Mlembi: John Stephens
Tsiku La Chilengedwe: 22 Jayuwale 2021
Sinthani Tsiku: 1 Kulayi 2024
Anonim
Cryptic - Aya Matenda ft 4Ka
Kanema: Cryptic - Aya Matenda ft 4Ka

Zamkati

Matenda a Wilson ndi ati?

Matenda a Wilson, omwe amadziwikanso kuti hepatolenticular degeneration ndi kuchepa kwa lenticular, ndi matenda osowa amtundu omwe amachititsa poyizoni wamkuwa m'thupi. Zimakhudza pafupifupi 1 mwa anthu 30,000 padziko lonse lapansi.

Thupi labwino, chiwindi chimasefa mkuwa wochulukirapo ndikuutulutsa kudzera mumkodzo. Ndi matenda a Wilson, chiwindi sichitha kuchotsa mkuwa wowonjezera bwino. Mkuwa wowonjezerayo kenako umamangidwa m'matupi monga ubongo, chiwindi, ndi maso.

Kuzindikira koyambirira ndikofunikira poletsa kukula kwa matenda a Wilson. Chithandizo chake chingaphatikizepo kumwa mankhwala kapena kupatsirana chiwindi. Kuchedwetsa kapena kusalandira chithandizo kumatha kuyambitsa chiwindi kulephera, kuwonongeka kwaubongo, kapena zochitika zina zowopsa.

Lankhulani ndi dokotala ngati banja lanu lili ndi mbiri ya matenda a Wilson. Anthu ambiri omwe ali ndi vutoli amakhala moyo wabwinobwino, wathanzi.

Zizindikiro ndi zizindikiro za matenda a Wilson

Zizindikiro za matenda a Wilson zimasiyanasiyana, kutengera kuti ndi chiwalo chiti chomwe chakhudzidwa. Amatha kulakwitsa chifukwa cha matenda ena kapena zovuta zina. Matenda a Wilson amatha kudziwika ndi dokotala komanso kudzera pakuyesa matenda.


Zokhudzana ndi chiwindi

Zizindikiro zotsatirazi zitha kuwonetsa kuchuluka kwa mkuwa m'chiwindi:

  • kufooka
  • kumva kutopa
  • kuonda
  • nseru
  • kusanza
  • kusowa chilakolako
  • kuyabwa
  • jaundice, kapena chikasu cha khungu
  • edema, kapena kutupa kwa miyendo ndi pamimba
  • kupweteka kapena kuphulika m'mimba
  • akangaude, kapena mitsempha yamagazi yooneka ngati nthambi pakhungu
  • kukokana kwa minofu

Zambiri mwazizindikirozi, monga jaundice ndi edema, ndizofanana ndi zikhalidwe zina monga kulephera kwa chiwindi ndi impso. Dokotala wanu ayesa kangapo asanatsimikizire kuti ali ndi matenda a Wilson.

Minyewa

Kuchulukana kwamkuwa muubongo kumatha kuyambitsa zizindikiro monga:

  • kukumbukira, kulankhula, kapena kuwonongeka kwa masomphenya
  • kuyenda kosazolowereka
  • mutu waching'alang'ala
  • kutsitsa
  • kusowa tulo
  • kusakhazikika ndi manja
  • kusintha kwa umunthu
  • amasintha malingaliro
  • kukhumudwa
  • mavuto kusukulu

Pakadutsa, zizindikilo izi zimatha kuphatikizira kutuluka kwa minofu, kugwidwa, ndi kupweteka kwa minofu poyenda.


Mphete za Kayser-Fleischer ndi maso a mpendadzuwa

Dokotala wanu adzawonanso mphete za Kayser-Fleischer (KF) ndi maso a mpendadzuwa m'maso. Mphete za KF ndizosazolowereka zofiirira m'maso zomwe zimayambitsidwa ndimitengo yambiri yamkuwa. Mphete za KF zimawonekera pafupifupi 97 peresenti ya anthu omwe ali ndi matenda a Wilson.

Ng'ona za mpendadzuwa zimawonekera mwa 1 mwa anthu asanu aliwonse omwe ali ndi matenda a Wilson. Awa ndi malo apadera okhala ndi masipoko omwe amawonekera panja.

