Mlembi: Roger Morrison
Tsiku La Chilengedwe: 27 Sepitembala 2021
Sinthani Tsiku: 8 Epulo 2025
Anonim
Acidose ou Alcalose ? Comment lire un bilan ( ph , HCO3- , CO2)
Kanema: Acidose ou Alcalose ? Comment lire un bilan ( ph , HCO3- , CO2)

Zamkati

Matenda a Fanconi ndi matenda osowa a impso omwe amatsogolera ku kudzikundikira kwa shuga, bicarbonate, potaziyamu, phosphates ndi ma amino acid owonjezera mumkodzo. Matendawa amatayanso mapuloteni mumkodzo ndipo mkodzo umakhala wolimba komanso wowonjezereka.

Hereditary Fanconi Syndrome imayambitsa kusintha kwa majini komwe kumachokera kwa bambo kupita kwa mwana wamwamuna. Kutengera pa Anapeza matenda a Fanconi, kumeza zitsulo zolemera, monga lead, kumeza maantibayotiki omwe atha nthawi yayitali, kuchepa kwa vitamini D, kumuika impso, multipleeloma kapena amyloidosis kungayambitse matendawa.

Fanconi Syndrome ilibe mankhwala ndipo chithandizo chake chimakhala m'malo mwa zinthu zomwe zatayika mumkodzo, zomwe a nephrologist amawonetsa.

Zizindikiro za Fanconi Syndrome

Zizindikiro za Fanconi Syndrome zitha kukhala:

  • Kukodza mkodzo wambiri;
  • Wamphamvu ndi acidic mkodzo;
  • Ludzu kwambiri;
  • Kutaya madzi m'thupi;
  • Mfupi;
  • High acidity m'magazi;
  • Zofooka;
  • Kupweteka kwa mafupa;
  • Zikwangwani zamtundu wa khofi pakhungu;
  • Kupezeka kapena kupunduka m'manja;

Nthawi zambiri, chikhalidwe cha Fanconi Syndrome cholowa chimawoneka muubwana wazaka pafupifupi 5 zakubadwa.


O matenda a Fanconi Syndrome imagwiritsidwa ntchito potengera zizindikilo, kuyesa magazi komwe kumawonetsa acidity yayikulu komanso kuyesa kwamkodzo komwe kumawonetsa shuga wochulukirapo, phosphate, bicarbonate, uric acid, potaziyamu ndi sodium.

Kuchiza kwa Fanconi Syndrome

Chithandizo cha Fanconi Syndrome cholinga chake ndi kuwonjezera zinthu zotayika ndi anthu mkodzo. Pachifukwa ichi, pangafunike kuti odwala atenge potaziyamu, phosphate ndi vitamini D supplementation, komanso sodium bicarbonate kuti ichepetse magazi acidosis.

Odwala omwe ali ndi vuto lalikulu la impso, kupatsidwa impso kumawonetsedwa.

Maulalo othandiza:

  • Zakudya za potaziyamu
  • Zakudya zokhala ndi vitamini D wambiri
  • Kuika Impso

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