Mlembi: Gregory Harris
Tsiku La Chilengedwe: 16 Epulo 2021
Sinthani Tsiku: 26 Kuni 2024
Anonim
Hypomelanosis of Ito
Kanema: Hypomelanosis of Ito

Hypomelanosis ya Ito (HMI) ndi vuto losabadwa kwambiri lomwe limayambitsa zigamba zosazolowereka za khungu lowoneka bwino ndipo limatha kuphatikizidwa ndi maso, dongosolo lamanjenje, ndi mavuto am'mafupa.

Osamalira zaumoyo sakudziwa chifukwa chenicheni cha HMI, koma amakhulupirira kuti atha kukhala ndi vuto lotengera zojambulajambula. Ndiwowirikiza kawiri mwa atsikana kuposa anyamata.

Zizindikiro zakhungu nthawi zambiri zimawoneka nthawi yomwe mwana amakhala wazaka pafupifupi 2.

Zizindikiro zina zimakula mwana akamakula, ndipo mwina ndi izi:

  • Maso owoloka (strabismus)
  • Mavuto akumva
  • Kuchulukitsa tsitsi la thupi (hirsutism)
  • Scoliosis
  • Kugwidwa
  • Zotumphuka, zikwere kapena zikopa zamagulu pamikono, miyendo, ndi pakati pa thupi
  • Kulemala kwamalingaliro, kuphatikiza mawonekedwe a autism komanso kulephera kuphunzira
  • Pakamwa kapena mavuto amano

Kuunika kwa ultraviolet (Nyali yamatabwa) kuwunika kwa khungu kungathandize kutsimikizira kuti ali ndi matendawa.

Mayeso omwe angachitike ndi awa:


  • Kujambula kwa CT kapena MRI kwa mwana yemwe ali ndi khunyu komanso zizindikiritso zamanjenje
  • X-ray ya mwana yemwe ali ndi mavuto am'mafupa
  • EEG kuyeza zamagetsi zamaubongo mwa mwana wogwidwa
  • Kuyesedwa kwachibadwa

Palibe chithandizo cha zigamba za khungu. Zodzoladzola kapena zovala zitha kugwiritsidwa ntchito kuphimba zigamba. Khunyu, scoliosis, ndi mavuto ena amathandizidwa pakufunika.

Maonekedwe amatengera mtundu ndi kuuma kwa zizindikilo zomwe zimayamba. Nthawi zambiri, khungu limatha kusintha kukhala labwinobwino.

Mavuto omwe amabwera chifukwa cha HMI ndi awa:

  • Zovuta komanso zovuta kuyenda chifukwa cha scoliosis
  • Mavuto am'mutu, okhudzana ndi mawonekedwe akuthupi
  • Kulemala kwamaluso
  • Kuvulala chifukwa cha kugwidwa

Itanani omwe akukuthandizani ngati mwana wanu ali ndi mtundu wina wa khungu. Komabe, mitundu iliyonse yachilendo imatha kukhala ndi chifukwa china kuposa HMI.

Zosagwirizana ndi pigmenti achromians; HMI; Ito hypomelanosis


Joyce JC. Zilonda za Hypopigmented. Mu: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, olemba. Nelson Textbook of Pediatrics. Wolemba 21. Philadelphia, PA: Elsevier; 2020: chap 672.

Patterson JW. Matenda a pigmentation. Mu: Patterson JW, mkonzi. Matenda a Khungu la Weedon. Wolemba 4. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: mutu 10.

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