Zizindikiro zina

Kuchuluka kwa mkuwa m'ziwalo zina kumatha kuyambitsa:

  • kutuluka kwamtundu wabuluu mumisomali
  • impso miyala
  • kufooka kwa mafupa msanga, kapena kuchepa kwa mafupa
  • nyamakazi
  • kusasamba kwa msambo
  • kuthamanga kwa magazi

Nchiyani chimayambitsa ndipo ndani ali pachiwopsezo cha matenda a Wilson?

Kusintha kwa Zamgululi jini, yomwe imafotokoza zamayendedwe amkuwa, imayambitsa matenda a Wilson. Muyenera kulandira cholowa kuchokera kwa makolo onse kuti mukhale ndi matenda a Wilson. Izi zitha kutanthauza kuti m'modzi mwa makolo anu ali ndi vutoli kapena ali ndi jini.


Jini limatha kudumpha m'badwo, kotero mungafune kuyang'ana mopitilira makolo anu kapena kukayezetsa chibadwa.

Kodi matenda a Wilson amapezeka bwanji?

Matenda a Wilson atha kukhala ovuta kuti madokotala azindikire poyambirira. Zizindikirozi ndizofanana ndi mavuto ena azaumoyo monga poyizoni wa heavy metal, hepatitis C, ndi ubongo.

Nthawi zina dokotala wanu amatha kuthana ndi matenda a Wilson pakangomaliza kuyambitsa matenda amitsempha ndipo palibe mphete ya K-F yomwe imawonekera.Koma izi sizili choncho nthawi zonse kwa anthu omwe ali ndi zizindikiro zokhudzana ndi chiwindi kapena osakhala ndi zizindikiro zina.

Dokotala adzafunsa za matenda anu ndikufunsani mbiri yakuchipatala yabanja lanu. Adzagwiritsanso ntchito mayeso osiyanasiyana kuti ayang'ane kuwonongeka komwe kumabwera chifukwa cha kuchuluka kwa mkuwa.

Kuyesa kwakuthupi

Pa nthawi ya thupi lanu, dokotala wanu:

  • fufuzani thupi lanu
  • mverani phokoso m'mimba
  • yang'anani maso anu pansi pa kuwala kowala kwa mphete za KF kapena mpendadzuwa wa mpendadzuwa
  • imayesa luso lanu lamagalimoto ndi kukumbukira

Mayeso a labu

Pofuna kuyezetsa magazi, dokotala wanu ajambula zitsanzo ndikuzifufuza ku labu kuti aone:

  • zovuta m'thupi lanu la chiwindi
  • misinkhu yamkuwa m'magazi
  • kutsika kwa ceruloplasmin, puloteni yomwe imanyamula mkuwa kudzera m'magazi
  • jini losinthidwa, lotchedwanso kuyesa kwa majini
  • shuga wotsika magazi

Dokotala wanu amathanso kukupemphani kuti mutenge mkodzo wanu kwa maola 24 kuti muwone kuchuluka kwa mkuwa.

Kodi matenda a Wilson amachiritsidwa bwanji?

Kuchiza bwino matenda a Wilson kumadalira nthawi yopitilira mankhwala. Chithandizo nthawi zambiri chimachitika m'magawo atatu ndipo chimayenera kukhala moyo wonse. Ngati munthu asiya kumwa mankhwalawo, mkuwa umatha kubwereranso.

Gawo loyamba

Chithandizo choyamba ndikuchotsa mkuwa wochulukirapo m'thupi lanu kudzera munthawi ya mankhwala. Othandizira ophatikizira amaphatikizapo mankhwala monga d-penicillamine ndi trientine, kapena Syprine. Mankhwalawa amachotsa mkuwa wowonjezera m'ziwalo zanu ndikuupereka m'magazi. Impso zanu zimasefa mkuwa mumkodzo.

Trientine ili ndi zovuta zochepa zomwe zanenedwa kuposa d-penicillamine. Zotsatira zoyipa d-penicillamine ndi monga:

  • malungo
  • zidzolo
  • nkhani za impso
  • Kutulutsa mafupa

Dokotala wanu azikupatsani mankhwala ocheperako ngati muli ndi pakati, chifukwa amatha kubala zovuta.

Gawo lachiwiri

Cholinga chachigawo chachiwiri ndikusungabe mkuwa ukachotsedwa. Dokotala wanu adzakupatsani zinc kapena tetrathiomolybdate ngati mwatsiriza chithandizo choyamba kapena simukuwonetsa zizindikiro koma muli ndi matenda a Wilson.

