Hemophilia

Hemophilia amatanthauza gulu lamavuto omwe amatuluka magazi momwe magazi amatenga nthawi yayitali.

Pali mitundu iwiri ya hemophilia:

• Hemophilia A (classic hemophilia, kapena factor VIII kusowa)
• Hemophilia B (matenda a Khrisimasi, kapena kuchepa kwa factor IX)

Mukamatuluka magazi, zochitika zingapo zimachitika mthupi zomwe zimathandiza kuundana kwamagazi. Izi zimatchedwa coagulation cascade. Zimaphatikizapo mapuloteni apadera otchedwa coagulation, kapena clotting factor. Mutha kukhala ndi mwayi wopita magazi ochulukirapo ngati chimodzi kapena zingapo mwazimene zikusowa kapena sizikugwira ntchito momwe ziyenera kukhalira.

Hemophilia amayamba chifukwa chakusowa kwa magazi oundana a VIII kapena IX m'magazi. Nthawi zambiri, hemophilia imafalikira kudzera m'mabanja (obadwa nawo). Nthawi zambiri, imaperekedwa kwa ana amuna.

Chizindikiro chachikulu cha hemophilia ndikutuluka magazi. Matenda ofooka sangazindikiridwe mpaka pambuyo pake m'moyo, atataya magazi kwambiri atachitidwa opaleshoni kapena kuvulala.

Nthawi zoyipa kwambiri, kutuluka magazi kumachitika popanda chifukwa. Kutuluka magazi mkati kumatha kupezeka paliponse ndipo kutuluka magazi m'malo olumikizana ndikofala.

Nthawi zambiri, hemophilia imapezeka munthu atakhala ndi vuto lakutuluka magazi. Ikhozanso kudziwika ndi kuyesa magazi komwe kwachitika kuti mupeze vutoli, ngati abale ena ali ndi vutoli.

Chithandizo chofala kwambiri ndikubwezeretsa magazi omwe asoweka m'magazi kudzera mumitsempha (infusions infusions).

Chisamaliro chapadera pa opaleshoni chiyenera kutengedwa ngati muli ndi matendawa. Chifukwa chake, onetsetsani kuti muuza dokotala wanu kuti muli ndi vutoli.

Ndikofunikanso kugawana zambiri zamatenda anu ndi abale amwazi momwe nawonso angakhudzidwire.

Kuyanjana ndi gulu lothandizira pomwe mamembala amagawana nawo zinthu zofananako kumatha kuthetsa nkhawa zamatenda ataliatali.

Anthu ambiri omwe ali ndi hemophilia amatha kuchita zinthu zachilendo. Koma anthu ena amataya magazi m'malo olumikizirana mafupa, zomwe zimachepetsa ntchito yawo.

Anthu ochepa omwe ali ndi hemophilia amatha kufa ndikutuluka magazi kwambiri.

Hemophilia A; Classic hemophilia; Kusowa kwa Factor VIII; Hemophilia B; Matenda a Khirisimasi; Kulephera kwa Factor IX; Kutaya magazi - hemophilia

• Kuundana kwamagazi

Carcao M, Moorehead P, Lillicrap D.Hemophilia A ndi B. Mu: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Mfundo Zoyambira ndi Zochita. Wachisanu ndi chiwiri. Philadelphia, PA: Elsevier; 2018: mutu 135.

Hall JE. Hemostasis ndi magazi coagulation. Mu: Hall JE, mkonzi. Guyton ndi Hall Textbook of Medical Physiology. Wolemba 13. Philadelphia, PA: Elsevier; 2016: chap 37.

Ragni MV. Matenda a hemorrhagic: coagulation factor deficience. Mu: Goldman L, Schafer AI, olemba. Mankhwala a Goldman-Cecil. Wolemba 25. Philadelphia, PA: Elsevier Saunders; 2016: chap 174.