri za matenda amtunduwu.

Momwe mankhwalawa amachitikira

Palibe mankhwala ochiritsira matenda a Crouzon, motero chithandizo cha mwana chimaphatikizapo kuchita maopaleshoni kuti achepetse kusintha kwa mafupa, kuchepetsa kupsinjika pamutu ndikupewa kusintha pakukula kwa chigaza ndi kukula kwa ubongo, poganizira zokongoletsa zonse ndi zotsatira zomwe zimayesetsa kukonza kuphunzira ndi magwiridwe antchito.


Momwemonso, opareshoni iyenera kuchitidwa mwana asanakwanitse chaka choyamba chobadwa, chifukwa mafupa amakhala osavuta kusintha. Kuphatikiza apo, kudzazidwa kwa zopindika za mafupa ndi methyl methacrylate prostheses kwagwiritsidwa ntchito pochita zodzikongoletsera kuti kusalaza ndikugwirizanitsa nkhope.

Kuphatikiza apo, mwanayo ayenera kulandira chithandizo chakuthupi ndi ntchito kwakanthawi. Cholinga cha physiotherapy ndikuthandizira kukhala ndi moyo wabwino wamwana ndikumupangitsa kuti akule bwino ngati momwe angathere. Psychotherapy ndi mankhwala olankhulira nawonso ndi mitundu yothandizirana yothandizira, ndipo opaleshoni yapulasitiki imathandizanso pakukweza nkhope ndikuthandizira kudzidalira kwa wodwalayo.

Komanso, onani masewera olimbitsa thupi omwe angapangidwe kunyumba kuti apange ubongo wa mwana ndikulimbikitsanso kuphunzira.

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