Zinc yotengedwa pakamwa ngati mchere kapena nthochi (Galzin) imapangitsa kuti thupi lisatenge mkuwa kuchokera ku zakudya. Mutha kukhala ndi vuto m'mimba pang'ono mukamamwa zinc. Ana omwe ali ndi matenda a Wilson koma alibe zizindikilo zilizonse zomwe angafune kutenga zinc kuti ateteze vutoli kapena kuchepetsako patsogolo.

Gawo lachitatu

Zizindikiro zikayamba kusintha ndipo milingo yanu yamkuwa ndiyabwino, mudzafunika kuyang'ana pa chithandizo chokhalitsa. Izi zikuphatikiza kupitiliza mankhwala a zinc kapena kubera komanso kuwunika momwe muliri mkuwa.

Muthanso kusamalira magawo anu amkuwa popewa zakudya zokhala ndi milingo yayikulu, monga:

  • zipatso zouma
  • chiwindi
  • bowa
  • mtedza
  • nkhono
  • chokoleti
  • mavitamini

Mungafune kuyang'ana kuchuluka kwanu kwamadzi kunyumba, inunso. Pakhoza kukhala mkuwa wowonjezera m'madzi anu ngati nyumba yanu ili ndi mapaipi amkuwa.

Mankhwala atha kutenga miyezi inayi mpaka isanu ndi umodzi kuti agwire ntchito mwa munthu amene akukumana ndi zizindikilo. Ngati munthu samayankha mankhwalawa, angafunike kumuika chiwindi. Kuthira bwino chiwindi kumatha kuchiza matenda a Wilson. Kuchuluka kwa kusintha kwa chiwindi ndi 85% patatha chaka chimodzi.

Kodi matenda a Wilson ndi otani?

Poyambirira mumadziwa ngati muli ndi jini la matenda a Wilson, ndibwino kuti mukudziwa bwino. Matenda a Wilson amatha kukhala kulephera kwa chiwindi komanso kuwonongeka kwa ubongo ngati atapanda kuchiritsidwa.

Chithandizo choyambirira chitha kuthandiza kuthana ndi mavuto amitsempha ndi kuwonongeka kwa chiwindi. Chithandizo pambuyo pake chitha kupewetsa kupita patsogolo kwa matendawa, koma sikubwezeretsanso kuwonongeka nthawi zonse. Anthu omwe ali patsogolo kwambiri ayenera kuphunzira momwe angathetsere matenda awo m'moyo wawo wonse.

Kodi mungapewe matenda a Wilson?

Matenda a Wilson ndi jini lobadwa nalo lomwe limaperekedwa kuchokera kwa makolo kupita kwa ana awo. Ngati makolo ali ndi mwana yemwe ali ndi matenda a Wilson, atha kukhala ndi ana ena omwe ali ndi vutoli.

Ngakhale simungathe kupewa matenda a Wilson, mutha kuchedwa kapena kuchepetsa kuyambika kwa vutoli. Ngati mupeza kuti muli ndi matenda a Wilson koyambirira, mutha kupewa kuti ziwonetsero zisamamwe ndikumwa mankhwala monga zinc. Katswiri wa majini amatha kuthandiza makolo kudziwa zomwe zitha kuchitika popatsira ana awo matenda a Wilson.

Masitepe otsatira

Pangani msonkhano ndi dokotala wanu ngati inu kapena munthu wina yemwe mumamudziwa mwina muli ndi matenda a Wilson kapena akuwonetsa zizindikiro zakulephera kwa chiwindi. Chizindikiro chachikulu cha vutoli ndi mbiri ya banja, koma jini losinthidwa limatha kudumpha m'badwo. Mungafune kufunsa kuyesedwa kwa majini limodzi ndi mayeso ena omwe dokotala angakonzekere.

Mudzafuna kuyamba chithandizo chanu nthawi yomweyo ngati mutapezeka ndi matenda a Wilson. Chithandizo choyambirira chitha kuthandiza kupewa kapena kuchedwetsa vutoli, makamaka ngati simukuwonetsa zizindikilo. Mankhwala amaphatikizapo ochita kubera ndi zinc ndipo amatha miyezi isanu ndi umodzi kuti agwire ntchito. Ngakhale milingo yanu yamkuwa ikabwerera mwakale, muyenera kupitiriza kumwa mankhwala, chifukwa matenda a Wilson amakhala moyo wonse.

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